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1Academic Journal
المؤلفون: Paolo Ritter, Stefania Oliveto, Chiara Cordiglieri, Alessandra Fasciani, Christian Andrea Di Buduo, Lucrezia della Volpe, Alberto Bocconi, Claudio Conci, Carolina Paula Miguel, Raffaella Di Micco, Alessandra Balduini, Manuela Teresa Raimondi, Stefano Biffo
المصدر: Frontiers in Bioengineering and Biotechnology, Vol 12 (2024)
مصطلحات موضوعية: CD4+, CD34+, gene therapy, fluidics, bone marrow, Biotechnology, TP248.13-248.65
وصف الملف: electronic resource
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المؤلفون: Anna Maria Sole Giordano, Marco Luciani, Francesca Gatto, Monah Abou Alezz, Chiara Beghè, Lucrezia Della Volpe, Alessandro Migliara, Sara Valsoni, Marco Genua, Monika Dzieciatkowska, Giacomo Frati, Julie Tahraoui-Bories, Silvia Clara Giliani, Simona Orcesi, Elisa Fazzi, Renato Ostuni, Angelo D’Alessandro, Raffaella Di Micco, Ivan Merelli, Angelo Lombardo, Martin A.M. Reijns, Natalia Gromak, Angela Gritti, Anna Kajaste-Rudnitski
المصدر: Giordano, A M S, Luciani, M, Gatto, F, Alezz, M A, Beghè, C, Volpe, L D, Migliara, A, Valsoni, S, Genua, M, Dzieciatkowska, M, Frati, G, Tahraoui-Bories, J, Giliani, S, Orcesi, S, Fazzi, E, Ostuni, R, D'Alessandro, A, Di Micco, R, Merelli, I, Lombardo, A, Reijns, M A M, Gromak, N, Gritti, A & Kajaste-Rudnitski, A 2022, ' DNA damage contributes to neurotoxic inflammation in Aicardi-Goutières Syndrome astrocytes ', Journal of Experimental Medicine . https://doi.org/10.1084/jem.20211121
مصطلحات موضوعية: Inflammation, Autoimmune Diseases of the Nervous System, Astrocytes, DNA Damage, Humans, Nervous System Malformations, Immunology, Immunology and Allergy
وصف الملف: application/pdf
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المؤلفون: Angela Bachi, Elisabeth Mangiameli, Vittoria Matafora, Angela Pesenti Gritti, Lucrezia della Volpe, Lucia Susani, Daniela Gnani, Marianna Paulis, Francesca Sanvito, Sabata Martino, Anna Cecchele, Raffaella Di Micco, Francesco Morena, Angela Cattaneo
المصدر: Stem Cell Reports
مصطلحات موضوعية: 0301 basic medicine, Senescence, leukodystrophy, senescence, Genetic enhancement, lysosomal enzymes, Induced Pluripotent Stem Cells, oligodendrocytes, neurons, neural progenitors, Biology, Biochemistry, Article, 03 medical and health sciences, 0302 clinical medicine, Pluripotent stem cells, Genetics, Lysosomal storage disease, medicine, Humans, Genetic Predisposition to Disease, Progenitor cell, Induced pluripotent stem cell, Cells, Cultured, Stem Cells, Neurodegeneration, Leukodystrophy, Psychosine, Cell Differentiation, Cell Biology, Genetic Therapy, medicine.disease, Phenotype, gene therapy, Cell biology, Leukodystrophy, Globoid Cell, Oligodendroglia, 030104 developmental biology, GALC activity, Krabbe disease, 030217 neurology & neurosurgery, Developmental Biology, Galactosylceramidase
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المؤلفون: Raffaella Di Micco, Anastasia Conti, Lucrezia della Volpe, Federico Midena, Samuele Ferrari, Teresa Tavella, Ivan Merelli, Luigi Naldini
المصدر: Experimental Hematology. 111:S22
مصطلحات موضوعية: Cancer Research, Genetics, Cell Biology, Hematology, Molecular Biology
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المؤلفون: Simona Allocca, Michela Ciano, Lucrezia della Volpe, Maria Camilla Ciardulli, Stefano Bonatti, Massimo D'Agostino
المساهمون: Ciano, Michela, Allocca, Simona, Ciardulli, Maria Camilla, Della Volpe, Lucrezia, Bonatti, Stefano, D'Agostino, Massimo
المصدر: Biochemical and Biophysical Research Communications
مصطلحات موضوعية: 0301 basic medicine, Protein Folding, DNA, Complementary, Green Fluorescent Proteins, Biophysics, Biology, TMP, transmembrane protein, Biochemistry, Article, CRYAB, αB-crystallin, ER, endoplasmic reticulum, Serine, 03 medical and health sciences, 0302 clinical medicine, Multipass transmembrane proteins, Chaperone activity, Cell Line, Tumor, Heat shock protein, Humans, Phosphorylation, Molecular Biology, Multipass transmembrane protein, Endoplasmic reticulum, Membrane Proteins, alpha-Crystallin B Chain, Cell Biology, Transmembrane protein, Cell biology, Folding (chemistry), Cytosol, 030104 developmental biology, αB-crystallin/HspB5/CRYAB, Mutagenesis, 030220 oncology & carcinogenesis, Mutation, FEVR, Familial exudative vitreoretinopathy, MAPK, mitogen-activated protein kinase, sHsp, small heat shock protein, Biogenesis, Molecular Chaperones, Plasmids, Protein Binding, Signal Transduction
