Academic Journal
Congenital Corrected Transposition of Great Arteries in Adults with Varied Presentation
العنوان: | Congenital Corrected Transposition of Great Arteries in Adults with Varied Presentation |
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المؤلفون: | Akshay Narendra Kotasthane, Susheel K. Malani, Chigullapalli Sridevi, Digvijay D Nalawade |
المصدر: | Journal of the Practice of Cardiovascular Sciences, Vol 10, Iss 3, Pp 197-202 (2024) |
بيانات النشر: | Wolters Kluwer Medknow Publications, 2024. |
سنة النشر: | 2024 |
المجموعة: | LCC:Medicine LCC:Surgery LCC:Diseases of the circulatory (Cardiovascular) system |
مصطلحات موضوعية: | complete heart block, congenital corrected transposition of great arteries, heart failure, permanent pacemaker implantation, Medicine, Surgery, RD1-811, Diseases of the circulatory (Cardiovascular) system, RC666-701 |
الوصف: | Congenital corrected transportation of great arteries (ccTGA) is a rare congenital heart disease, accounting for < 1% of congenital heart diseases. It remains undiagnosed until adulthood, in the absence of associated congenital anomalies. Adults with ccTGA are usually asymptomatic or their diagnosis may be missed during initial evaluation. It is sometimes diagnosed inadvertently while evaluating a murmur or a low heart rate. We aim to report three cases of ccTGA with varied presentations. We presented three cases of ccTGA with varied presentation, two cases of complete heart block requiring permanent pacemaker, out of which one had situs inversus totalis with levocardia, the other had situs solitus. The 3rd case was presented as case of ccTGA with heart failure with viseroarterial situs solitus, large atrial septal defect, large inlet ventricular septal defect, and severe pulmonary stenosis and had undergone bidirectional Glenn shunt. These cases illustrate the challenges confronted in adult practices when patient with unrecognized ccTGA presents during initial visits. Congenital corrected transposition of great arteries is rare congenital anomaly that poses a challenge in adulthood due to its varied presentation. Thus, an increased awareness about key diagnostic features is crucial for early recognition of ccTGA and its effective management. |
نوع الوثيقة: | article |
وصف الملف: | electronic resource |
اللغة: | English |
تدمد: | 2395-5414 2454-2830 |
Relation: | https://journals.lww.com/10.4103/jpcs.jpcs_83_23; https://doaj.org/toc/2395-5414; https://doaj.org/toc/2454-2830 |
DOI: | 10.4103/jpcs.jpcs_83_23 |
URL الوصول: | https://doaj.org/article/ea965bc8c5c14d32a47df265e6ee54af |
رقم الانضمام: | edsdoj.965bc8c5c14d32a47df265e6ee54af |
قاعدة البيانات: | Directory of Open Access Journals |
تدمد: | 23955414 24542830 |
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DOI: | 10.4103/jpcs.jpcs_83_23 |