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1Academic Journal
المؤلفون: Dharmesh V. Hirani, Florian Thielen, Siavash Mansouri, Soula Danopoulos, Christina Vohlen, Pinar Haznedar-Karakaya, Jasmine Mohr, Rebecca Wilke, Jaco Selle, Thomas Grosch, Ivana Mizik, Margarete Odenthal, Cristina M. Alvira, Celien Kuiper-Makris, Gloria S. Pryhuber, Christian Pallasch, S. van Koningsbruggen-Rietschel, Denise Al-Alam, Werner Seeger, Rajkumar Savai, Jörg Dötsch, Miguel A. Alejandre Alcazar
المصدر: Inflammation and Regeneration, Vol 43, Iss 1, Pp 1-20 (2023)
مصطلحات موضوعية: CXCL10, Hyperoxia, Elastic fibers, Collagen, Lung matrix remodeling, Bronchopulmonary dysplasia, Pathology, RB1-214
وصف الملف: electronic resource
Relation: https://doaj.org/toc/1880-8190
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2Academic JournalThe effect of TGF-β1 polymorphisms on pulmonary disease progression in patients with cystic fibrosis
المؤلفون: T. Trojan, Miguel A. Alejandre Alcazar, G. Fink, J. C. Thomassen, M. V. Maessenhausen, E. Rietschel, P. M. Schneider, S. van Koningsbruggen-Rietschel
المصدر: BMC Pulmonary Medicine, Vol 22, Iss 1, Pp 1-10 (2022)
مصطلحات موضوعية: Transforming-growth-factor Beta 1 (TGF-β1), Cystic fibrosis, Polymorphisms, Inflammation, Forced expiratory volume in one second (FEV1), Pseudomonas aeruginosa, Diseases of the respiratory system, RC705-779
وصف الملف: electronic resource
Relation: https://doaj.org/toc/1471-2466
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المؤلفون: JC Thomassen, R Körner, M Meyer, A Striegel, E Rietschel, S van Koningsbruggen-Rietschel
المصدر: Klinische Pädiatrie.
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4
المؤلفون: J. C. Thomassen, M. Meyer, L. Hagmeyer, A. K. Striegel, F. Metz, R. Körner, E. Rietschel, S. van Koningsbruggen-Rietschel
المصدر: Monatsschrift Kinderheilkunde.
مصطلحات موضوعية: Pediatrics, Perinatology and Child Health, Surgery
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5
المؤلفون: B. Schwartbeck, C. Rumpf, R. Hait, C. Decker, T. Janssen, K. Romme, A. Dübbers, P. Küster, U. Graepler-Mainka, H. Hebestreit, S. Van-Koningsbruggen-Rietschel, S. Renner, B. Wollschläger, S. Naehrig, F. Stehling, A. Schlegtendahl, M. Ballmann, S. Junge, S. Sutharsan, B. Kahl
المصدر: Journal of Cystic Fibrosis. 21:S299
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Pediatrics, Perinatology and Child Health
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المؤلفون: C. Rumpf, B. Schwartbeck, R.J. Hait, S. Deiwick, C. Decker, K. Romme, A. Dübbers, P. Küster, U. Graepler-Mainka, H. Hebestreit, S. van Koningsbruggen-Rietschel, S. Renner, B. Wollschläger, S. Naehrig, F. Sterling, A. Schlegtendal, S. Sutharsan, M. Ballmann, S. Junge, B. Kahl
المصدر: Journal of Cystic Fibrosis. 21:S49
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Pediatrics, Perinatology and Child Health
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7
المؤلفون: C.M. Sloan, L.J. Sherrard, G.G. Einarsson, L.J. Dupont, S. van Koningsbruggen-Rietschel, N.J. Simmonds, D.G. Downey
المصدر: Journal of Cystic Fibrosis. 21:S107
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Pediatrics, Perinatology and Child Health
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8
المؤلفون: J.C. Thomassen, T. Trojan, C. Vohlen, E. Rietschel, M.A. Alejandre Alcazar, S. van Koningsbruggen-Rietschel
المصدر: Journal of Cystic Fibrosis. 21:S24
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Pediatrics, Perinatology and Child Health
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9
المؤلفون: N. Simmonds, Jonathan D Cogen, Yvonne C. W. Yau, S. Hewko, Lieven Dupont, Damian G. Downey, R. Hernandez, H. Groves, Ana C. Blanchard, J. Julien, Valerie Waters, Anne L. Stephenson, Ranjani Somayaji, S. van Koningsbruggen-Rietschel, Lucas R. Hoffman, Bradley S. Quon
المصدر: Journal of Cystic Fibrosis
