A case of C3 glomerulopathy with nephritis-associated plasmin receptor positivity without a history of streptococcal infection

التفاصيل البيبلوغرافية
العنوان: A case of C3 glomerulopathy with nephritis-associated plasmin receptor positivity without a history of streptococcal infection
المؤلفون: Marina Asano, Takashi Oda, Masashi Mizuno
المصدر: CEN Case Rep
بيانات النشر: Springer Science and Business Media LLC, 2021.
سنة النشر: 2021
مصطلحات موضوعية: Male, Pathology, medicine.medical_specialty, Nephritis, Adolescent, Receptors, Peptide, business.industry, C3 Glomerulonephritis, Case Report, Glomerulonephritis, General Medicine, medicine.disease, Glomerulopathy, Streptococcal Infections, Group A streptococcal infection, Membranoproliferative glomerulonephritis, medicine, Humans, Female, Microscopic hematuria, business, Nephrotic syndrome, Hematuria
الوصف: A 17-year-old lady was diagnosed with proteinuria and microscopic hematuria within the prior 2 years to this presentation. Further tests revealed nephrotic syndrome with hematuria and hypocomplementemia. Renal histopathology showed membranoproliferative glomerulonephritis. Immunostaining and electron microscopy, suggested C3 glomerulonephritis (C3GN). Nephritis-associated plasmin receptor (NAPlr) and plasmin activity (PA), markers of infection-related glomerulonephritis, were identified in the aforementioned pathology specimens. There are several reports suggesting a causal relationship between group A streptococcal infection and C3 glomerulopathy (C3G). There are many intractable cases, whereas some have responded to immunosuppressive therapy, as did our case. However, there is currently no established gold standard treatment for this disease. We herein report a case of C3G with glomerular positive NAPlr and PA despite the absence of a streptococcal infection. Accumulation of cases such as this may help advance treatment by clarifying the etiology and pathogenic mechanism of C3G and future prognosis. SUPPLEMENTARY INFORMATION: The online version contains supplementary material available at 10.1007/s13730-021-00662-2.
تدمد: 2192-4449
DOI: 10.1007/s13730-021-00662-2
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::5189bac15d898a6b47af32791e49ab3c
https://doi.org/10.1007/s13730-021-00662-2
Rights: OPEN
رقم الانضمام: edsair.doi.dedup.....5189bac15d898a6b47af32791e49ab3c
قاعدة البيانات: OpenAIRE
الوصف
تدمد:21924449
DOI:10.1007/s13730-021-00662-2