Academic Journal

Two cases of airway-centered fibroelastosis treated with an antifibrotic agent and corticosteroids

التفاصيل البيبلوغرافية
العنوان: Two cases of airway-centered fibroelastosis treated with an antifibrotic agent and corticosteroids
المؤلفون: Miwa Kamatani, Minoru Inomata, Akari Misumi, Ken Ito, Takashi Maeda, Haruka Chin, Yu Ito, Keita Sakamoto, Nobuyasu Awano, Naoyuki Kuse, Yoshiaki Furuhata, Yuan Bae, Hiroaki Sugiura, Tamiko Takemura, Takehiro Izumo
المصدر: Respiratory Medicine Case Reports, Vol 50, Iss , Pp 102036- (2024)
بيانات النشر: Elsevier, 2024.
سنة النشر: 2024
المجموعة: LCC:Diseases of the respiratory system
مصطلحات موضوعية: Airway-centered fibroelastosis, Pleuroparenchymal fibroelastosis, Nintedanib, Corticosteroids, Progressive fibrosing interstitial lung disease, Diseases of the respiratory system, RC705-779
الوصف: Airway-centered fibroelastosis is characterized by peribronchovascular fibroelastosis, predominantly in the upper lobes, with little-to-no pleural involvement. In this study, we describe two cases of airway-centered fibroelastosis diagnosed based on radiological and pathological findings. The first case comprised a 44-year-old man whose forced vital capacity improved over three months following treatment with nintedanib. The second case involved a 50-year-old woman who was treated with oral corticosteroids but yielded an unfavorable outcome. An effective treatment for airway-centered fibroelastosis has not yet been identified; therefore, this study may help contribute to a more thorough discussion regarding treatment strategies for this disease.
نوع الوثيقة: article
وصف الملف: electronic resource
اللغة: English
تدمد: 2213-0071
Relation: http://www.sciencedirect.com/science/article/pii/S2213007124000595; https://doaj.org/toc/2213-0071
DOI: 10.1016/j.rmcr.2024.102036
URL الوصول: https://doaj.org/article/3375839ba5c54ad1aa008e6ec3a4b898
رقم الانضمام: edsdoj.3375839ba5c54ad1aa008e6ec3a4b898
قاعدة البيانات: Directory of Open Access Journals
الوصف
تدمد:22130071
DOI:10.1016/j.rmcr.2024.102036