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1Academic Journal
المؤلفون: Libo Yu-Taeger, Ali El-Ayoubi, Pengfei Qi, Lusine Danielyan, Hoa Huu Phuc Nguyen
المصدر: Cells, Vol 13, Iss 6, p 469 (2024)
مصطلحات موضوعية: Huntington disease, mesenchymal stromal cells, intravenous, R6/2 mice, liver function, hepatic pathology, Cytology, QH573-671
Relation: https://www.mdpi.com/2073-4409/13/6/469; https://doaj.org/toc/2073-4409; https://doaj.org/article/68c0c184414a4ba697ff84266ce72fe3
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2Academic Journal
المؤلفون: Roberto Speziale, Camilla Montesano, Giulia Di Pietro, Daniel Oscar Cicero, Vincenzo Summa, Edith Monteagudo, Laura Orsatti
المصدر: Metabolites; Volume 13; Issue 8; Pages: 961
مصطلحات موضوعية: urine metabolome, mass spectrometry, R6/2 mice, zQ175DN mice, Huntington’s disease
وصف الملف: application/pdf
Relation: Endocrinology and Clinical Metabolic Research; https://dx.doi.org/10.3390/metabo13080961
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3Academic Journal
المؤلفون: Reidling, Jack C, Relaño-Ginés, Aroa, Holley, Sandra M, Ochaba, Joseph, Moore, Cindy, Fury, Brian, Lau, Alice, Tran, Andrew H, Yeung, Sylvia, Salamati, Delaram, Zhu, Chunni, Hatami, Asa, Cepeda, Carlos, Barry, Joshua A, Kamdjou, Talia, King, Alvin, Coleal-Bergum, Dane, Franich, Nicholas R, LaFerla, Frank M, Steffan, Joan S, Blurton-Jones, Mathew, Meshul, Charles K, Bauer, Gerhard, Levine, Michael S, Chesselet, Marie-Francoise, Thompson, Leslie M
المصدر: Stem Cell Reports. 10(1)
مصطلحات موضوعية: Biochemistry and Cell Biology, Biological Sciences, Aging, Stem Cell Research - Nonembryonic - Human, Stem Cell Research, Neurosciences, Biotechnology, Orphan Drug, Genetics, Regenerative Medicine, Rare Diseases, Stem Cell Research - Embryonic - Human, Neurodegenerative, Brain Disorders, Transplantation, Huntington's Disease, 5.2 Cellular and gene therapies, 2.1 Biological and endogenous factors, Neurological, Animals, Cell Line, Cognition, Disease Models, Animal, Heterografts, Human Embryonic Stem Cells, Humans, Huntington Disease, Mice, Motor Activity, Neural Stem Cells, Recovery of Function, Huntington's disease, Q140 mice, R6/2 mice, embryonic stem cells, neural stem cell, transplantation, Clinical Sciences, Biochemistry and cell biology
وصف الملف: application/pdf
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4Academic Journal
المؤلفون: Libo Yu-Taeger, Arianna Novati, Jonasz Jeremiasz Weber, Elisabeth Singer-Mikosch, Ann-Sophie Pabst, Fubo Cheng, Carsten Saft, Jennifer Koenig, Gisa Ellrichmann, Taneli Heikkinen, Mahmoud A. Pouladi, Olaf Riess, Huu Phuc Nguyen
المصدر: Cells; Volume 11; Issue 23; Pages: 3779
مصطلحات موضوعية: Huntington disease, musculoskeletal growth, brain growth, sex-difference, BACHD rats, R6/2 mice, testosterone synthesis, transcription dysregulation
وصف الملف: application/pdf
Relation: https://dx.doi.org/10.3390/cells11233779
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5Dissertation/ Thesis
المؤلفون: Mena, Débora Tatiana de Sousa
المساهمون: Duarte, Ana Isabel Marques, Moreno, António Joaquim de Matos
مصطلحات موضوعية: Disfunção metabólica cerebral, doença de Huntington, liraglutida e grelina, murganhos R6/2, stress intracelular, Brain metabolic dysfunction, Huntington’s disease, liraglutide and ghrelin, R6/2 mice, intracellular stress
الاتاحة: http://hdl.handle.net/10316/88136
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6Academic Journal
المؤلفون: Mijung Lee, Wooseok Im, Manho Kim
المصدر: Neurobiology of Disease, Vol 155, Iss , Pp 105374- (2021)
