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1Academic Journal
المؤلفون: Iskren Menkovic, Monika Williams, Neelam Makhijani, Ruhan Wei, Sarah P. Young, Areeg El-Gharbawy, Ashlee R. Stiles
المصدر: Molecular Genetics and Metabolism Reports, Vol 42, Iss , Pp 101191- (2025)
مصطلحات موضوعية: GM1 gangliosidosis, Alkaline phosphatase, Keratan sulfate, Skeletal survey, Glycosaminoglycan, Medicine (General), R5-920, Biology (General), QH301-705.5
Relation: http://www.sciencedirect.com/science/article/pii/S2214426925000060; https://doaj.org/toc/2214-4269; https://doaj.org/article/415c08cc6dad4835996007a756023022
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2Academic Journal
المؤلفون: Wu, Yunfei, Bosman, Gerlof P, Chapla, Digantkumar, Huang, Chin, Moremen, Kelley W, de Vries, Robert P, Boons, Geert-Jan
المساهمون: Afd Chemical Biology and Drug Discovery, Sub Chemical Biology and Drug Discovery, Chemical Biology and Drug Discovery
مصطلحات موضوعية: Biomimetics, Carbohydrate Sulfotransferases, Galactose, Galactosides, Keratan Sulfate/chemistry, Oligosaccharides, Proteoglycans, Sulfates
وصف الملف: application/pdf
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3Academic Journal
المؤلفون: Takeda-Uchimura, Yoshiko, Ikezaki, Midori, Akama, Tomoya, O, Ihara, Yoshito, Allain, Fabrice, Nishitsuji, Kazuchika, Uchimura, Kenji
المساهمون: Unité de Glycobiologie Structurale et Fonctionnelle - UMR 8576 (UGSF), Université de Lille-Centre National de la Recherche Scientifique (CNRS), Department of Biochemistry, Wakayama Medical University
المصدر: ISSN: 1420-3049 ; Molecules ; https://hal.science/hal-04479404 ; Molecules, 2024, 29, ⟨10.3390/molecules29040764⟩.
مصطلحات موضوعية: Sulfotransferase, Keratan sulfate, Sialomucin, Mesothelium, MUC16, [SDV]Life Sciences [q-bio]
Relation: hal-04479404; https://hal.science/hal-04479404; https://hal.science/hal-04479404/document; https://hal.science/hal-04479404/file/molecules-29-00764%20%2B%20SI.pdf
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4Academic Journal
المؤلفون: Yunfei Wu, Gerlof P. Bosman, Digantkumar Chapla, Chin Huang, Kelley W. Moremen, Robert P. de Vries, Geert-Jan Boons
مصطلحات موضوعية: Biochemistry, Genetics, Biotechnology, Evolutionary Biology, Plant Biology, Chemical Sciences not elsewhere classified, various tissue types, examine substrate specificities, >- glycans decorated, remove blocking fucosides, provide keratan sulfate, least understood proteoglycan, biomimetic synthetic strategy, defined ks oligosaccharides, ii oligosaccharides, enzymatic strategy, biomimetic approach, >- acetyllactosamine, widely expressed, turn controls, structural element, stage treatment, specific arrangements, regioselective manner, oligo -<, n <, mutually exclusive, mutual exclusivity, extracellular matrix, drug development
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5Academic Journal
المؤلفون: Sodhi, Harkanwalpreet, Panitch, Alyssa
المصدر: Biomolecules. 11(1)
مصطلحات موضوعية: Medical Biotechnology, Biochemistry and Cell Biology, Biomedical and Clinical Sciences, Biological Sciences, Stem Cell Research, Bioengineering, Regenerative Medicine, Stem Cell Research - Nonembryonic - Non-Human, Biotechnology, Generic health relevance, Animals, Biocompatible Materials, Cell Communication, Cell Differentiation, Cell Proliferation, Extracellular Matrix, Glycosaminoglycans, Humans, Stem Cells, Tissue Engineering, Tissue Scaffolds, glycosaminoglycans, tissue engineering, extracellular matrix, chondroitin sulfate, hyaluronic acid, dermatan sulfate, keratan sulfate, heparan sulfate, Biochemistry and cell biology, Bioinformatics and computational biology, Medical biotechnology
وصف الملف: application/pdf
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6Academic Journal
المؤلفون: Sodhi, Harkanwalpreet, Panitch, Alyssa
المصدر: Biomolecules. 11(1)
مصطلحات موضوعية: chondroitin sulfate, dermatan sulfate, extracellular matrix, glycosaminoglycans, heparan sulfate, hyaluronic acid, keratan sulfate, tissue engineering, Biochemistry and Cell Biology
وصف الملف: application/pdf
URL الوصول: https://escholarship.org/uc/item/8s71g25c
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7Academic Journal
