Therapeutic Blockade of Immune Complex-Mediated Glomerulonephritis by Highly Selective Inhibition of Bruton’s Tyrosine Kinase

التفاصيل البيبلوغرافية
العنوان: Therapeutic Blockade of Immune Complex-Mediated Glomerulonephritis by Highly Selective Inhibition of Bruton’s Tyrosine Kinase
المؤلفون: Christian Harcken, Meera Ramanujam, Sara Khalil, Leal Herlitz, Todd Bosanac, Janice Dimock, Elliott Klein, Samantha A. Chalmers, Jessica Doerner, Deborah Webb, Jay S. Fine, Elise Seccareccia, Chaim Putterman, Di Feng, Evan Der, Dustin Smith
المصدر: Scientific Reports
بيانات النشر: Nature Publishing Group, 2016.
سنة النشر: 2016
مصطلحات موضوعية: 0301 basic medicine, Immunology, Lupus nephritis, Antigen-Antibody Complex, Pharmacology, Kidney, Article, Proinflammatory cytokine, 03 medical and health sciences, Mice, 0302 clinical medicine, immune system diseases, hemic and lymphatic diseases, medicine, Agammaglobulinaemia Tyrosine Kinase, Immunology and Allergy, Bruton's tyrosine kinase, Animals, Enzyme Inhibitors, Multidisciplinary, biology, business.industry, Sequence Analysis, RNA, Gene Expression Profiling, Glomerulonephritis, Complement C3, Protein-Tyrosine Kinases, medicine.disease, Lupus Nephritis, Immune complex, Disease Models, Animal, 030104 developmental biology, medicine.anatomical_structure, Treatment Outcome, biology.protein, Cytokines, business, Tyrosine kinase, Nephritis, Blood Chemical Analysis, 030215 immunology
الوصف: Lupus nephritis (LN) is a potentially dangerous end organ pathology that affects upwards of 60% of SLE patients. Bruton’s tyrosine kinase (BTK) is important for B cell development, Fc receptor signaling, and macrophage polarization. In this study, we investigated the effects of a novel, highly selective and potent BTK inhibitor, BI-BTK-1, in an inducible model of LN in which mice receive nephrotoxic serum (NTS) containing anti-glomerular antibodies. Mice were treated once daily with vehicle alone or BI-BTK-1 (0.3–10 mg/kg, n=16/group), either prophylactically or therapeutically. When compared with control treated mice, NTS-challenged mice treated prophylactically with BI-BTK-1 exhibited significantly attenuated disease which was dose dependent, as measured by proteinuria, serum creatinine, and serum BUN. Histological assessment confirmed marked renal protection in the BI-BTK-1 treatment groups. BI-BTK-1 treatment resulted in decreased recruitment of inflammatory monocytes from the splenic reservoir, and a decrease in infiltrating IBA-1+ cells, as well as C3 deposition, within the kidney. RT-PCR on whole kidney RNA and serum profiling indicated that BTK inhibition significantly decreased levels of LN-relevant inflammatory cytokines and chemokines. Renal RNA expression profiling by RNA-seq revealed that BI-BTK-1 dramatically modulated pathways related to inflammation and glomerular injury. Importantly, when administered therapeutically, BI-BTK-1 reversed established proteinuria and improved renal histopathology. Our results highlight the important role for BTK in the pathogenesis of immune complex-mediated nephritis, and BTK inhibition as a promising therapeutic target for LN.
اللغة: English
تدمد: 2045-2322
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::7d2dc162780d57e517fbf0fa23f280c6
http://europepmc.org/articles/PMC4872164
Rights: OPEN
رقم الانضمام: edsair.doi.dedup.....7d2dc162780d57e517fbf0fa23f280c6
قاعدة البيانات: OpenAIRE