Traqueobroncomegalia y bronquiectasias en el síndrome de Mouniere-Kuhn. Colonización por Pseudomonas aeruginosa y antibioterapia inhalada

التفاصيل البيبلوغرافية
العنوان: Traqueobroncomegalia y bronquiectasias en el síndrome de Mouniere-Kuhn. Colonización por Pseudomonas aeruginosa y antibioterapia inhalada
المؤلفون: M. Zuil Martín, F. Villegas Fernández, T. Gutiérrez Jiménez, J. Jareño Esteban, J.I. de Granda Orive, S. Campos Téllez
المصدر: Revista de Patología Respiratoria. 13:127-129
بيانات النشر: Elsevier BV, 2010.
سنة النشر: 2010
مصطلحات موضوعية: Pulmonary and Respiratory Medicine
الوصف: Resumen El sindrome de Mouniere-Kuhn se caracteriza por bronquiectasias (BQ) congenitas asociadas a traqueobroncomegalia. Es una enfermedad poco prevalente en la poblacion general (1–4,5%), siendo infrecuente el diagnostico en la edad adulta. Las infecciones respiratorias constituyen una complicacion frecuente en su evolucion y entre ellas, la infeccion y colonizacion por Pseudomona aeruginosa . La terapia antibiotica inhalada con colistina, tobramicina, etc. ha demostrado su eficacia en pacientes con BQ asociadas a fibrosis quistica. La instauracion de este tratamiento en nuestro caso se asocio con una mejoria en la sintomatologia clinica y reduccion de las exacerbaciones.
تدمد: 1576-9895
DOI: 10.1016/s1576-9895(10)70005-9
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_________::fe78f7e524236eb8e1d9e5a11b92506f
https://doi.org/10.1016/s1576-9895(10)70005-9
Rights: CLOSED
رقم الانضمام: edsair.doi...........fe78f7e524236eb8e1d9e5a11b92506f
قاعدة البيانات: OpenAIRE
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