Academic Journal

Sterile, Recurrent, And Bilateral Corneal Perforation Related To Primary Biliary Cirrhosis Complicated By Secondary Sjögren Syndrome And Vitamin A Deficiency

التفاصيل البيبلوغرافية
العنوان: Sterile, Recurrent, And Bilateral Corneal Perforation Related To Primary Biliary Cirrhosis Complicated By Secondary Sjögren Syndrome And Vitamin A Deficiency
المؤلفون: Martín, Leyre Lloreda, Rocha de Lossada, Carlos, Marín-Martínez, Sara, Peraza-Nieves, Jorge Ernesto
المساهمون: Universidad de Sevilla. Departamento de Cirugía
بيانات النشر: Belfort Editora
سنة النشر: 2022
المجموعة: idUS - Deposito de Investigación Universidad de Sevilla
مصطلحات موضوعية: Primary biliary cirrhosis, Corneal perforation, Sjogren syndrome, Vitamin A deficiency, Autoimmune disease
الوصف: Primary biliary cirrhosis is a rare progressive autoimmune liver disease that causes chronic cholestasis. Of patients with primary biliary cirrhosis, 75% develop secondary Sjogren syndrome and could develop vitamin A deficiency. Here, we report the case of a patient with primary biliary cirrhosis who developed a secondary Sjogren syndrome and vitamin A deficiency, which led to severe and unusual eye involvement with multiple and recurrent spontaneous corneal perforations. Corneal perforations in patients with primary biliary cirrhosis and secondary Sjogren syndrome are rare but devastating complications, in contrast to other eye clinical manifestations of the disease.
نوع الوثيقة: article in journal/newspaper
اللغة: English
Relation: Arquivos Brasileiros de Oftalmologia, 84 (6), 606-609.; http://doi.org/10.5935/0004-2749.20210100; https://idus.us.es/handle//11441/137434
الاتاحة: https://idus.us.es/handle//11441/137434
Rights: Attribution-NonCommercial-NoDerivatives 4.0 Internacional ; http://creativecommons.org/licenses/by-nc-nd/4.0/ ; info:eu-repo/semantics/openAccess
رقم الانضمام: edsbas.4A7D9801
قاعدة البيانات: BASE