A 32-year-old female with a history of hypertension and paroxysmal supraventricular tachycardia (PSVT) presented with a 63×39 mm, well-circumscribed retroperitoneal mass found by ultrasonography and abdominal computed tomography (CT). CT revealed a round, homogeneous tumor with calcification at the left renal hilum, and compressing the left adrenal and renal veins. Endocrinological examinations were within the normal range. Transabdominal laparoscopic excision of the retroperitoneal mass was planned because tumor malignancy could not be excluded by preoperative analyses. Histopathological examination proved that the tumor was a ganglioneuroma arising from the extra-adrenal retroperitoneum.