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1Academic Journal
المؤلفون: A. Daly, A. Pinto, S. Evans, M.F. Almeida, M. Assoun, A. Belanger-Quintana, S.M. Bernabei, S. Bollhalder, D. Cassiman, H. Champion, H. Chan, J. Dalmau, F. de Boer, C. de Laet, A. de Meyer, A. Desloovere, A. Dianin, M. Dixon, K. Dokoupil, S. Dubois, F. Eyskens, A. Faria, I. Fasan, E. Favre, F. Feillet, A. Fekete, G. Gallo, C. Gingell, J. Gribben, K. Kaalund Hansen, N.M. Ter Horst, C. Jankowski, R. Janssen-Regelink, I. Jones, C. Jouault, G.E. Kahrs, I.L. Kok, A. Kowalik, C. Laguerre, S. Le Verge, R. Lilje, C. Maddalon, D. Mayr, U. Meyer, A. Micciche, U. Och, M. Robert, J.C. Rocha, H. Rogozinski, C. Rohde, K. Ross, I. Saruggia, A. Schlune, K. Singleton, E. Sjoqvist, R. Skeath, L.H. Stolen, A. Terry, C. Timmer, L. Tomlinson, A. Tooke, K. Vande Kerckhove, E. van Dam, T. van den Hurk, L. van der Ploeg, M. van Driessche, M. van Rijn, A. van Wegberg, C. Vasconcelos, H. Vestergaard, I. Vitoria, D. Webster, F.J. White, L. White, H. Zweers, A. MacDonald
المصدر: Molecular Genetics and Metabolism Reports, Vol 13, Iss C, Pp 83-89 (2017)
مصطلحات موضوعية: Propionic acidemia, Protein restricted diet, Precursor-free amino acids, Natural protein, Medicine (General), R5-920, Biology (General), QH301-705.5
وصف الملف: electronic resource
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2Academic Journal
المؤلفون: A. Pinto, A. Daly, S. Evans, M.F. Almeida, M. Assoun, A. Belanger-Quintana, S. Bernabei, S. Bollhalder, D. Cassiman, H. Champion, H. Chan, J. Dalmau, F. de Boer, C. de Laet, A. de Meyer, A. Desloovere, A. Dianin, M. Dixon, K. Dokoupil, S. Dubois, F. Eyskens, A. Faria, I. Fasan, E. Favre, F. Feillet, A. Fekete, G. Gallo, C. Gingell, J. Gribben, K. Kaalund-Hansen, N. Horst, C. Jankowski, R. Janssen-Regelink, I. Jones, C. Jouault, G.E. Kahrs, I.L. Kok, A. Kowalik, C. Laguerre, S. Le Verge, R. Lilje, C. Maddalon, D. Mayr, U. Meyer, A. Micciche, M. Robert, J.C. Rocha, H. Rogozinski, C. Rohde, K. Ross, I. Saruggia, A. Schlune, K. Singleton, E. Sjoqvist, L.H. Stolen, A. Terry, C. Timmer, L. Tomlinson, A. Tooke, K. Vande Kerckhove, E. van Dam, T. van den Hurk, L. van der Ploeg, M. van Driessche, M. van Rijn, A. van Teeffelen-Heithoff, A. van Wegberg, C. Vasconcelos, H. Vestergaard, I. Vitoria, D. Webster, F.J. White, L. White, H. Zweers, A. MacDonald
المصدر: Molecular Genetics and Metabolism Reports, Vol 12, Iss C, Pp 16-22 (2017)
مصطلحات موضوعية: Isovaleric acidemia, Protein restricted diet, Leucine, Leucine free l-amino acids, Natural protein, Medicine (General), R5-920, Biology (General), QH301-705.5
وصف الملف: electronic resource
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المؤلفون: H. Vestergaard, Júlio César Rocha, Joanna Gribben, Sylvain Dubois, Clara Vasconcelos, H. Zweers, U. Meyer, C. Maritz, M. Heddrich-Ellerbrok, S.M. Bernabei, K. Va nde Kerckhove, F.J. White, S. Adam, C. Jankowski, I. Saruggia, S. Bigot, A. van Teeffelen-Heithoff, R. Link, A. Terry, J. Wildgoose, J. Baruteau, François Eyskens, K. van Wyk, R.G. Janssen-Regelink, C. Ferguson, A.M.J. van Wegberg, M. Robert, C. Laguerre, K. Luyten, Marjorie Dixon, R. Thom, Louise Robertson, S. Dawson, Anne Daly, Katharina Dokoupil, Carolyn Dunlop, Anita MacDonald, A. Faria, S. Lowry, M.F. Almeida, E. Favre, M. van Rijn, M. Dassy, E. Sjoqvist, H. Champion, C. Jouault, S. McDowell, Carmen Rohde, S. Le Verge, Sharon Evans, J. Stafford, M. Assoun, Carolina Gonçalves, D. Webster, A. Micciche
