Academic Journal
Stomatological management of patients with pycnodysostosis Report of a case. ; Manejo estomatológico de paciente con picnodisostosis Presentación de un caso.
| العنوان: | Stomatological management of patients with pycnodysostosis Report of a case. ; Manejo estomatológico de paciente con picnodisostosis Presentación de un caso. |
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| المؤلفون: | Martínez Liares, María Elena, Pérez Peláez, Edgar Mauricio, Badillo Estévez, Bitia Eunice |
| المصدر: | Ciencia Latina Revista Científica Multidisciplinar; Vol. 6 Núm. 6 (2022); 6452-6461 ; 2707-2215 ; 2707-2207 ; 10.37811/cl_rcm.v6i6 |
| بيانات النشر: | Centro de Investigación ALAC - Asociación Latinoamérica para el Avance de las Ciencias |
| سنة النشر: | 2022 |
| مصطلحات موضوعية: | picnodisostosis, osteosclerosis, maxillofacial anomaly, dental management, anomalía maxilofacial, manejo odontológico |
| الوصف: | Pycnodysostosis is an autosomal recessive disease characterized by bone fragility and delayed closure of cranial sutures whose pathophysiology has been attributed to a deficiency of cathepsin K, the incidence is 1 per 100,000 in a population. The most frequent clinical manifestations are spontaneous fractures. The patients present characteristic cranial malformations, voluminous frontal, exophthalmos, small mandible, ogival palate, periodontal disease, delayed eruption and dental persistence. The management is symptomatic and multidisciplinary, it includes an orthopedic follow-up, for the treatment of fractures, in the area of dentistry, it can be rehabilitated considering the time of each appointment and care to avoid fractures. A 9-year-old female patient diagnosed with pycnodysostosis, from Puebla, attended a pediatric stomatology clinic of the FEBUAP due to dental caries, with characteristic features of the syndrome, a complete clinical history was performed, a oral hygiene, prophylaxis with topical application of 5% sodium fluoride, extractions of temporary teeth, resins and monitoring of their oral habits. Patients with pycnodysostosis should be examined and treated carefully for risks to bone fractures involving short work times in the dental chair, it is recommended to implement oral hygiene measures to prevent tooth decay and periodontal problems. ; La picnodisostosis es una enfermedad autosómica recesiva caracterizada por fragilidad ósea, baja estatura y cierre retardado de las suturas craneales cuya fisiopatología se ha atribuido a una deficiencia de catepsina K, la incidencia es 1 por cada 100,000 en una población. Las manifestaciones clínicas más frecuentes son estatura baja, fragilidad de los huesos asociada a fracturas espontáneas. Los pacientes presentan malformaciones craneales características como megacefalea y braquicefalia, frontal voluminoso, exoftalmos, nariz prominente, mandíbula pequeña, paladar ojival, enfermedad periodontal, retraso en la erupción y persistencia dental. El manejo es ... |
| نوع الوثيقة: | article in journal/newspaper |
| وصف الملف: | application/pdf; text/html |
| اللغة: | Spanish; Castilian |
| Relation: | https://ciencialatina.org/index.php/cienciala/article/view/3898/5911; https://ciencialatina.org/index.php/cienciala/article/view/3898/5912; https://ciencialatina.org/index.php/cienciala/article/view/3898 |
| DOI: | 10.37811/cl_rcm.v6i6.3898 |
| الاتاحة: | https://ciencialatina.org/index.php/cienciala/article/view/3898 https://doi.org/10.37811/cl_rcm.v6i6.3898 |
| Rights: | Derechos de autor 2022 María Elena Martínez Liares;Edgar Mauricio Pérez Peláez;Bitia Eunice Badillo Estévez;Bitia Eunice Badillo Estévez ; https://creativecommons.org/licenses/by/4.0 |
| رقم الانضمام: | edsbas.BB9A7BF9 |
| قاعدة البيانات: | BASE |
| DOI: | 10.37811/cl_rcm.v6i6.3898 |
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