التفاصيل البيبلوغرافية
العنوان: |
Two cases of airway-centered fibroelastosis treated with an antifibrotic agent and corticosteroids |
المؤلفون: |
Miwa Kamatani, Minoru Inomata, Akari Misumi, Ken Ito, Takashi Maeda, Haruka Chin, Yu Ito, Keita Sakamoto, Nobuyasu Awano, Naoyuki Kuse, Yoshiaki Furuhata, Yuan Bae, Hiroaki Sugiura, Tamiko Takemura, Takehiro Izumo |
المصدر: |
Respiratory Medicine Case Reports, Vol 50, Iss , Pp 102036- (2024) |
بيانات النشر: |
Elsevier, 2024. |
سنة النشر: |
2024 |
المجموعة: |
LCC:Diseases of the respiratory system |
مصطلحات موضوعية: |
Airway-centered fibroelastosis, Pleuroparenchymal fibroelastosis, Nintedanib, Corticosteroids, Progressive fibrosing interstitial lung disease, Diseases of the respiratory system, RC705-779 |
الوصف: |
Airway-centered fibroelastosis is characterized by peribronchovascular fibroelastosis, predominantly in the upper lobes, with little-to-no pleural involvement. In this study, we describe two cases of airway-centered fibroelastosis diagnosed based on radiological and pathological findings. The first case comprised a 44-year-old man whose forced vital capacity improved over three months following treatment with nintedanib. The second case involved a 50-year-old woman who was treated with oral corticosteroids but yielded an unfavorable outcome. An effective treatment for airway-centered fibroelastosis has not yet been identified; therefore, this study may help contribute to a more thorough discussion regarding treatment strategies for this disease. |
نوع الوثيقة: |
article |
وصف الملف: |
electronic resource |
اللغة: |
English |
تدمد: |
2213-0071 |
Relation: |
http://www.sciencedirect.com/science/article/pii/S2213007124000595; https://doaj.org/toc/2213-0071 |
DOI: |
10.1016/j.rmcr.2024.102036 |
URL الوصول: |
https://doaj.org/article/3375839ba5c54ad1aa008e6ec3a4b898 |
رقم الانضمام: |
edsdoj.3375839ba5c54ad1aa008e6ec3a4b898 |
قاعدة البيانات: |
Directory of Open Access Journals |