Neglected right diaphragmatic hernia with transthoracic herniation of gallbladder and malrotated left liver lobe in an adult

التفاصيل البيبلوغرافية
العنوان: Neglected right diaphragmatic hernia with transthoracic herniation of gallbladder and malrotated left liver lobe in an adult
المؤلفون: Mohammed A. Neimatallah, Mazen A. Alshahrani, Fahd A. Alshehri
المصدر: Radiology Case Reports, Vol 15, Iss 10, Pp 1792-1794 (2020)
Radiology Case Reports
بيانات النشر: Elsevier, 2020.
سنة النشر: 2020
مصطلحات موضوعية: lcsh:Medical physics. Medical radiology. Nuclear medicine, medicine.medical_specialty, Gastrointestinal, Cholangitis, medicine.medical_treatment, Gallbladder Herniation, lcsh:R895-920, Diaphragmatic breathing, Diaphragmatic Hernia, Liver transplantation, 030218 nuclear medicine & medical imaging, Primary sclerosing cholangitis, Right hemithorax, 03 medical and health sciences, 0302 clinical medicine, medicine, Radiology, Nuclear Medicine and imaging, Diaphragmatic hernia, Adult patients, business.industry, Liver Malrotation, Gallbladder, Primary Sclerosing, medicine.disease, Surgery, medicine.anatomical_structure, Left liver lobe, business, 030217 neurology & neurosurgery
الوصف: Diaphragmatic hernias are commonly encountered in radiological practice, especially in pediatric patients. Delayed presentation of diaphragmatic hernias can occur in children and less frequently in adult patients. We present an extremely rare case of a 15-year-old male patient with recurrent attacks of cholestatic hepatitis who has been misdiagnosed to have primary sclerosing cholangitis and was planned for liver transplantation. On imaging, the patient was found to have neglected right diaphragmatic hernia causing hypogenesis of the right hemithorax and right lower lung lobe. A transthoracic herniation of gallbladder and malrotated left liver lobe is also diagnosed on imaging. Biliary dilatation with transition point at the diaphragmatic hernia neck was identified. Major hepatic anomaly such as liver malformation is an exceedingly rare case with only 3 reported cases in the literature. In our case, the patient suffered from recurrent cholestatic hepatitis and unfortunate misdiagnosis with primary sclerosing cholangitis, which have delayed his appropriate management. In addition, the patient was found to have interrupted IVC with azygos and hemiazygos continuation without evidence of heterotaxy syndrome.
اللغة: English
تدمد: 1930-0433
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::e592c7f69d03cd74b25b14706f038f20
http://www.sciencedirect.com/science/article/pii/S1930043320303460
Rights: OPEN
رقم الانضمام: edsair.doi.dedup.....e592c7f69d03cd74b25b14706f038f20
قاعدة البيانات: OpenAIRE