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1Academic Journal
المؤلفون: Ivan Pećin, Iveta Merćep, Vanja Bašić-Kes, Ervina Bilić, Fran Borovečki, Mirna Bradamante, Maja Čikeš, Ksenija Fumić, Ana Godan Hauptman, Bojan Jelaković, Dunja Leskovar, Kristina Paponja Mihanović, Dražen Perica, Luka Prgomet, Sanjin Rački, Kristina Selthofer-Relatić, Marija Štanfel, Nediljko Šućur, Božidar Vujičić, Tamara Vukić, Željko Reiner
المصدر: Liječnički vjesnik, Vol 146, Iss 5-6, Pp 157-169 (2024)
مصطلحات موضوعية: FABRIJEVA BOLEST – dijagnoza, farmakoterapija, komplikacije, ALFA GALAKTOZIDAZA – genetika, GLIKOLIPIDI, LIZOSOMI, ENZIMSKA NADOMJESNA TERAPIJA, HIPERTROFIČNA KARDIOMIOPATIJA, Medicine (General), R5-920
وصف الملف: electronic resource
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2Academic Journal
المؤلفون: Pećin, Ivan, Merćep, Iveta, Bašić-Kes, Vanja, Bilić, Ervina, Borovečki, Fran, Bradamante, Mirna, Čikeš, Maja, Fumić, Ksenija, Godan Hauptman, Ana, Jelaković, Bojan, Leskovar, Dunja, Paponja Mihanović, Kristina, Perica, Dražen, Prgomet, Luka, Rački, Sanjin, Selthofer-Relatić, Kristina, Štanfel, Marija, Šućur, Nediljko, Vujičić, Božidar, Vukić, Tamara, Reiner, Željko
المصدر: Liječnički vjesnik ; Volume 146 ; Issue 5-6 ; ISSN 0024-3477 (Print) ; ISSN 1849-2177 (Online) ; https://hrcak.srce.hr/319957
مصطلحات موضوعية: FABRIJEVA BOLEST – dijagnoza, farmakoterapija, komplikacije, ALFA GALAKTOZIDAZA – genetika, GLIKOLIPIDI, LIZOSOMI, ENZIMSKA NADOMJESNA TERAPIJA, HIPERTROFIČNA KARDIOMIOPATIJA, KRONIČNA BUBREŽNA BOLEST, ISHEMIJSKI MOŽDANI UDAR, SMJERNICE, HRVATSKA, FABRY DISEASE – complications, diagnosis, drug therapy, ALPHA-GALACTOSIDASE – genetics, GLYCOLIPIDS, LYSOSOMES, ENZYME REPLACEMENT THERAPY, CARDIOMYOPATHY, HYPERTROPHIC, RENAL INSUFFICIENCY, CHRONIC, ISCHEMIC STROKE, PRACTICE GUIDELINES AS TOPIC, CROATIA, BIOMEDICINA I ZDRAVSTVO. Kliničke medicinske znanosti. Interna medicina, BIOMEDICINE AND HEALTHCARE. Clinical Medical Sciences. Internal Medicine
وصف الملف: application/pdf
Relation: Sveučilište u Rijeci. Medicinski fakultet. Katedra za internu medicinu.; University of Rijeka. Faculty of Medicine. Department of Internal Medicine.; https://www.unirepository.svkri.uniri.hr/islandora/object/medri:8939; https://urn.nsk.hr/urn:nbn:hr:184:788165; https://www.unirepository.svkri.uniri.hr/islandora/object/medri:8939/datastream/FILE0
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3Academic Journal
المؤلفون: Božić, Mićo, Verkhratsky, Alexei, Zorec, Robert, Stenovec, Matjaž
المصدر: Cellular and molecular life sciences, vol. 77, no. 16, pp. 3245-3264, 2020. ; ISSN: 1420-682X
مصطلحات موضوعية: astroglia, inflammatory cytokines, fusion pore, adaptive immunity, patch clamp, lysosomes, vnetni citokini, fuzijske pore, adaptivna imunost, obliž, lizosomi, info:eu-repo/classification/udc/616-092
وصف الملف: application/pdf; text/url
Relation: info:eu-repo/grantAgreement/ARRS//P3-0310; info:eu-repo/grantAgreement/ARRS//J3-6790; info:eu-repo/grantAgreement/ARRS//J3-9266; https://repozitorij.uni-lj.si/IzpisGradiva.php?id=128778; https://repozitorij.uni-lj.si/Dokument.php?id=145652&dn=; https://repozitorij.uni-lj.si/Dokument.php?id=145653&dn=; https://plus.si.cobiss.net/opac7/bib/34551513?lang=sl
