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Progressive retinal vessel malformation in a premature infant with Sturge-Weber syndrome: a case report and a literature review of ocular manifestations in Sturge-Weber syndrome

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العنوان: Progressive retinal vessel malformation in a premature infant with Sturge-Weber syndrome: a case report and a literature review of ocular manifestations in Sturge-Weber syndrome
المؤلفون: Zhengping Hu, Jian Cao, Eun Young Choi, Yun Li
المصدر: BMC Ophthalmology, Vol 21, Iss 1, Pp 1-6 (2021)
بيانات النشر: BMC, 2021.
سنة النشر: 2021
المجموعة: LCC:Ophthalmology
مصطلحات موضوعية: Sturge-weber syndrome, Ocular manifestation, Retinal vessel malformation, Nevus flammeus, Diffuse choroidal hemangioma, Ophthalmology, RE1-994
الوصف: Abstract Background Sturge-Weber syndrome is a disorder marked by a distinctive facial capillary malformation, neurological abnormalities, and ocular abnormalities such as glaucoma and choroidal hemangioma. Case presentation We report a case of progressively formed retinal vessel malformation in a premature male infant with Sturge-Weber syndrome and retinopathy of prematurity, after treatment with intravitreal anti-vascular endothelial growth factor (VEGF). The baby was born at 30 weeks gestation with a nevus flammeus involving his left eyelids and maxillary area. On postmenstrual age week 39, he received intravitreal anti-VEGF. Diffuse choroidal hemangioma became evident at 40 weeks, with the classic “tomato catsup fundus” appearance. These clinical findings characterized Sturge-weber syndrome. He presented with posterior retinal vessel tortuosity and vein-to-vein anastomoses at 44 weeks. Conclusion This is a rare case of documented progression of retinal vessel malformations in a patient with Sturge-Weber syndrome and retinopathy of prematurity.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
تدمد: 1471-2415
Relation: https://doaj.org/toc/1471-2415
DOI: 10.1186/s12886-021-01815-8
URL الوصول: https://doaj.org/article/afa4cc442ff14161b913f47f64a576f0
رقم الانضمام: edsdoj.fa4cc442ff14161b913f47f64a576f0
قاعدة البيانات: Directory of Open Access Journals
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