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المؤلفون: Ya Fei Xu, Jeannie Chew, Jonathan C. Grima, Kevin B. Boylan, Amanda M. Liesinger, Wen Lang Lin, Chad A. Dickey, Guojun Bu, Christopher D. Link, Jennifer Gass, Yong Jie Zhang, Zizhao S. Wang, Aliesha Garrett, Emilie A. Perkerson, Jeremy D. Baker, Hiroki Sasaguri, Jeannette N. Stankowski, Mei Yue, Clotilde Lagier-Tourenne, Rebecca B. Katzman, Leonard Petrucelli, Jie Jiang, John D. Fryer, Tania F. Gendron, Karen Jansen-West, Monica Castanedes-Casey, Lillian M. Daughrity, Jimei Tong, Aishe Kurti, Dieter Edbauer, Dennis W. Dickson, Mitsuru Shinohara, Melissa E. Murray, Jeffrey D. Rothstein, Don W. Cleveland, Rosa Rademakers
المصدر: Nature reviews / Neuroscience 19(5), 668-677 (2016). doi:10.1038/nn.4272
Nature neuroscience, vol 19, iss 5
Nature neuroscienceمصطلحات موضوعية: 0301 basic medicine, metabolism [Inclusion Bodies], Gene Expression, Neurodegenerative, Inclusion bodies, Mice, genetics [Gene Expression], 0302 clinical medicine, pathology [Brain], C9orf72, Gene expression, Psychology, pathology [Neurons], Guanine Nucleotide Exchange Factors, ultrastructure [Inclusion Bodies], Neurons, Inclusion Bodies, C9orf72 protein, mouse, pathology [Atrophy], Behavior, Animal, General Neuroscience, Nucleocytoplasmic Transport Proteins, Neurodegeneration, Brain, pathology [Nerve Degeneration], metabolism [Proteins], Ubiquitinated Proteins, DNA-Binding Proteins, poly(glycyl-alanyl), Xpc protein, mouse, metabolism [Neurons], Frontotemporal Dementia, metabolism [Frontotemporal Dementia], Cognitive Sciences, Rad23a protein, mouse, metabolism [DNA-Binding Proteins], metabolism [Ubiquitinated Proteins], metabolism [Guanine Nucleotide Exchange Factors], Primary Cell Culture, Biology, Rad23b protein, mouse, DNA-binding protein, Article, 03 medical and health sciences, TDP-43 protein, mouse, ddc:570, Acquired Cognitive Impairment, medicine, Animals, Humans, pathology [Amyotrophic Lateral Sclerosis], Behavior, Neurology & Neurosurgery, C9orf72 Protein, toxicity [Proteins], Animal, metabolism [Amyotrophic Lateral Sclerosis], Amyotrophic Lateral Sclerosis, Neurosciences, Proteins, medicine.disease, genetics [Proteins], Brain Disorders, 030104 developmental biology, metabolism [Brain], Nucleocytoplasmic Transport, Nerve Degeneration, pathology [Frontotemporal Dementia], Mutation, ultrastructure [Brain], Dementia, Human medicine, Atrophy, Carrier Proteins, Neuroscience, 030217 neurology & neurosurgery, metabolism [Carrier Proteins]
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