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1
المؤلفون: Haibo Wang, Daogong Zhang, Na Zhang, Lei Xu, Zhibing Zhang, Jerome F. Strauss, Wenwen Liu, Xiaofei Li
المصدر: Journal of Pharmacological Sciences, Vol 147, Iss 4, Pp 325-330 (2021)
مصطلحات موضوعية: Axoneme, Male, Stereocilia (inner ear), Mice, Transgenic, Apoptosis, RM1-950, Biology, Vestibular Nerve, Hair cells, Hair Cells, Vestibular, Hearing, medicine, otorhinolaryngologic diseases, Animals, Inner ear, Vestibular dysfunction, Sperm-associated antigen 6, Cochlea, Vestibular Hair Cell, Pharmacology, Vestibular system, Cell Polarity, Scarpa's ganglion cells, Cell biology, Crista, medicine.anatomical_structure, Vestibular Diseases, Vestibule, Mutation, Microtubule Proteins, Molecular Medicine, Female, sense organs, Therapeutics. Pharmacology
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2
المؤلفون: Eva Trevisson, Alessandro Martini, Valeria Brasson, Chiara Rigon, Ugo Sorrentino, Matteo Cassina, Francesca Boaretto, Chiara Piccolo
المصدر: Audiology Research
Audiology Research, Vol 11, Iss 52, Pp 582-593 (2021)مصطلحات موضوعية: Genetics, ACTG1, DFNA20, Hearing loss, Stereocilia (inner ear), DFNA26, gamma-actin, non-syndromic hearing loss, NGS, Case Report, Biology, Phenotype, Otorhinolaryngology, RF1-547, medicine, otorhinolaryngologic diseases, Missense mutation, medicine.symptom, Gene, Tinnitus, Actin
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3
المؤلفون: Erdogan Bulut, Gulnur Kizilay, Onur Ersoy, Selis Gulseven Guven, Cem Uzun, Ruhan Deniz Topuz
المصدر: Audiology and Neurotology. 27:109-121
مصطلحات موضوعية: medicine.medical_specialty, Physiology, Monosodium glutamate, Stereocilia (inner ear), Guinea Pigs, Otoacoustic Emissions, Spontaneous, Speech and Hearing, Route of administration, chemistry.chemical_compound, Internal medicine, Sodium Glutamate, Evoked Potentials, Auditory, Brain Stem, otorhinolaryngologic diseases, medicine, Animals, Cochlea, business.industry, Glutamate receptor, Perilymph, Sensory Systems, Hair Cells, Auditory, Outer, medicine.anatomical_structure, Endocrinology, Auditory brainstem response, Otorhinolaryngology, chemistry, sense organs, Hair cell, business
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4
المصدر: The Journal of Neuroscience. 41:6812-6821
مصطلحات موضوعية: Membrane potential, Chemistry, Ryanodine receptor, General Neuroscience, Stereocilia (inner ear), Glutamate receptor, Long-term potentiation, Stimulation, medicine.anatomical_structure, medicine, Biophysics, Inner ear, sense organs, Hair cell
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5
المؤلفون: Cheng Cheng, Liyan Zhang, Zhonghong Zhang, Ling Lu, Wei Xie, Pei Jiang, Chengwen Zhu, Yanfei Wang, Xia Gao, Qiaojun Fang, Junyan Gao, Zhigang Xu, Zhengping Jia, Renjie Chai, Xufeng Liu, Yilin Hou, Song Gao
المصدر: Journal of Genetics and Genomics. 48:324-332
مصطلحات موضوعية: Candidate gene, Hearing loss, Stereocilia (inner ear), Apoptosis, macromolecular substances, Deafness, Biology, Stereocilia, Mice, 03 medical and health sciences, 0302 clinical medicine, PAK1, Hair Cells, Auditory, otorhinolaryngologic diseases, Genetics, medicine, Animals, Humans, Autistic Disorder, Hearing Loss, Molecular Biology, Cochlea, 030304 developmental biology, Mice, Knockout, 0303 health sciences, Cofilin, medicine.disease, Cell biology, medicine.anatomical_structure, p21-Activated Kinases, Synapses, Autism, Hair cell, medicine.symptom, 030217 neurology & neurosurgery
