التفاصيل البيبلوغرافية
| العنوان: |
Atypical skeletal involvement in patients with Erdheim–Chester disease: CT imaging findings |
| المؤلفون: |
Zaizhu Zhang, Wei Yu, Wenmin Guan, Qiang Lin, Ali Guermazi |
| المصدر: |
Orphanet Journal of Rare Diseases, Vol 17, Iss 1, Pp 1-9 (2022) |
| بيانات النشر: |
BMC, 2022. |
| سنة النشر: |
2022 |
| المجموعة: |
LCC:Medicine |
| مصطلحات موضوعية: |
Erdheim–Chester disease, Atypical skeletal involvement, Computed tomography, Imaging findings, Medicine |
| الوصف: |
Abstract Objectives To review retrospectively atypical bone findings from computed tomographic (CT) imaging in patients with Erdheim–Chester disease. Methods All 28 patients with Erdheim–Chester disease (13 men and 15 women; mean age, 45 years; range, 7–63 years) underwent chest-abdomen-pelvis CT. CT images were reviewed and analyzed for the various features of atypical bone lesions by two radiologists in consensus. Results Twenty-one patients had atypical bone involvement. Radiologically, these atypical osseous lesions were categorized into three types: diffuse, nodular and patchy. Eleven (52%) of the 21 patients had spinal lesions, of which four (36%) had the diffuse type, eight (73%) had the nodular pattern, and six (55%) had the patchy pattern. Sixteen (76%) of the 21 patients had pelvic involvement, of which two (13%) were diffuse, nine (56%) were nodular and 11 were (69%) patchy. Ribs were involved in seven (33%) of the 21 patients, with the nodular pattern in one (14%) patient and the patchy type in six (86%) patients. Clavicle involvement was seen in nine (43%) of the 21 patients, of which the diffuse type was found in only one (11%) patient, the nodular type in six (67%) patients, the solitary patchy type in four (44%) patients. Sternum involvement was seen in 10 (48%) of the 21 patients and all were nodular. Conclusions This series provides a detailed description of atypical bone involvement in Erdheim–Chester disease which on CT displays three major patterns. Understanding these patterns may help increase the accuracy of diagnosis of this disease. |
| نوع الوثيقة: |
article |
| وصف الملف: |
electronic resource |
| اللغة: |
English |
| تدمد: |
1750-1172 |
| Relation: |
https://doaj.org/toc/1750-1172 |
| DOI: |
10.1186/s13023-022-02185-0 |
| URL الوصول: |
https://doaj.org/article/09e3a0f640e5403ca1529ff63a761b2f |
| رقم الانضمام: |
edsdoj.09e3a0f640e5403ca1529ff63a761b2f |
| قاعدة البيانات: |
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