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, 2019-20 coronavirus outbreak, Coronavirus disease 2019 (COVID-19), Posters, business.industry, Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2), Infection/Microbiology, medicine.disease, Cystic fibrosis, Serology, Immune system, Pediatrics, Perinatology and Child Health, Immunology, medicine, business, Prospective cohort study
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المؤلفون: John P. Clancy, K. De Boeck, Michael W. Konstan, Pavel Drevinek, George Z. Retsch-Bogart, Amalia Magaret, Isabelle Fajac, Bradley S. Quon, Anthony G. Durmowicz, S.M. Singleton, Donald R. VanDevanter, Jane C. Davies, Scott C. Bell, Scott H. Donaldson, Patrick A. Flume, K. Pearson, Jennifer L. Taylor-Cousar, Christopher H. Goss, Damian G Downey, S. van Koningsbruggen-Rietschel, Nicole Mayer-Hamblett, Felix Ratjen, Tim W.R. Lee, Jill M. VanDalfsen, Dave P. Nichols
المصدر: J Cyst Fibros
Mayer-Hamblett, N, van Koningsbruggen-Rietschel, S, Nichols, D P, VanDevanter, D R, Davies, J C, Lee, T, Durmowicz, A G, Ratjen, F, Konstan, M W, Pearson, K, Bell, S C, Clancy, J P, Taylor-Cousar, J L, De Boeck, K, Donaldson, S H, Downey, D G, Flume, P A, Drevinek, P, Goss, C H, Fajac, I, Magaret, A S, Quon, B S, Singleton, S M, VanDalfsen, J M & Retsch-Bogart, G Z 2020, ' Building global development strategies for cf therapeutics during a transitional cftr modulator era ', Journal of Cystic Fibrosis, vol. 19, no. 5, pp. 677-687 . https://doi.org/10.1016/j.jcf.2020.05.011مصطلحات موضوعية: 0301 basic medicine, Pulmonary and Respiratory Medicine, Standard of care, International Cooperation, Harmonization, Article, 03 medical and health sciences, 0302 clinical medicine, Pairwise sequence alignment, Medicine, Humans, Pediatrics, Perinatology, and Child Health, business.industry, Drug Development/organization & administration, Clinical study design, Cystic Fibrosis Transmembrane Conductance Regulator/drug effects, 030104 developmental biology, 030228 respiratory system, Drug development, Risk analysis (engineering), Pediatrics, Perinatology and Child Health, Cystic Fibrosis/drug therapy, business, International development, Cftr modulator
وصف الملف: application/pdf
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المؤلفون: Ernst Rietschel, B. Schulte-Hubbert, R. Mahlberg, Carsten Schwarz, U. Düesberg, Michael Puderbach, F. Mattner, Christian Hügel, S. van Koningsbruggen-Rietschel, M. O. Wielpütz, C. Muche-Borowski, Ralf-Peter Vonberg, A. Möller, Helmut Ellemunter, Michael Hogardt, A. Koitschev, S. Illing, Jutta Hammermann, T. Nüßlein, S. Schmidt, D. Dieninghoff, H. Hebestreit, W. Bremer, Felix C. Ringshausen, Martin J. Hug, F. Brunsmann, Burkhard Tümmler, Helmut Sitter, Ingo Baumann, L. Sedlacek, B. Kahl, M. Abele-Horn, J. Grosse-Onnebrink, Rainald Fischer, J. Bend, H. Wilkens, A. Mehl, Andreas Jung, S. Renner, J. Zerlik, Olaf Eickmeier, B Wollschläger, Jochen G. Mainz, Christina Smaczny
المصدر: Pneumologie. 72:347-392
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Gynecology, 03 medical and health sciences, medicine.medical_specialty, 0302 clinical medicine, 030228 respiratory system, business.industry, Medicine, 030212 general & internal medicine, business
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المؤلفون: S. van Koningsbruggen-Rietschel, Ernst Rietschel
المصدر: Monatsschrift Kinderheilkunde. 165:681-687
مصطلحات موضوعية: Gynecology, 03 medical and health sciences, medicine.medical_specialty, 0302 clinical medicine, 030228 respiratory system, business.industry, Pediatrics, Perinatology and Child Health, medicine, Surgery, 030212 general & internal medicine, business
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المؤلفون: Margarete Odenthal, Christina Vohlen, Jörg Dötsch, S. S. Pullamsetti, M.A. Alejandre Alcazar, Katharina Dinger, Vanessa Jentgen, S. van Koningsbruggen-Rietschel, Johannes Will, Swati Dabral
المصدر: D16. EVERY CELL YOU BREAK: HOW CELLULAR PHENOTYPES CONTRIBUTE TO PAH.