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6
المؤلفون: Katharine K. Miller, Nicolas Grillet, Noor-E-Seher Ali, Alix Trouillet, Anthony J. Ricci, Pei Wang, Shefin S George
المصدر: The Journal of Neuroscience
مصطلحات موضوعية: 0301 basic medicine, PLAT domain, nonsense-associated altered splicing, Stereocilia (inner ear), Mutant, hair cell, 03 medical and health sciences, 0302 clinical medicine, Immunochemistry, otorhinolaryngologic diseases, medicine, Inner ear, Mechanotransduction, Research Articles, stereocilia, mechanotransduction, LOXHD1, integumentary system, Chemistry, General Neuroscience, Phenotype, Cell biology, 030104 developmental biology, medicine.anatomical_structure, sense organs, Hair cell, 030217 neurology & neurosurgery, Cellular/Molecular
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7
المؤلفون: Lukas Rüttiger, Stuart L. Johnson, Adam J Carlton, Kevin P. Legan, Jing-Yi Jeng, Philine Marchetta, Guy P. Richardson, Richard J. Goodyear, Laura F. Corns, Csaba Harasztosi, Walter Marcotti
المصدر: The Journal of Physiology. 599:2015-2036
مصطلحات موضوعية: 0301 basic medicine, biology, Physiology, Chemistry, Tectorial membrane, Stereocilia (inner ear), Receptor potential, Depolarization, 03 medical and health sciences, 030104 developmental biology, 0302 clinical medicine, medicine.anatomical_structure, Organ of Corti, otorhinolaryngologic diseases, medicine, Biophysics, biology.protein, sense organs, TECTA, Prestin, 030217 neurology & neurosurgery, Cochlea
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8
المؤلفون: Shi Li Zhang, Wei Guo Shi, Fei Ji, Yue Zhang, David Z.Z. He, Wei Sun, Shi Ming Yang, Tao Cong, Xin Song, Wei Wei Guo, Mian Zu
المصدر: BMC Neuroscience, Vol 22, Iss 1, Pp 1-14 (2021)
BMC Neuroscienceمصطلحات موضوعية: Hearing Loss, Sensorineural, Stereocilia (inner ear), Expression, Biology, Ribbon synapse, lcsh:RC321-571, Lesion, Mice, 03 medical and health sciences, Cellular and Molecular Neuroscience, 0302 clinical medicine, medicine, otorhinolaryngologic diseases, Animals, Auditory system, Cochlear Nerve, NAV1.9 Voltage-Gated Sodium Channel, lcsh:Neurosciences. Biological psychiatry. Neuropsychiatry, Cochlea, 030304 developmental biology, Mice, Knockout, Mice, Inbred ICR, 0303 health sciences, Progressive hearing loss, Hair Cells, Auditory, Inner, General Neuroscience, lcsh:QP351-495, medicine.disease, Nav1.9 knockout, CTBP2, Cell biology, medicine.anatomical_structure, lcsh:Neurophysiology and neuropsychology, Synaptopathy, SGN, Synapses, Sensorineural hearing loss, sense organs, medicine.symptom, Gene Deletion, 030217 neurology & neurosurgery, Research Article, TTX resistant sodium channels
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9
المؤلفون: Naoki Oishi, Kaoru Ogawa, Makoto Hosoya, Takanori Nishiyama, Chika Saegusa, Hideyuki Saya, Masato Fujioka, Tatsuhiko Harada
المصدر: Biochemical and Biophysical Research Communications. 534:921-926
مصطلحات موضوعية: Male, 0301 basic medicine, Cochlear amplifier, Stereocilia (inner ear), Biophysics, Cuticular plate, Protein Serine-Threonine Kinases, Biology, Biochemistry, 03 medical and health sciences, 0302 clinical medicine, otorhinolaryngologic diseases, medicine, Animals, Hearing Loss, Molecular Biology, Cochlea, Mice, Knockout, Hippo signaling pathway, Cell Biology, Kinocilium, Cell biology, 030104 developmental biology, medicine.anatomical_structure, Organ of Corti, 030220 oncology & carcinogenesis, Female, sense organs, Hair cell, Gene Deletion