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4
المؤلفون: Katušić, Silva
المساهمون: Katušić Hećimović, Silva
مصطلحات موضوعية: neurodegeneracija, neuroinflamacija, rijetke bolesti, kolesterol, NPC, endosomi, lizosomi, BIOMEDICINA I ZDRAVSTVO. Temeljne medicinske znanosti. Neuroznanost, BIOMEDICINE AND HEALTHCARE. Basic Medical Sciences. Neuroscience
Relation: info:eu-repo/grantAgreement/Hrvatska zaklada za znanost/Research Projects/IP-2022-10-7325/HR/Biogeneza endosoma u Niemann-Pickovoj bolesti tipa C/ENDOGENESIS; Institut Ruđer Bošković. Zavod za molekularnu medicinu.; Ruđer Bošković Institute. Division of Molecular Medicine.; https://data.fulir.irb.hr/islandora/object/irb:629; https://urn.nsk.hr/urn:nbn:hr:241:043461
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5Dissertation/ Thesis
المؤلفون: Dolić, Valentina
المساهمون: Ljubojević, Marija, Đikić, Domagoj
مصطلحات موضوعية: PRIRODNE ZNANOSTI. Biologija, NATURAL SCIENCES. Biology, autofagocitoza, feritinofagija, lizosomi, prijelazni metali, nanokavez, autophagocytosis, ferritinophagy, lysosomes, transition metals, nanocage
وصف الملف: application/pdf
Relation: info:eu-repo/grantAgreement/Europska unija//533-03-23-0006/EU/Procjena učinkovitosti i toksičnosti biološki aktivnih tvari/BioMolTox; https://zir.nsk.hr/islandora/object/pmf:13703; https://urn.nsk.hr/urn:nbn:hr:217:269937; https://repozitorij.unizg.hr/islandora/object/pmf:13703; https://repozitorij.unizg.hr/islandora/object/pmf:13703/datastream/PDF
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6Dissertation/ Thesis
المؤلفون: Kujundžić, Mislav
المساهمون: Pereza, Nina
مصطلحات موضوعية: BIOMEDICINA I ZDRAVSTVO. Kliničke medicinske znanosti. Pedijatrija, BIOMEDICINE AND HEALTHCARE. Clinical Medical Sciences. Pediatrics, lizosomi, lizosomske bolesti nakupljanja, autosomno recesivno, X-vezano, genetičko testiranje, ERT, lysosomes, lysosomal storage diseases, autosomal recessive, X-linked, genetic testing
وصف الملف: application/pdf
Relation: https://www.unirepository.svkri.uniri.hr/islandora/object/medri:8798; https://urn.nsk.hr/urn:nbn:hr:184:739026; https://www.unirepository.svkri.uniri.hr/islandora/object/medri:8798/datastream/PDF
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7
المؤلفون: Martinović, Lovro
المساهمون: Katušić Hećimović, Silva, Erhardt, Julija
مصطلحات موضوعية: kolesterol, NPC1, lizosomi, neurodegeneracija, neuroinflamacija, rijetke bolesti, PRIRODNE ZNANOSTI. Biologija, neurodegeneration, cholesterol, rare diseases, neuroinflammation, lysosome, NATURAL SCIENCES. Biology, lizosom
وصف الملف: application/pdf
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8Dissertation/ Thesis
المؤلفون: Vidoša, Lorena
المساهمون: Basarić, Nikola, Malatesti, Nela
مصطلحات موضوعية: BODIPY, endoplazmatski retikulum, fluorescencijska mikroskopija, fotofizika, lizosomi, mitohondrij, organska sinteza, fluorescence microscopy, endoplasmic reticulum, lysosomes, mitochondria, organic synthesis, photophysics, BIOTEHNIČKE ZNANOSTI. Biotehnologija, BIOTECHNICAL SCIENCES. Biotechnology
وصف الملف: application/pdf
Relation: https://www.unirepository.svkri.uniri.hr/islandora/object/biotechri:917; https://urn.nsk.hr/urn:nbn:hr:193:408694; https://www.unirepository.svkri.uniri.hr/islandora/object/biotechri:917/datastream/PDF