المؤلفون: Nato D. Vashakmadze, Natalia V. Zhurkova, Ludmila K. Mikhaylova, Volha Ya. Smirnova, Grigorii V. Revunenkov
المصدر: Вопросы современной педиатрии, Vol 21, Iss 6S, Pp 529-534 (2023)
مصطلحات موضوعية: mucopolysaccharidosis type iva, morquio syndrome, enzyme replacement therapy, lysosomal storage disease, glycosaminoglycans, keratan sulfate, n-acetylglucosamine-6-sulfate sulfatase, corneal opacity, short neck, Pediatrics, RJ1-570
وصف الملف: electronic resource
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8Academic Journal
المؤلفون: Bindia Sahu, Diya Deepak Sharma, Gladstone Christopher Jayakumar, Balaraman Madhan, Farhan Zameer
المصدر: Carbohydrate Polymer Technologies and Applications, Vol 5, Iss , Pp 100275- (2023)
مصطلحات موضوعية: Glycosaminoglycans, Heparin, Chondroitin sulfate, Dermatan sulfate, Keratan sulfate, Hyaluronic acid, Biochemistry, QD415-436
وصف الملف: electronic resource
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9Academic Journal
المؤلفون: Ru Chen, Weili Wang, Ronghua Yin, Ying Pan, Chen Xu, Na Gao, Xiaodong Luo, Jinhua Zhao
المصدر: Marine Drugs, Vol 21, Iss 12, p 632 (2023)
مصطلحات موضوعية: aminoglycan, structural features, keratan sulfate, depolymerization, oligosaccharides, anticoagulant activity, Biology (General), QH301-705.5
وصف الملف: electronic resource
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10Academic Journal
المؤلفون: Perez, Serge, Makshakova, Olga, Angulo, Jesus, Bedini, Emiliano, Bisio, Antonella, de Paz, Jose, Luis, Fadda, Elisa, Guerrini, Marco, Hricovini, Michal, Hricovini, Milos, Lisacek, Frederique, Nieto, Pedro, M., Pagel, Kevin, Pairardi, Giulia, Richter, Ralf, Samsonov, Sergey, A., Vivès, Romain, A., Nikitovic, Dragana, Ricard Blum, Sylvie
المساهمون: Centre de Recherches sur les Macromolécules Végétales (CERMAV), Institut de Chimie - CNRS Chimie (INC-CNRS)-Centre National de la Recherche Scientifique (CNRS)-Université Grenoble Alpes (UGA), Kazan Scientific Centre of the Russian Academy of Sciences, Consejo Superior de Investigaciones Cientificas España = Spanish National Research Council Spain (CSIC), University of Naples Federico II = Università degli studi di Napoli Federico II, Istituto di Chimica e Biochimica G. Ronzoni, National University of Ireland Maynooth (Maynooth University), Slovak Academy of Science Bratislava (SAS), Université de Genève = University of Geneva (UNIGE), Swiss Institute of Bioinformatics Genève (SIB), Institut für Chemie und Biochemie Berlin, Freie Universität Berlin, Molecular and Cellular Modeling Group, Heidelberg Institute for Theoretical Studies (HITS), Universität Heidelberg Heidelberg = Heidelberg University, University of Leeds, University of Gdańsk (UG), Institut de biologie structurale (IBS - UMR 5075), Centre National de la Recherche Scientifique (CNRS)-Institut de Recherche Interdisciplinaire de Grenoble (IRIG), Direction de Recherche Fondamentale (CEA) (DRF (CEA)), Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Direction de Recherche Fondamentale (CEA) (DRF (CEA)), Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Commissariat à l'énergie atomique et aux énergies alternatives (CEA)-Université Grenoble Alpes (UGA), University of Crete Heraklion (UOC), Institut de Chimie et Biochimie Moléculaires et Supramoléculaires (ICBMS), Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon-École Supérieure de Chimie Physique Électronique de Lyon (CPE)-Institut National des Sciences Appliquées de Lyon (INSA Lyon), Université de Lyon-Institut National des Sciences Appliquées (INSA)-Institut National des Sciences Appliquées (INSA)-Institut de Chimie - CNRS Chimie (INC-CNRS)-Centre National de la Recherche Scientifique (CNRS), ANR-19-CE13-0031,GlyCON,Décrypter la base biophysique par laquelle les glycosaminoglycanes contrôlent la signalisation des facteurs de croissance pendant le développement : une approche biomimétique(2019), ANR-21-CE29-0022,CarboCHIPS,Des biopuces pour l'étude des séquences saccharidiques au sein d'assemblages supramoléculaires par spectrométrie de masse(2021)
المصدر: ISSN: 2691-3704 ; JACS Au ; https://hal.science/hal-04019701 ; JACS Au, 2023, ⟨10.1021/jacsau.2c00569⟩ ; https://pubs.acs.org/doi/10.1021/jacsau.2c00569.
