Double-outlet left ventricle: single-center experience and literature review

التفاصيل البيبلوغرافية
العنوان: Double-outlet left ventricle: single-center experience and literature review
المؤلفون: Michele Lioncino, Fausto Badolato, Emanuele Monda, Stella Maiolo, Andrea De Zorzi, Giulio Calcagni, Marcello Chinali, Alessia del Pasqua, Claudia Esposito, Mariella Iacomino, Paolo Guccione, Aurelio Secinaro, Lorenzo Galletti, Adriano Carotti, Maria Giovanna Russo, Giuseppe Limongelli, Fabrizio Drago, Gabriele Rinelli
المساهمون: Lioncino, Michele, Badolato, Fausto, Monda, Emanuele, Maiolo, Stella, De Zorzi, Andrea, Calcagni, Giulio, Chinali, Marcello, del Pasqua, Alessia, Esposito, Claudia, Iacomino, Mariella, Guccione, Paolo, Secinaro, Aurelio, Galletti, Lorenzo, Carotti, Adriano, Russo, MARIA GIOVANNA, Limongelli, Giuseppe, Drago, Fabrizio, Rinelli, Gabriele
سنة النشر: 2022
المجموعة: Sapienza Università di Roma: CINECA IRIS
مصطلحات موضوعية: Double-outlet left ventricle, ecocardiography, congenital cardiac malformation
الوصف: Double-outlet left ventricle (DOLV) is an abnormal ventriculo-arterial connection characterized by origin of both great arteries, or more than 50% of each arterial root, from the morphological left ventricle. The aim of our paper is to describe the anatomic, echocardiographic, and multi-modality imaging characteristics of DOLV and associated malformations, and to assess its surgical outcomes. Methods: From 2011 to 2022, we retrospectively reviewed case records, intra-operatory reports and follow-up data of patients diagnosed with DOLV at Bambino Gesu Children’s Hospital. A systematic search was developed in MEDLINE, EMBASE and Web of Science databases, to identify original reports between January 1, 1975 and May 30, 2022, assessing the morphology and surgical outcomes of DOLV. Retrospective cohort studies, cross-sectional and case series were included in the analysis. Single case reports and reviews were excluded. Results: At our center, four cases of DOLV were identified. Patient 1 was diagnosed with (S,D,D) DOLV and hypoplastic right ventricle. The aorta overrode a large, doubly-committed VSD with absence of infundibular septum. A tenuous mitro-aortic discontinuity and a well-developed subpulmonary conus were present. Associated abnormalities included crossed pulmonary arteries and two adjacent, side-by-side coronary ostia, located in the anterior facing sinus, which gave origin to the left anterior descending (LAD) and the right coronary artery (RCA). Left circumflex artery (LCx) had a retro-aortic course and originated from the RCA. After pulmonary artery banding, Damus-Kaye-Stansel and Glenn intervention were proposed as first-stage of univentricular palliation. Patient 2 and 3 were diagnosed with (S,D,D) DOLV, subaortic VSD and pulmonary stenosis. Patient 2 underwent Rastelli operation and no anatomic detail were available. Patient 3 showed absence of the infundibular septum and mitro-pulmonary continuity, whereas subaortic conus was well developed. Anomalous origin of the LCx, originating from the ...
نوع الوثيقة: conference object
اللغة: English
Relation: Italian Society of Paediatric Cardiology SICPED 27-29 October 2022; https://hdl.handle.net/11573/1673652
الاتاحة: https://hdl.handle.net/11573/1673652
رقم الانضمام: edsbas.23B4BA18
قاعدة البيانات: BASE