Academic Journal

Rehabilitation Strategies for Patients With Spinal Muscular Atrophy in the Era of Disease-Modifying Therapy.

التفاصيل البيبلوغرافية
العنوان: Rehabilitation Strategies for Patients With Spinal Muscular Atrophy in the Era of Disease-Modifying Therapy.
المؤلفون: Shin, Hyung-Ik1 hyungik1@snu.ac.kr
المصدر: Annals of Rehabilitation Medicine. Aug2024, Vol. 48 Issue 4, p229-238. 10p.
مصطلحات موضوعية: *SPINAL muscular atrophy, *BOTTLE feeding, *CONTRACTURE (Pathology), *ORTHOPEDIC braces, *MUSCLE strength, *ADOLESCENT idiopathic scoliosis, *LORDOSIS, *INFANT development, *FEEDING tubes
مستخلص: The impact of disease-modifying therapy ranges from cure to no impact with a wide range of intermediates. In cases where the intermediate group reaches a plateau after the acquisition of some muscle strength, it is necessary to set a functional level appropriate for increased motor power and establish a long-term exercise plan to maintain it. As the disease status stabilizes and the life span increases, early nonsurgical interventions are required, such as using a standing frame to prevent joint contracture, applying a spinal brace at the early stage of scoliosis, and maintaining sitting postures that exaggerate lumbar lordosis. In cases where scoliosis and hip displacement occur and progress even after conservative managements are implemented, early referral to surgery should be considered. Oromotor activity and swallowing function are influenced not only by the effects of disease-modifying drugs, but also by post-birth experience and training. Therefore, although the feeding tube cannot be removed, it is necessary to make efforts to simulate the infant feeding development while maintaining partial oral feeding. Since the application period of non-invasive ventilators has increased, it has become more important to prevent long-term complications such as facial abrasion, skin allergy, orthodontic deformities, and maxillary flattening caused by the interface. Dual ventilator mode or interface can also be utilized. [ABSTRACT FROM AUTHOR]
قاعدة البيانات: Academic Search Index
الوصف
تدمد:22340645
DOI:10.5535/arm.240046