مصطلحات موضوعية: Exosome, Parabiosis, Huntington's disease, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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7Academic Journal
المؤلفون: Ido Rippin, Katherina Bonder, Shirley Joseph, Ammar Sarsor, Lilach Vaks, Hagit Eldar-Finkelman
المصدر: Neurobiology of Disease, Vol 154, Iss , Pp 105336- (2021)
مصطلحات موضوعية: GSK-3, Huntington's diseases, Autophagy, Lysosome, Sirt1, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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8Academic Journal
المؤلفون: A. Di Pardo, G. Pepe, L. Capocci, F. Marracino, E. Amico, L. Del Vecchio, S. Giova, S.K. Jeong, B.M. Park, B.D. Park, V. Maglione
المصدر: Neurobiology of Disease, Vol 143, Iss , Pp 105009- (2020)
مصطلحات موضوعية: K6PC-5, HD, Neurodegeneration, Sphingolipids, Intestinal homeostasis, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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9Academic Journal
المؤلفون: Masashi Fukuoka, Masaki Takahashi, Hiromi Fujita, Tomoko Chiyo, H. Akiko Popiel, Shoko Watanabe, Hirokazu Furuya, Miho Murata, Keiji Wada, Takashi Okada, Yoshitaka Nagai, Hirohiko Hohjoh
المصدر: Molecular Therapy: Nucleic Acids, Vol 11, Iss C, Pp 79-90 (2018)
مصطلحات موضوعية: Huntington’s disease, microRNA, adeno-associated virus, miR-132 supplementation, R6/2 mice, Therapeutics. Pharmacology, RM1-950
وصف الملف: electronic resource
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10Academic Journal
المؤلفون: Jack C. Reidling, Aroa Relaño-Ginés, Sandra M. Holley, Joseph Ochaba, Cindy Moore, Brian Fury, Alice Lau, Andrew H. Tran, Sylvia Yeung, Delaram Salamati, Chunni Zhu, Asa Hatami, Carlos Cepeda, Joshua A. Barry, Talia Kamdjou, Alvin King, Dane Coleal-Bergum, Nicholas R. Franich, Frank M. LaFerla, Joan S. Steffan, Mathew Blurton-Jones, Charles K. Meshul, Gerhard Bauer, Michael S. Levine, Marie-Francoise Chesselet, Leslie M. Thompson
المصدر: Stem Cell Reports, Vol 10, Iss 1, Pp 58-72 (2018)
مصطلحات موضوعية: Huntington's disease, neural stem cell, transplantation, R6/2 mice, Q140 mice, embryonic stem cells, Medicine (General), R5-920, Biology (General), QH301-705.5
وصف الملف: electronic resource
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11Academic Journal
المؤلفون: Libo Yu-Taeger, Janice Stricker-Shaver, Katrin Arnold, Patrycja Bambynek-Dziuk, Arianna Novati, Elisabeth Singer, Ali Lourhmati, Claire Fabian, Janine Magg, Olaf Riess, Matthias Schwab, Alexandra Stolzing, Lusine Danielyan, Hoa Huu Phuc Nguyen
المصدر: Cells; Volume 8; Issue 6; Pages: 595
مصطلحات موضوعية: Huntington disease, cell therapy, mesenchymal stem cells, intranasal, R6/2 mice, dopamine transmission, microglia, neuroinflammation
وصف الملف: application/pdf
Relation: Cells of the Nervous System; https://dx.doi.org/10.3390/cells8060595
الاتاحة: https://doi.org/10.3390/cells8060595
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12Academic Journal
المؤلفون: Wei Li, Henrique B. Silva, Joana Real, Yu-Mei Wang, Daniel Rial, Ping Li, Marie-Pierce Payen, Yuanguo Zhou, Christa E. Muller, Angelo R. Tomé, Rodrigo A. Cunha, Jiang-Fan Chen
المصدر: Neurobiology of Disease, Vol 79, Iss , Pp 70-80 (2015)
مصطلحات موضوعية: Adenosine A2A receptor, Huntington's disease, Cognition, Working memory, Long-term depression, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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13Academic Journal
المؤلفون: Eloise Larson, Ian Fyfe, A. Jennifer Morton, Darren G. Monckton
المصدر: Neurobiology of Disease, Vol 76, Iss , Pp 98-111 (2015)
مصطلحات موضوعية: Huntington disease (HD), Polyglutamine expansion, Trinucleotide repeat expansion, Somatic instability, Mutation, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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14Academic Journal