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9
المؤلفون: Zovko, Ana
المساهمون: Katušić Hećimović, Silva, Blažević, Sofia Ana
مصطلحات موضوعية: congenital, hereditary, and neonatal diseases and abnormalities, kasni endosomi/lizosomi, PRIRODNE ZNANOSTI. Biologija, hemic and lymphatic diseases, late endosomes/lysosomes, neuroinflamacija, nutritional and metabolic diseases, tau hiperfosforilacija, NATURAL SCIENCES. Biology, hyperphosphorylation of tau, NPC1, neuroinflammation
وصف الملف: application/pdf
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10
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11
المؤلفون: Hulita, Andrea
المساهمون: Fumić, Ksenija
مصطلحات موضوعية: neuronal ceroid lipofuscinose type 1, Batten disease, CLN1 disease, neuronal ceroid lipofuscinose, Battenova bolest, neuronalna ceroidna lipofuscinoza, lizosomi, neuronalna ceroidna lipofuscinoza tipa 1, BIOMEDICINE AND HEALTHCARE. Pharmacy. Medical Biochemistry, CLN1 bolest, PPT1, lysosomes, CLN1, PPT1, Battenova bolest, BIOMEDICINA I ZDRAVSTVO. Farmacija. Medicinska biokemija
وصف الملف: application/pdf
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12
المؤلفون: Alexei Verkhratsky, Mićo Božić, Robert Zorec, Matjaž Stenovec
المصدر: Božić, M, Verkhratsky, A, Zorec, R & Stenovec, M 2019, ' Exocytosis of large-diameter lysosomes mediates interferon γ-induced relocation of MHC class II molecules toward the surface of astrocytes ', Cellular and Molecular Life Sciences . https://doi.org/10.1007/s00018-019-03350-8
Cellular and Molecular Life Sciences
Cellular and molecular life sciences, vol. 77, no. 16, pp. 3245-3264, 2020.مصطلحات موضوعية: 0301 basic medicine, Central Nervous System, Immunolabeling, Astroglia, 0302 clinical medicine, Cells, Cultured, fuzijske pore, Antigen Presentation, Chemistry, respiratory system, Inflammatory cytokines, Endocytosis, Astrogliosis, Cell biology, Protein Transport, medicine.anatomical_structure, Molecular Medicine, Original Article, Female, Patch clamp, obliž, Astrocyte, Endosome, Antigen presentation, Adaptive immunity, chemical and pharmacologic phenomena, vnetni citokini, Endosomes, Exocytosis, 03 medical and health sciences, Cellular and Molecular Neuroscience, Interferon-gamma, medicine, Animals, Rats, Wistar, Molecular Biology, Neuroinflammation, Pharmacology, Inflammation, adaptivna imunost, Secretory Vesicles, Cell Membrane, Histocompatibility Antigens Class II, Cell Biology, medicine.disease, lizosomi, Fusion pore, Rats, 030104 developmental biology, Astrocytes, udc:616-092, Lysosomes, 030217 neurology & neurosurgery, Biomarkers
وصف الملف: application/pdf; text/url
URL الوصول: https://explore.openaire.eu/search/publication?articleId=doi_dedup___::ddb3551110bfc383435c30d530f8753d
https://www.research.manchester.ac.uk/portal/en/publications/exocytosis-of-largediameter-lysosomes-mediates-interferon-induced-relocation-of-mhc-class-ii-molecules-toward-the-surface-of-astrocytes(2e147911-aa1d-44d3-b274-fda67d7e8b47).html -
13Dissertation/ Thesis
المؤلفون: Hulita, Andrea
المساهمون: Fumić, Ksenija
مصطلحات موضوعية: neuronalna ceroidna lipofuscinoza, neuronalna ceroidna lipofuscinoza tipa 1, CLN1 bolest, PPT1, Battenova bolest, lizosomi, neuronal ceroid lipofuscinose, neuronal ceroid lipofuscinose type 1, CLN1 disease, Batten disease, lysosomes, BIOMEDICINA I ZDRAVSTVO. Farmacija. Medicinska biokemija, BIOMEDICINE AND HEALTHCARE. Pharmacy. Medical Biochemistry
