Academic Journal

Pediatric Intracochlear Schwannoma: Case Series and Review of the Literature

التفاصيل البيبلوغرافية
العنوان: Pediatric Intracochlear Schwannoma: Case Series and Review of the Literature
المؤلفون: Enrico Liaci, Maurizio Negri, Francesco Maccarrone, Silvia Piccinini, Enrico Pasanisi, Andrea Bacciu, Filippo Di Lella
المصدر: Journal of International Advanced Otology, Vol 20, Iss 6, Pp 484-488 (2024)
بيانات النشر: AVES, 2024.
سنة النشر: 2024
المجموعة: LCC:Otorhinolaryngology
مصطلحات موضوعية: Otorhinolaryngology, RF1-547
الوصف: Background: Intracochlear schwannomas (ICSs) are a subtype of intralabyrinthine schwannomas, completely located in the cochlear lumen. ICSs are particularly rare in the pediatric population. Putative diagnosis is made on the basis of magnetic resonance findings with signal characteristics that should remain the same at follow-up imaging. Methods: A retrospective review was performed searching for pediatric patients affected by ICS treated at the Otolaryngology Department, Ospedale Ramazzini, Carpi (Italy), and Otolaryngology and Otoneurosurgery Department, Azienda Ospedaliero-Universitaria di Parma, (Italy). A scoping literature review of the period January 2000 - June 2024 was performed. Results: Two cases of ICS in pediatric patients are described. Neither family history nor genetic signs of neurofibromatosis type II were found. A single report was identified in the literature review. Data analysis resumes the pooled data of the latter case and the authors’ patients. The most common symptom at presentation was progressive sensorineural hearing loss (66%). Mean pure tone average at diagnosis was 74.2 dB. Intracochlear location was in the basal turn in 2 cases and in the apical and middle turns in the third patient. All cases initially underwent a “wait and scan” strategy. The mean follow-up time was 23.3 months. Conclusion: Management planning of pediatric ICSs should be accurate as surgical removal may require partial or total cochlear demolition, resulting in vestibular dysfunction and precluding future positioning of a cochlear implant. Close clinical and radiological follow-up with serial MRI scans allows to evaluate both symptom progression and rate of growth, in order to provide patients with the best therapeutic option.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
تدمد: 2148-3817
Relation: https://www.advancedotology.org/en/pediatric-intracochlear-schwannoma-case-series-and-review-of-the-literature-131963; https://doaj.org/toc/2148-3817
DOI: 10.5152/iao.2024.241645
URL الوصول: https://doaj.org/article/9c32fffe641d4af1af57c90de67e5071
رقم الانضمام: edsdoj.9c32fffe641d4af1af57c90de67e5071
قاعدة البيانات: Directory of Open Access Journals
الوصف
تدمد:21483817
DOI:10.5152/iao.2024.241645