Traqueobroncomegalia y bronquiectasias en el síndrome de Mouniere-Kuhn. Colonización por Pseudomonas aeruginosa y antibioterapia inhalada
العنوان: | Traqueobroncomegalia y bronquiectasias en el síndrome de Mouniere-Kuhn. Colonización por Pseudomonas aeruginosa y antibioterapia inhalada |
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المؤلفون: | M. Zuil Martín, F. Villegas Fernández, T. Gutiérrez Jiménez, J. Jareño Esteban, J.I. de Granda Orive, S. Campos Téllez |
المصدر: | Revista de Patología Respiratoria. 13:127-129 |
بيانات النشر: | Elsevier BV, 2010. |
سنة النشر: | 2010 |
مصطلحات موضوعية: | Pulmonary and Respiratory Medicine |
الوصف: | Resumen El sindrome de Mouniere-Kuhn se caracteriza por bronquiectasias (BQ) congenitas asociadas a traqueobroncomegalia. Es una enfermedad poco prevalente en la poblacion general (1–4,5%), siendo infrecuente el diagnostico en la edad adulta. Las infecciones respiratorias constituyen una complicacion frecuente en su evolucion y entre ellas, la infeccion y colonizacion por Pseudomona aeruginosa . La terapia antibiotica inhalada con colistina, tobramicina, etc. ha demostrado su eficacia en pacientes con BQ asociadas a fibrosis quistica. La instauracion de este tratamiento en nuestro caso se asocio con una mejoria en la sintomatologia clinica y reduccion de las exacerbaciones. |
تدمد: | 1576-9895 |
DOI: | 10.1016/s1576-9895(10)70005-9 |
URL الوصول: | https://explore.openaire.eu/search/publication?articleId=doi_________::fe78f7e524236eb8e1d9e5a11b92506f https://doi.org/10.1016/s1576-9895(10)70005-9 |
Rights: | CLOSED |
رقم الانضمام: | edsair.doi...........fe78f7e524236eb8e1d9e5a11b92506f |
قاعدة البيانات: | OpenAIRE |
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