المؤلفون: Alipi V. Naydenov, Marja D. Sepers, Katie Swinney, Lynn A. Raymond, Richard D. Palmiter, Nephi Stella
المصدر: Neurobiology of Disease, Vol 71, Iss , Pp 140-150 (2014)
مصطلحات موضوعية: Huntington's disease, R6/2 mice, Endocannabinoids, CB1, Synaptic loss, Dendritic spines, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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15Academic Journal
المؤلفون: Antonella Ferrante, Alberto Martire, Rita Pepponi, Katia Varani, Fabrizio Vincenzi, Luca Ferraro, Sarah Beggiato, Maria Teresa Tebano, Patrizia Popoli
المصدر: Neurobiology of Disease, Vol 71, Iss , Pp 193-204 (2014)
مصطلحات موضوعية: Huntington's disease, R6/2 mice, Striatum, Adenosine A1 receptors, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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16Academic Journal
المؤلفون: Valdeolivas Rojas, Sara, Sagredo Ezquioga, Onintza, Delgado Wallace, Mercedes, Pozo García, Miguel Ángel, Fernández Ruiz, Javier
مصطلحات موضوعية: phytocannabinoids, cannabidiol, Δ9-tetrahydrocannabinol, Huntington’s disease, R6/2 mice, basal ganglia, neuroprotection, Bioquímica (Medicina), Farmacología (Medicina), Fisiología, Biología molecular (Farmacia), Bioquímica (Farmacia), Farmacología (Farmacia), 2411 Fisiología Humana, 3209 Farmacología
وصف الملف: application/pdf
Relation: SAF2009/11847; CB06/05/0089; https://hdl.handle.net/20.500.14352/19209
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17Academic JournalAltered Aconitase 2 Activity in Huntington’s Disease Peripheral Blood Cells and Mouse Model Striatum
المؤلفون: Chiung-Mei Chen, Yih-Ru Wu, Kuo-Hsuan Chang
المصدر: International Journal of Molecular Sciences; Volume 18; Issue 11; Pages: 2480
مصطلحات موضوعية: Huntington’s disease, Hdh (CAG)150 and R6/2 mice, peripheral blood mononuclear cells, aconitase 2, N -acetyl-l-cysteine, biomarker
جغرافية الموضوع: agris
وصف الملف: application/pdf
Relation: Molecular Pathology, Diagnostics, and Therapeutics; https://dx.doi.org/10.3390/ijms18112480
الاتاحة: https://doi.org/10.3390/ijms18112480
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18
المؤلفون: Mccourt, Andy
مصطلحات موضوعية: Huntington’s disease, weight loss, white adipose tissue, brown adipose tissue, peripheral symptoms, R6/2 mice, UCP1, CREB1, gene expression, Medicin och hälsovetenskap, Medicinska och farmaceutiska grundvetenskaper, Neurovetenskaper, Medical and Health Sciences, Basic Medicine, Neurosciences
وصف الملف: electronic
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19Academic Journal
المؤلفون: Valentina Chiodi, Motokazu Uchigashima, Sarah Beggiato, Antonella Ferrante, Monica Armida, Alberto Martire, Rosa Luisa Potenza, Luca Ferraro, Sergio Tanganelli, Masahiko Watanabe, Maria Rosaria Domenici, Patrizia Popoli
المصدر: Neurobiology of Disease, Vol 45, Iss 3, Pp 983-991 (2012)
مصطلحات موضوعية: Cannabinoid CB1 receptor, Huntington's disease, R6/2 mice, Synaptic transmission, Neurotransmitter release, Immunoelectron microscopy, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource
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20Academic Journal
المؤلفون: Alberto Martire, Antonella Ferrante, Rosa Luisa Potenza, Monica Armida, Roberta Ferretti, Antonella Pézzola, Maria Rosaria Domenici, Patrizia Popoli
المصدر: Neurobiology of Disease, Vol 37, Iss 1, Pp 99-105 (2010)
مصطلحات موضوعية: Huntington disease, Adenosine A2A receptor, NMDA receptor subunit, BDNF, R6/2 mice, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571
وصف الملف: electronic resource