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المؤلفون: Raffaella Di Micco, Giulia Schiroli, Valentina Vavassori, Anastasia Conti, Pietro Genovese, Delphine Ndiaye-Lobry, Patrizia Gasparini, Julie Chaumeil, Chiara Brombin, Lucrezia della Volpe, Ivan Merelli, Aurelien Jacob, Eugenio Montini, Andrea Calabria, Samuele Ferrari, Luigi Naldini, Stefano Beretta, Luisa Albano, Eralda Salataj
المساهمون: Schiroli, Giulia, Conti, Anastasia, Ferrari, Samuele, Della Volpe, Lucrezia, Jacob, Aurelien, Albano, Luisa, Beretta, Stefano, Calabria, Andrea, Vavassori, Valentina, Gasparini, Patrizia, Salataj, Eralda, Ndiaye-Lobry, Delphine, Brombin, Chiara, Chaumeil, Julie, Montini, Eugenio, Merelli, Ivan, Genovese, Pietro, Naldini, Luigi, Di Micco, Raffaella, Schiroli, G, Conti, A, Ferrari, S, della Volpe, L, Jacob, A, Albano, L, Beretta, S, Calabria, A, Vavassori, V, Gasparini, P, Salataj, E, Ndiaye-Lobry, D, Brombin, C, Chaumeil, J, Montini, E, Merelli, I, Genovese, P, Naldini, L, Di Micco, R
المصدر: Cell stem cell
(2019). doi:10.1016/j.stem.2019.02.019
info:cnr-pdr/source/autori:Schiroli G, Conti A, Ferrari S, Della Volpe L, Jacob A, Albano L, Beretta S, Calabria A, Vavassori V, Gasparini P, Salataj E, Ndiaye-Lobry D, Brombin C, Chaumeil J, Montini E, Merelli I, Genovese P, Naldini L, Di Micco R./titolo:Precise Gene Editing Preserves Hematopoietic Stem Cell Function following Transient p53-Mediated DNA Damage Response/doi:10.1016%2Fj.stem.2019.02.019/rivista:Cell stem cell (Print)/anno:2019/pagina_da:/pagina_a:/intervallo_pagine:/volumeمصطلحات موضوعية: DNA damage, DNA repair, adeno-associated vector, Mice, SCID, Biology, DNA damage response, Cell Line, DNA double strand break, Mice, 03 medical and health sciences, 0302 clinical medicine, Genome editing, Mice, Inbred NOD, K562 Cell, Genetics, medicine, genome editing, Animals, Humans, CRISPR, Progenitor cell, programmable nuclease, 030304 developmental biology, Gene Editing, Mice, Knockout, 0303 health sciences, Animal, Cas9, Hematopoietic stem cell, Hematopoietic Stem Cell, Cell Biology, Hematopoietic Stem Cells, Cell biology, hematopoietic stem and progenitor cell, Haematopoiesis, medicine.anatomical_structure, Molecular Medicine, DNA double strand breaks, hematopoietic stem and progenitor cells, p53 pathway, programmable nucleases, Tumor Suppressor Protein p53, K562 Cells, 030217 neurology & neurosurgery, Human, DNA Damage
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المؤلفون: Daniela Gnani, Stefania Crippa, Anastasia Conti, Maria Ester Bernardo, Marco Ometti, Valeria Rossella, Raffaella Di Micco, Gianfranco Fraschini, Emanuele Lettera, Lucrezia della Volpe, Silvia Rivis
المساهمون: Gnani, D., Crippa, S., della Volpe, L., Rossella, V., Conti, A., Lettera, E., Rivis, S., Ometti, M., Fraschini, G., Bernardo, M. E., Di Micco, R.
المصدر: Aging Cell
مصطلحات موضوعية: Adult, 0301 basic medicine, Senescence, Aging, senescence, Adolescent, DNA damage, hematopoietic stem and progenitor cells, Inflammation, Biology, SASP, Lipofuscin, Colony-Forming Units Assay, Young Adult, 03 medical and health sciences, 0302 clinical medicine, medicine, Humans, Progenitor cell, Clonogenic assay, Cells, Cultured, Cellular Senescence, Aged, Cell Proliferation, Original Paper, aging, Mesenchymal stem cell, Mesenchymal Stem Cells, Cell Biology, Flow Cytometry, Hematopoietic Stem Cells, beta-Galactosidase, Original Papers, Haematopoiesis, 030104 developmental biology, medicine.anatomical_structure, Cancer research, Cytokines, Bone marrow, medicine.symptom, mesenchymal stromal cells, Reactive Oxygen Species, 030217 neurology & neurosurgery