Electronic Resource
Assessment of congenital neutropenia in children: common clinical sceneries and clues for management
| العنوان: | Assessment of congenital neutropenia in children: common clinical sceneries and clues for management |
|---|---|
| المؤلفون: | Lazzareschi, Ilaria, Rossi, Elena, Curatola, A, Capozio, G, Benacquista, Luca, Iezzi, Ludovica, Rigante, Donato, Lazzareschi I (ORCID:0000-0001-7221-2983), Rossi E (ORCID:0000-0002-7572-9379), Benacquista L, Iezzi L, Rigante D (ORCID:0000-0001-7032-7779) |
| بيانات النشر: | 2021 |
| نوع الوثيقة: | Electronic Resource |
| مستخلص: | A disparate group of rare hematological diseases characterized by impaired maturation of neutrophil granulocytes defines congenital neutropenias. Neutropenic patients are prone to recurrent infections beginning in the first months of life. Of interest is "cyclic neutropenia," an ultra-rare disorder revealed by sinusoidal variations in the neutrophil count and recurring infections every 21 days. Diagnosis of these disorders is frequently obscured by the multiple causes of recurrent fevers in children. The aim of this overview is to outline the physical assessment of children presenting with early-onset symptomatic neutropenia, identify the disease between the many medical conditions and even emergencies which should enter in differential diagnosis, hint at the potential management with granulocyte-colony stimulating factor, define the risk of evolution to hematologic malignancy, and summarize inter-professional team strategies for improving care coordination and outcomes of patients. |
| مصطلحات الفهرس: | Neutropenia, Settore MED/38 - PEDIATRIA GENERALE E SPECIALISTICA, info:eu-repo/semantics/article |
| URL: | info:eu-repo/semantics/altIdentifier/pmid/35070215 info:eu-repo/semantics/altIdentifier/wos/WOS:000765024600008 volume:2022 issue:14(1) firstpage:1 lastpage:11 numberofpages:11 issueyear:2022 journal:MEDITERRANEAN JOURNAL OF HEMATOLOGY AND INFECTIOUS DISEASES |
| الاتاحة: | Open access content. Open access content info:eu-repo/semantics/openAccess |
| ملاحظة: | English |
| Other Numbers: | SYC oai:publicatt.unicatt.it:10807/191863 10.4084/MJHID.2022.008 info:eu-repo/semantics/altIdentifier/scopus/2-s2.0-85123342416 1330708314 |
| المصدر المساهم: | UNIV CATTOLICA DEL SACRO CUORE From OAIster®, provided by the OCLC Cooperative. |
| رقم الانضمام: | edsoai.on1330708314 |
| قاعدة البيانات: | OAIster |
| الوصف غير متاح. |