مصطلحات موضوعية: glycosaminoglycans, chondroitin sulfate, dermatan sulfate, heparan sulfate, heparin, keratan sulfate heparosan, hyaluronan, [CHIM]Chemical Sciences
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11Academic Journal
المؤلفون: Wu, Yunfei, Vos, Gaël M., Huang, Chin, Chapla, Digantkumar, Kimpel, Anne L.M., Moremen, Kelley W., de Vries, Robert P., Boons, Geert Jan
المساهمون: Afd Chemical Biology and Drug Discovery, Sub Chemical Biology and Drug Discovery, Chemical Biology and Drug Discovery
مصطلحات موضوعية: chemoenzymatic synthesis, glycosyltransferases, influenza A, keratan sulfate, Siglec, Analytical Chemistry, Chemistry (miscellaneous), Physical and Theoretical Chemistry, Organic Chemistry
وصف الملف: application/pdf
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12Academic Journal
المصدر: Department of Pediatrics Faculty Papers
مصطلحات موضوعية: humans, mice, Animals, Mucopolysaccharidosis IV, keratan sulfate, chondroitin sulfates, chondrocytes, disease models, animal, chondroitinsulfatases, Medicine and Health Sciences, Pediatrics
وصف الملف: application/pdf
Relation: https://jdc.jefferson.edu/pedsfp/147; https://jdc.jefferson.edu/context/pedsfp/article/1149/viewcontent/Mucopolysaccharidosis_IVA.pdf
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13Academic Journal
المؤلفون: Tzu-Ju Chen, Bei-Hao Hsu, Sung-Wei Lee, Ching-Chieh Yang, Yu-Feng Tian, Yu-Hsuan Kuo, Wan-Shan Li, Hsin-Hwa Tsai, Li-Ching Wu, Cheng-Fa Yeh, Chia-Lin Chou, Hong-Yue Lai
المصدر: Pathology and Oncology Research, Vol 28 (2022)
مصطلحات موضوعية: biomarker, rectal cancer, DHRS9, epithelial cell differentiation, keratan sulfate, mucin, Neoplasms. Tumors. Oncology. Including cancer and carcinogens, RC254-282, Pathology, RB1-214
وصف الملف: electronic resource
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14Academic Journal
المؤلفون: Burak Boyraz (11998699), Jessica Saatz (5734214), Inga-Marie Pompös (11998702), Michel Gad (11998705), Jens Dernedde (698160), Anna-Karina B. Maier (5536427), Oren Moscovitz (1996369), Peter H. Seeberger (255011), Heike Traub (2021464), Rudolf Tauber (314154)
مصطلحات موضوعية: Biochemistry, Physiology, Biotechnology, Space Science, Chemical Sciences not elsewhere classified, random fluorescent labeling, highly sensitive detection, extracellular matrix resulting, ocular tissue sections, keratan sulfate landscape, imaging keratan sulfate, laser ablation icp, keratan sulfate, human tissue, valuable tools, specific antibodies, ms carbohydrate, monitor alterations, metal cage, immunofluorescence microscopy, directed introduction, corneal stroma
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15Academic Journal
المؤلفون: Sylvia Stockler‐Ipsiroglu, Nahid Yazdanpanah, Mojgan Yazdanpanah, Marioara Moisa Popurs, Nataliya Yuskiv, Mara Lúcia Schmitz Ferreira Santos, Chong Ae Kim, Carolina Fischinger Moura de Souza, Charles Marques Lourenço, Carlos Eduardo Steiner, Andressa Federhen, Luciana Giugliani, Débora Maria Bastos Pereira, Luz Elena Durán‐Carabali, Roberto Giugliani
المصدر: JIMD Reports, Vol 60, Iss 1, Pp 23-31 (2021)
مصطلحات موضوعية: dystonia, keratan sulfate, mucopolysaccharidosis type IVB, spondyloepiphyseal dysplasia, type 3 GM1 gangliosidosis, β‐galactosidase, Diseases of the endocrine glands. Clinical endocrinology, RC648-665, Genetics, QH426-470
وصف الملف: electronic resource
Relation: https://doaj.org/toc/2192-8312
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16Academic Journal
المؤلفون: Harmatz, Paul R, Mengel, Eugen, Geberhiwot, Tarekegn, Muschol, Nicole, Hendriksz, Christian J, Burton, Barbara K, Jameson, Elisabeth, Berger, Kenneth I, Jester, Andrea, Treadwell, Marsha, Sisic, Zlatko, Decker, Celeste