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10
المؤلفون: Adam J Carlton, Michael R. Bowl, Julia Halford, Steve D.M. Brown, Jing-Yi Jeng, Walter Marcotti, Matthew R. Avenarius, Merle L. Gilbert, Kimimuepigha Ebisine, Peter G. Barr-Gillespie, Federico Ceriani, Anna Underhill
المصدر: The Journal of Physiology
مصطلحات موضوعية: 0301 basic medicine, Physiology, Molecular and Cellular, Stereocilia (inner ear), CDC42, Deafness, Biology, Stereocilia, Motor protein, EPS8, Mice, 03 medical and health sciences, 0302 clinical medicine, otorhinolaryngologic diseases, Animals, development, mouse, Cochlea, Actin, hearing loss, Hair Cells, Auditory, Inner, Microfilament Proteins, Membrane Proteins, mechanoelectrical transduction, Cell biology, cochlear, Hair Cells, Auditory, Outer, 030104 developmental biology, Mechanosensitive channels, sense organs, actin, Transduction (physiology), 030217 neurology & neurosurgery, Research Paper
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11
المؤلفون: Pascal Martin, M. Tobin, A. J. Hudspeth, R. G. Alonso
المساهمون: Rockefeller University [New York], Laboratoire Physico-Chimie Curie [Institut Curie] (PCC), Institut Curie [Paris]-Institut de Chimie du CNRS (INC)-Sorbonne Université (SU)-Centre National de la Recherche Scientifique (CNRS), ANR-16-CE13-0015,HAIRBUNDLEMORPH,Contrôle de la taille de la touffe ciliaire des cellules mécanosensorielles ciliées pour une détection auditive sélective en fréquence(2016), ANR-10-IDEX-0001,PSL,Paris Sciences et Lettres(2010)
المصدر: Proceedings of the National Academy of Sciences of the United States of America
Proceedings of the National Academy of Sciences of the United States of America, National Academy of Sciences, 2020, 117 (48), pp.30722-30727. ⟨10.1073/pnas.2016858117⟩مصطلحات موضوعية: [PHYS.PHYS.PHYS-BIO-PH]Physics [physics]/Physics [physics]/Biological Physics [physics.bio-ph], Stereocilia (inner ear), cochlea, Action Potentials, Stimulation, [SDV.BC.BC]Life Sciences [q-bio]/Cellular Biology/Subcellular Processes [q-bio.SC], auditory system, Mechanotransduction, Cellular, hair cell, Stereocilia, 03 medical and health sciences, 0302 clinical medicine, Bullfrog, Hair Cells, Auditory, otorhinolaryngologic diseases, medicine, Animals, [SDV.MHEP.OS]Life Sciences [q-bio]/Human health and pathology/Sensory Organs, Cochlea, Calcium Chelating Agents, Mechanical Phenomena, 030304 developmental biology, Vestibular system, 0303 health sciences, Multidisciplinary, Iontophoresis, Chemistry, vestibular system, [SCCO.NEUR]Cognitive science/Neuroscience, Biological Sciences, Electrophysiological Phenomena, Rats, cadherin, medicine.anatomical_structure, Bundle, Biophysics, Calcium, Mechanosensitive channels, sense organs, Hair cell, Transduction (physiology), Biomarkers, 030217 neurology & neurosurgery, PCDH15, Neuroscience
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12
المؤلفون: Huijun Yuan, Cuicui Wang, Xuemin Cai, Xiuqin Xu, Jing Liu, Mengkai Zhang, Longqing Zheng
المصدر: RNA Biol
مصطلحات موضوعية: Hearing loss, RNA Splicing, Stereocilia (inner ear), RNA-binding protein, Biology, Organ development, Mice, 03 medical and health sciences, 0302 clinical medicine, otorhinolaryngologic diseases, medicine, Animals, Humans, Auditory system, Inner ear, Hearing Loss, Molecular Biology, 030304 developmental biology, Mice, Knockout, 0303 health sciences, Alternative splicing, RNA-Binding Proteins, Cell Biology, Motor coordination, Alternative Splicing, HEK293 Cells, medicine.anatomical_structure, Ear, Inner, 030220 oncology & carcinogenesis, Auditory Perception, sense organs, medicine.symptom, Neuroscience, Locomotion, Psychomotor Performance, Research Paper, HeLa Cells