وصف الملف: application/pdf
Relation: https://zir.nsk.hr/islandora/object/pharma:1938; https://urn.nsk.hr/urn:nbn:hr:163:592151; https://repozitorij.unizg.hr/islandora/object/pharma:1938; https://repozitorij.unizg.hr/islandora/object/pharma:1938/datastream/PDF
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14Academic Journal
المؤلفون: Matjaž ČERVEK, D. ATTAIX, Jasna M.A. STEKAR
المصدر: Acta Agriculturae Slovenica, Vol 70, Iss 1 (1997)
مصطلحات موضوعية: razkroj beljakovin, proteolitični sistemi, lizosomi, proteazomi, skeletno mišičje, Agriculture
وصف الملف: electronic resource
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15
المؤلفون: Čermak, Stjepko
مصطلحات موضوعية: Alzheimerova bolest, APP, lizosomi, LAMP1, NPC1, BACE1, bolest Niemann-Pick tipa C, kolesterol, EGFR, neurodegeneracija, CB2 receptori
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16
المؤلفون: Jović, Tanja
مصطلحات موضوعية: lizosomi, Niemann-Pick tip C, glikani
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17
المؤلفون: Padovan, Ingrid
المساهمون: Drobne, Damjana
مصطلحات موضوعية: udc:54, diplomske naloge, Porcellio scaber, nevtral rdeče, živo srebro, lizosomi
وصف الملف: text/url; application/pdf
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18
المؤلفون: Usenović, Marija
المساهمون: Krainc, Dimitri, Terzić, Janoš, Volarević, Siniša, Đogaš, Zoran
مصطلحات موضوعية: Lizosomi, Adenozin trifosfat, BIOMEDICINA I ZDRAVSTVO. Kliničke medicinske znanosti. Neurologija, udc:616(043.3), Adenosine Triphosphate, Autofagija, BIOMEDICINE AND HEALTHCARE. Clinical Medical Sciences. Neurology, Nerve Degeneration, Degeneracija živaca, Autophagy, Pathology. Clinical medicine, Lysosomes, Patologija. Klinička medicina
وصف الملف: application/pdf
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19Dissertation/ Thesis
المؤلفون: Bertović, Ivana
المساهمون: Jurak Begonja, Antonija
مصطلحات موضوعية: megakaryocytes, PI3P, Rab GTPases, lysosomes, nucleolus, megakariociti, Rab GTPaze, lizosomi, jezgrica, BIOTEHNIČKE ZNANOSTI. Biotehnologija. Molekularna biotehnologija, BIOTECHNICAL SCIENCES. Biotechnology. Molecular Biotechnology, Biokemija. Molekularna biologija. Biofizika, Biochemistry. Molecular biology. Biophysics, info:eu-repo/classification/udc/577(043.3)
وصف الملف: application/pdf
Relation: https://www.unirepository.svkri.uniri.hr/islandora/object/biotechri:686; https://urn.nsk.hr/urn:nbn:hr:193:767447; https://www.unirepository.svkri.uniri.hr/islandora/object/biotechri:686/datastream/PDF
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20Dissertation/ Thesis
المؤلفون: Zovko, Ana
المساهمون: Katušić Hećimović, Silva, Blažević, Sofia Ana
مصطلحات موضوعية: NPC1, kasni endosomi/lizosomi, neuroinflamacija, tau hiperfosforilacija, late endosomes/lysosomes, neuroinflammation, hyperphosphorylation of tau, PRIRODNE ZNANOSTI. Biologija, NATURAL SCIENCES. Biology
وصف الملف: application/pdf
Relation: https://zir.nsk.hr/islandora/object/pmf:9924; https://urn.nsk.hr/urn:nbn:hr:217:538752; https://repozitorij.unizg.hr/islandora/object/pmf:9924; https://repozitorij.unizg.hr/islandora/object/pmf:9924/datastream/PDF