المصدر: American Journal of Medical Genetics Part A. 173(2)
مصطلحات موضوعية: Biomedical and Clinical Sciences, Clinical Sciences, Patient Safety, Rare Diseases, Clinical Research, 6.1 Pharmaceuticals, Activities of Daily Living, Adolescent, Adult, Biomarkers, Child, Chondroitinsulfatases, Enzyme Replacement Therapy, Exercise, Female, Humans, Keratan Sulfate, Male, Mucopolysaccharidosis IV, Quality of Life, Respiratory Function Tests, Self Report, Treatment Outcome, Walking, Young Adult, mucopolysaccharidosis IV, safety, physical endurance, GALNS protein, human [supplementary concept], enzyme replacement therapy, mobility limitation, GALNS protein, human [supplementary concept], Genetics, Clinical sciences
وصف الملف: application/pdf
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17Academic Journal
المؤلفون: Kazuki Sawamoto, Subha Karumuthil-Melethil, Shaukat Khan, Molly Stapleton, Joseph T. Bruder, Olivier Danos, Shunji Tomatsu
المصدر: Molecular Therapy: Methods & Clinical Development, Vol 18, Iss , Pp 50-61 (2020)
مصطلحات موضوعية: MPS IVA, GALNS, AAV, liver targeting, keratan sulfate, skeletal dysplasia, Genetics, QH426-470, Cytology, QH573-671
وصف الملف: electronic resource
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18Academic Journal
المؤلفون: Yoshiko Takeda-Uchimura, Kazuchika Nishitsuji, Midori Ikezaki, Tomoya O. Akama, Yoshito Ihara, Fabrice Allain, Kenji Uchimura
المصدر: Frontiers in Neuroanatomy, Vol 16 (2022)
مصطلحات موضوعية: keratan sulfate (KS), B3gnt7, N-acetylglucosaminyltransferase, oligodendrocyte, adult brain, Neurosciences. Biological psychiatry. Neuropsychiatry, RC321-571, Human anatomy, QM1-695
وصف الملف: electronic resource
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19Academic Journal
المؤلفون: Vallet, Sylvain, Berthollier, Coline, Ricard-Blum, Sylvie
المساهمون: Institut de Chimie et Biochimie Moléculaires et Supramoléculaires (ICBMS), Université Claude Bernard Lyon 1 (UCBL), Université de Lyon-Université de Lyon-École Supérieure de Chimie Physique Électronique de Lyon (CPE)-Institut National des Sciences Appliquées de Lyon (INSA Lyon), Université de Lyon-Institut National des Sciences Appliquées (INSA)-Institut National des Sciences Appliquées (INSA)-Institut de Chimie - CNRS Chimie (INC-CNRS)-Centre National de la Recherche Scientifique (CNRS), Institut Français de Bioinformatique Glycomatrix project, call 2015, Fondation pour la Recherche Médicale, grant DBI20141231336, CNRS, GDR 3739, Structure, Fonction et Régulation des Glycosaminoglycanes
المصدر: ISSN: 0363-6143.
مصطلحات موضوعية: Glycosaminoglycan, Interaction network, Glycobiology, Interactome, Heparin, Heparan sulfate, Chondroitin sulfate, Dermatan sulfate, Keratan sulfate, Hyaluronan, Extracellular matrix ECM, Matrisome, [SDV]Life Sciences [q-bio], [INFO.INFO-BI]Computer Science [cs]/Bioinformatics [q-bio.QM]
Relation: info:eu-repo/semantics/altIdentifier/pmid/35544698; PUBMED: 35544698
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20Academic Journal
المؤلفون: Takeda-Uchimura, Yoshiko, Nishitsuji, Kazuchika, Ikezaki, Midori, Akama, Tomoya O., Ihara, Yoshito, Allain, Fabrice, Uchimura, Kenji
المساهمون: Université de Lille, CNRS, Unité de Glycobiologie Structurale et Fonctionnelle UMR 8576 UGSF, Wakayama University, Kansai University, Unité de Glycobiologie Structurale et Fonctionnelle (UGSF) - UMR 8576
مصطلحات موضوعية: keratan sulfate (KS), B3gnt7, N-acetylglucosaminyltransferase, oligodendrocyte, adult brain
وصف الملف: application/octet-stream; application/rdf+xml; charset=utf-8
Relation: Frontiers in Neuroanatomy; Front. Neuroanat.; http://hdl.handle.net/20.500.12210/74299