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13
المؤلفون: Thomas Lenarz, Gerrit Paasche, Athanasia Warnecke, Marvin N Peter, U Reich
المصدر: Neurotoxicity Research
مصطلحات موضوعية: 0301 basic medicine, medicine.medical_specialty, Hearing loss, Stereocilia (inner ear), Stimulation, Ribbon synapse, Toxicology, Dexamethasone, Stereocilia, 03 medical and health sciences, Organ Culture Techniques, 0302 clinical medicine, Internal medicine, otorhinolaryngologic diseases, medicine, Animals, Eye Proteins, Glucocorticoids, Organ of Corti, chemistry.chemical_classification, Reactive oxygen species, Microscopy, Confocal, General Neuroscience, Free radical scavenger, Immunohistochemistry, Electric Stimulation, Rats, Neuroprotective Agents, 030104 developmental biology, Endocrinology, medicine.anatomical_structure, chemistry, Synapses, Original Article, sense organs, medicine.symptom, 030217 neurology & neurosurgery, medicine.drug
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14
المؤلفون: Anna Shipman, Matthew Hill, Teresa Nicolson, Eliot T Smith, Itallia V. Pacentine
المصدر: The Journal of Neuroscience. 40:4457-4468
مصطلحات موضوعية: 0301 basic medicine, Vestibular system, Cell type, Mechanosensation, General Neuroscience, Stereocilia (inner ear), Protocadherin, Biology, biology.organism_classification, Transmembrane protein, Cell biology, 03 medical and health sciences, 030104 developmental biology, 0302 clinical medicine, medicine.anatomical_structure, otorhinolaryngologic diseases, medicine, Inner ear, sense organs, Zebrafish, 030217 neurology & neurosurgery
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15
المؤلفون: Bernd Fritzsch
المصدر: Diversity, Vol 13, Iss 364, p 364 (2021)
مصطلحات موضوعية: hair cells, QH301-705.5, Stereocilia (inner ear), neurons, Sensory system, Biology, Vestibular nuclei, otorhinolaryngologic diseases, medicine, Auditory system, Biology (General), Sox2, Nature and Landscape Conservation, Vestibular system, bHLH genes, brainstem nuclei, Ecology, Electroreception, Ecological Modeling, Agricultural and Biological Sciences (miscellaneous), Eya1, medicine.anatomical_structure, Auditory nuclei, sense organs, Brainstem, Neuroscience
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16
المؤلفون: Lisa L. Cunningham, Inna A. Belyantseva, Meghan C. Drummond, Thomas B. Friedman, Sherri M. Jones, Tracy S. Fitzgerald, Wade W. Chien, Andrew J. Griffith, Kevin Isgrig, Sarath Vijayakumar, Jack W. Shteamer
المصدر: Mol Ther
مصطلحات موضوعية: 0301 basic medicine, Hearing loss, Genetic enhancement, Stereocilia (inner ear), Usher syndrome, Gene Expression, medicine.disease_cause, Stereocilia, 03 medical and health sciences, Mice, Hearing, Drug Discovery, otorhinolaryngologic diseases, Genetics, medicine, Animals, Humans, Inner ear, Molecular Biology, Postural Balance, Pharmacology, Mice, Knockout, Mutation, Hair Cells, Auditory, Inner, Behavior, Animal, business.industry, Posterior Semicircular Canal, Hearing Tests, Correction, Membrane Proteins, Anatomy, Genetic Therapy, medicine.disease, Disease Models, Animal, 030104 developmental biology, medicine.anatomical_structure, Phenotype, Molecular Medicine, Original Article, sense organs, Hair cell, medicine.symptom, business, Neuroscience, Usher Syndromes