المساهمون: Faculteit Medische Wetenschappen/UMCG
المصدر: Molecular Genetics and Metabolism, 110, 4, pp. 439-45
Molecular genetics and metabolism
Molecular Genetics and Metabolism, 110, 439-45
Molecular Genetics and Metabolism, 110(4), 439-445. ACADEMIC PRESS INC ELSEVIER SCIENCEمصطلحات موضوعية: Adult, medicine.medical_specialty, Pediatrics, Adolescent, Endocrinology, Diabetes and Metabolism, Amino-Acid N-Acetyltransferase, Argininosuccinic Aciduria, MULTICENTER, Branch chain amino acids (BCAA), Body weight, DIAGNOSIS, Biochemistry, THERAPY, Endocrinology, Urea cycle disorders (UCD), Internal medicine, Surveys and Questionnaires, Genetics, medicine, Diet, Protein-Restricted, Humans, Molecular gastro-enterology and hepatology [IGMD 2], Child, Molecular Biology, Urea Cycle Disorders, Inborn, Ornithine Carbamoyltransferase, Total protein, Citrullinemia, Arginase, business.industry, Metabolic disorder, Dietary management, Infant, Newborn, Protein restricted diet, Infant, medicine.disease, Europe, Treatment Outcome, Argininosuccinic aciduria, Dietary treatment, Urea cycle, Child, Preschool, Amino Acids, Essential, Carbon-Nitrogen Ligases with Glutamine as Amide-N-Donor, Human medicine, Metabolic, business, Essential amino acids (EAA)
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المؤلفون: S. Le Verge, J.M. Ricard, Nathalie Moutier
المساهمون: ProdInra, Migration, Amélioration génétique et adaptation des plantes méditerranéennes et tropicales (UMR AGAP), Institut National de la Recherche Agronomique (INRA)-Institut national d’études supérieures agronomiques de Montpellier (Montpellier SupAgro), Institut national d'enseignement supérieur pour l'agriculture, l'alimentation et l'environnement (Institut Agro)-Institut national d'enseignement supérieur pour l'agriculture, l'alimentation et l'environnement (Institut Agro)-Centre international d'études supérieures en sciences agronomiques (Montpellier SupAgro)-Centre de Coopération Internationale en Recherche Agronomique pour le Développement (Cirad), Centre de Balandran, Centre Technique Interprofessionnel des Fruits et Légumes (CTIFL), Centre technique de l’olivier, maison des agriculteurs, Partenaires INRAE, International Society for Horticultural Science (ISHS). INT.
المصدر: Acta Horticulturae
IHC2010
IHC2010, International Society for Horticultural Science (ISHS). INT., Aug 2010, Lisbonne, Portugal. 9 pمصطلحات موضوعية: 0106 biological sciences, 2. Zero hunger, [SPI.GPROC] Engineering Sciences [physics]/Chemical and Process Engineering, pruning, Sowing, tree management, olea europaea L, 04 agricultural and veterinary sciences, 15. Life on land, Horticulture, [SDV.IDA] Life Sciences [q-bio]/Food engineering, 01 natural sciences, Tree (data structure), Agronomy, [SDV.IDA]Life Sciences [q-bio]/Food engineering, 040103 agronomy & agriculture, 0401 agriculture, forestry, and fisheries, [SPI.GPROC]Engineering Sciences [physics]/Chemical and Process Engineering, genotype characterization, 010606 plant biology & botany, Mathematics