مصطلحات موضوعية: Lung, biology, business.industry, Activator (genetics), FOXO1, chemistry.chemical_compound, medicine.anatomical_structure, Paclitaxel, chemistry, biology.protein, Cancer research, Medicine, business, Interleukin 6
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المؤلفون: Kate Hayes, Fiona Dunlevy, Veerle Bulteel, Damian G. Downey, Anne Verbrugge, S. van Koningsbruggen-Rietschel
المصدر: Journal of Cystic Fibrosis
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, 2019-20 coronavirus outbreak, Study drug, Cell Biology/Physiology/New Therapies/Clinical Trials, Coronavirus disease 2019 (COVID-19), business.industry, Posters, Severe acute respiratory syndrome coronavirus 2 (SARS-CoV-2), Clinical trial, Clinical research, Pediatrics, Perinatology and Child Health, Emergency medicine, Pandemic, medicine, business
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المؤلفون: C, Schwarz, B, Schulte-Hubbert, J, Bend, M, Abele-Horn, I, Baumann, W, Bremer, F, Brunsmann, D, Dieninghoff, O, Eickmeier, H, Ellemunter, R, Fischer, J, Grosse-Onnebrink, J, Hammermann, H, Hebestreit, M, Hogardt, C, Hügel, M, Hug, S, Illing, A, Jung, B, Kahl, A, Koitschev, R, Mahlberg, J G, Mainz, F, Mattner, A, Mehl, A, Möller, C, Muche-Borowski, T, Nüßlein, M, Puderbach, S, Renner, E, Rietschel, F C, Ringshausen, S, Schmidt, L, Sedlacek, H, Sitter, C, Smaczny, B, Tümmler, R, Vonberg, M O, Wielpütz, H, Wilkens, B, Wollschläger, J, Zerlik, U, Düesberg, S, van Koningsbruggen-Rietschel
المصدر: Pneumologie (Stuttgart, Germany). 72(5)
مصطلحات موضوعية: Cystic Fibrosis, Germany, Practice Guidelines as Topic, Pseudomonas aeruginosa, Cystic Fibrosis Transmembrane Conductance Regulator, Humans, Pseudomonas Infections
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المؤلفون: Ernst Rietschel, Tobias Trojan, Christina Vohlen, J.C. Thomassen, S. van Koningsbruggen-Rietschel, M.A. Alejandre Alcazar
المصدر: Journal of Cystic Fibrosis. 18:S119-S120
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, business.industry, Pseudomonas aeruginosa, medicine.disease, medicine.disease_cause, Cystic fibrosis, Microbiology, Cftr mutation, Pediatrics, Perinatology and Child Health, Medicine, Sputum, medicine.symptom, business, Elafin, Transforming growth factor
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المؤلفون: Alex Horsley, Patrick A. Flume, J. Miller, Tacjana Pressler, Sivagurunathan Sutharsan, S. Wilson, S. van Koningsbruggen-Rietschel, Damian G. Downey, Isabelle Fajac, Jennifer L. Taylor-Cousar, G. Poirier, Manu Jain, P.-S. Lee, J. Jiang, T. Inoue, G. Gilmartin, Carsten Schwarz
المصدر: Journal of Cystic Fibrosis. 18:S10
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, business.industry, Pediatrics, Perinatology and Child Health, medicine, Cancer research, Potentiator, medicine.disease, business, Cystic fibrosis
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18
المؤلفون: S. van Koningsbruggen-Rietschel, Jane C. Davies, O. Van de Steen, Edward F. McKone, Katja Conrath, Scott C. Bell, H. de Kock, C. Gesson, Pavel Drevinek, D. Kanters, Gordon MacGregor
المصدر: Journal of Cystic Fibrosis. 16:S24-S25
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, medicine.medical_specialty, business.industry, Phases of clinical research, medicine.disease, Cystic fibrosis, Gastroenterology, 03 medical and health sciences, 0302 clinical medicine, 030228 respiratory system, Internal medicine, Pediatrics, Perinatology and Child Health, Mutation (genetic algorithm), medicine, 030212 general & internal medicine, business
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19
المؤلفون: Ernst Rietschel, Gregor Lippach, J.C. Thomassen, M.A. Alejandre Alcazar, Tobias Trojan, M.-L. Walz, S. van Koningsbruggen-Rietschel
المصدر: Journal of Cystic Fibrosis. 17:S30
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Pathology, medicine.medical_specialty, business.industry, Pediatrics, Perinatology and Child Health, Medicine, Sputum, medicine.symptom, business, medicine.disease, Cystic fibrosis
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20
المؤلفون: J.C. Thomassen, M.A. Alejandre Alcazar, S. van Koningsbruggen-Rietschel, Christina Vohlen, Ernst Rietschel
المصدر: Journal of Cystic Fibrosis. 17:S8
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, business.industry, Pediatrics, Perinatology and Child Health, Cancer research, Wild type, Medicine, business, medicine.disease, Cystic fibrosis