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17
المؤلفون: Nicolas Grillet, Kyssia Ruth Mendoza, Dáibhid Ó Maoiléidigh, Katharine K. Miller, Patrick J. Atkinson
المصدر: Frontiers in Cell and Developmental Biology, Vol 9 (2021)
Frontiers in Cell and Developmental Biologyمصطلحات موضوعية: QH301-705.5, Stereocilia (inner ear), Sensory system, Fluorescent imaging, hair cell, Cell and Developmental Biology, deafness, otorhinolaryngologic diseases, medicine, Electronic microscopy, Biology (General), Mechanotransduction, Postnatal day, stereocilia, mouse, Original Research, hearing loss, mechanotransduction, electron microscopy, integumentary system, Chemistry, hair bundle, Cell Biology, medicine.anatomical_structure, Bundle, Biophysics, sense organs, Hair cell, Developmental Biology
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18Conserved and Divergent Principles of Planar Polarity Revealed by Hair Cell Development and Function
المؤلفون: Michael R. Deans
المصدر: Frontiers in Neuroscience
Frontiers in Neuroscience, Vol 15 (2021)مصطلحات موضوعية: Vestibular system, vestibular, Mechanosensation, Polarity (physics), Chemistry, Stereocilia (inner ear), General Neuroscience, Neurosciences. Biological psychiatry. Neuropsychiatry, Review, Sensory receptor, hair cell, medicine.anatomical_structure, otorhinolaryngologic diseases, medicine, Inner ear, auditory, sense organs, Hair cell, Neuroscience, planar cell polarity (PCP), planar polarity, Vestibular Hair Cell, RC321-571
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19
المؤلفون: Hailong Tu, Aizhen Zhang, Xiaolong Fu, Shiqi Xu, Xiaohui Bai, Haibo Wang, Jiangang Gao
المصدر: Frontiers in Cell and Developmental Biology
Frontiers in Cell and Developmental Biology, Vol 9 (2021)مصطلحات موضوعية: Programmed cell death, medicine.medical_specialty, QH301-705.5, Hearing loss, Stereocilia (inner ear), Degeneration (medical), Biology, hair cell, Frameshift mutation, Cell and Developmental Biology, Internal medicine, medicine, otorhinolaryngologic diseases, Biology (General), Original Research, hearing loss, Point mutation, Cell Biology, medicine.anatomical_structure, Auditory brainstem response, Endocrinology, Smpx, stereocilia degeneration, Hair cell, medicine.symptom, CRISPR-Cas9, Developmental Biology
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20
المؤلفون: Atsushi Tamura, Kazuo Oshima, Kazuya Ohata, Masahide Takahashi, Yumi Ohta, Maki Takagishi, Shogo Nakayama, Takao Imai, Yukiko Hanada, Elisa Herawati, Hidenori Inohara, Sachiko Tsukita, Takashi Sato, Yoshiyuki Ozono
المصدر: Scientific Reports
Scientific Reports, Vol 11, Iss 1, Pp 1-12 (2021)مصطلحات موضوعية: Cell biology, Hearing loss, Science, Stereocilia (inner ear), Cochlear duct, Biology, Microtubules, Article, Stereocilia, Gene Knockout Techniques, Mice, chemistry.chemical_compound, Organ Culture Techniques, Microtubule, Developmental biology, Morphogenesis, Evoked Potentials, Auditory, Brain Stem, otorhinolaryngologic diseases, medicine, Animals, Hearing Loss, Cochlea, Multidisciplinary, Nocodazole, Cell Membrane, Kinocilium, Disease Models, Animal, medicine.anatomical_structure, Auditory brainstem response, chemistry, Cell polarity, Microscopy, Electron, Scanning, Medicine, sense organs, medicine.symptom, Carrier Proteins