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1Academic Journal
المؤلفون: Stephen D. Betschel, Teresa Caballero, Douglas H. Jones, Hilary J. Longhurst, Michael Manning, Sally van Kooten, Markus Heckmann, Sherry Danese, Ledia Goga, Autumn Ford Burnette
المصدر: Allergy, Asthma & Clinical Immunology, Vol 20, Iss 1, Pp 1-8 (2024)
مصطلحات موضوعية: Hereditary angioedema (HAE), Attacks, On-demand treatment, Decision-making, Burden of treatment, Survey, HAE attack journey, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
Relation: https://doaj.org/toc/1710-1492
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2Academic Journal
المؤلفون: Anna Valerieva, Hilary J. Longhurst
المصدر: Frontiers in Allergy, Vol 3 (2022)
مصطلحات موضوعية: bradykinin B2 receptor antagonist, complement C1 inhibitor protein, hereditary angioedema, kallikreins, prophylaxis, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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3Academic Journal
المؤلفون: Konrad Bork, John T. Anderson, Teresa Caballero, Timothy Craig, Douglas T. Johnston, H. Henry Li, Hilary J. Longhurst, Cristine Radojicic, Marc A. Riedl
المصدر: Allergy, Asthma & Clinical Immunology, Vol 17, Iss 1, Pp 1-14 (2021)
مصطلحات موضوعية: Consensus document, Disease burden, Hereditary angioedema, Management, Quality of life, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
Relation: https://doaj.org/toc/1710-1492
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4Academic Journal
المؤلفون: H. Henry Li, Bruce Zuraw, Hilary J. Longhurst, Marco Cicardi, Konrad Bork, James Baker, William Lumry, Jonathan Bernstein, Michael Manning, Donald Levy, Marc A. Riedl, Henrike Feuersenger, Subhransu Prusty, Ingo Pragst, Thomas Machnig, Timothy Craig, for the COMPACT Investigators
المصدر: Allergy, Asthma & Clinical Immunology, Vol 15, Iss 1, Pp 1-8 (2019)
مصطلحات موضوعية: C1-esterase inhibitor protein, C1-INH (SC), COMPACT study, HAEGARDA®, Hereditary angioedema, Long-term prophylaxis, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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5Academic Journal
المؤلفون: Anette Bygum, Teresa Caballero, Anete S. Grumach, Hilary J. Longhurst, Laurence Bouillet, Werner Aberer, Andrea Zanichelli, Jaco Botha, Irmgard Andresen, Marcus Maurer, for the IOS Study Group
المصدر: Clinical and Translational Allergy, Vol 9, Iss 1, Pp 1-8 (2019)
مصطلحات موضوعية: Hereditary angioedema, Icatibant Outcome Survey, Safety, Elderly, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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6Academic Journal
المؤلفون: Anna Duckworth, Hilary J. Longhurst, Jane K. Paxton, Chris J. Scotton
المصدر: Frontiers in Medicine, Vol 8 (2021)
مصطلحات موضوعية: pulmonary fibrosis, herpes virus, CMV, EBV, telomeres, senescence, Medicine (General), R5-920
وصف الملف: electronic resource
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7Academic Journal
المؤلفون: Andrea Zanichelli, Markus Magerl, Hilary J. Longhurst, Werner Aberer, Teresa Caballero, Laurence Bouillet, Anette Bygum, Anete S. Grumach, Jaco Botha, Irmgard Andresen, Marcus Maurer, the IOS Study Group
المصدر: Clinical and Translational Allergy, Vol 8, Iss 1, Pp 1-5 (2018)
مصطلحات موضوعية: Hereditary angioedema, HAE, C1-INH-HAE, Diagnosis, Delay in diagnosis, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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8Academic Journal
المؤلفون: Hilary J. Longhurst, John Dempster, Lorena Lorenzo, Matthew Buckland, Sofia Grigoriadou, Christine Symons, Claire Bethune, Vincent Fabien, Catherine Bangs, Tomaz Garcez
المصدر: Allergy, Asthma & Clinical Immunology, Vol 14, Iss 1, Pp 1-11 (2018)
مصطلحات موضوعية: C1-inhibitor deficiency, Acquired angioedema, Hereditary angioedema, Icatibant, Icatibant Outcome Survey, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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9Academic Journal
المؤلفون: Teresa Caballero, Andrea Zanichelli, Werner Aberer, Marcus Maurer, Hilary J. Longhurst, Laurence Bouillet, Irmgard Andresen, the IOS Study Group
المصدر: Clinical and Translational Allergy, Vol 8, Iss 1, Pp 1-10 (2018)
مصطلحات موضوعية: Hereditary angioedema, Icatibant, Bradykinin, Body mass index, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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10Academic Journal
المؤلفون: Marc A. Riedl, Jonathan A. Bernstein, Timothy Craig, Aleena Banerji, Markus Magerl, Marco Cicardi, Hilary J. Longhurst, Mustafa M. Shennak, William H. Yang, Jennifer Schranz, Jovanna Baptista, Paula J. Busse
المصدر: Clinical and Translational Allergy, Vol 7, Iss 1, Pp 1-10 (2017)
مصطلحات موضوعية: Hereditary angioedema, Lanadelumab, Monoclonal antibody, Bradykinin, Plasma kallikrein, Prophylaxis, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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11Academic Journal
المؤلفون: Werner Aberer, Marcus Maurer, Laurence Bouillet, Andrea Zanichelli, Teresa Caballero, Hilary J. Longhurst, Amandine Perrin, Irmgard Andresen, for the IOS Study Group
المصدر: Allergy, Asthma & Clinical Immunology, Vol 13, Iss 1, Pp 1-9 (2017)
مصطلحات موضوعية: Hereditary angioedema, Icatibant, Breakthrough attacks, Prophylaxis, Bradykinin, Immunologic diseases. Allergy, RC581-607
وصف الملف: electronic resource
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12
المؤلفون: Hilary J Longhurst, Anna Valerieva
المصدر: Journal of Asthma and Allergy. 16:269-277
مصطلحات موضوعية: Pulmonary and Respiratory Medicine, Immunology and Allergy
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13
المؤلفون: Emel Aygören-Pürsün, Andrea Zanichelli, Danny M Cohn, Mauro Cancian, Roman Hakl, Tamar Kinaciyan, Markus Magerl, Inmaculada Martinez-Saguer, Marcin Stobiecki, Henriette Farkas, Sorena Kiani-Alikhan, Vesna Grivcheva-Panovska, Jonathan A Bernstein, H Henry Li, Hilary J Longhurst, Paul K Audhya, Michael D Smith, Christopher M Yea, Andreas Maetzel, Daniel K Lee, Edward P Feener, Richard Gower, William R Lumry, Aleena Banerji, Marc A Riedl, Marcus Maurer
المساهمون: Vascular Medicine, ACS - Atherosclerosis & ischemic syndromes, Amsterdam Cardiovascular Sciences
المصدر: The Lancet, 401(10375), 458-469. Elsevier Limited
مصطلحات موضوعية: General Medicine
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14
المؤلفون: Hilary J. Longhurst, Rohan Ameratunga
المصدر: The New England journal of medicine. 386(11)
مصطلحات موضوعية: Angioedemas, Hereditary, Oligonucleotides, Humans, General Medicine, Oligonucleotides, Antisense, Complement C1 Inhibitor Protein
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15
المصدر: Frontiers Research Topics ISBN: 9782832508466
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16Academic Journal
المؤلفون: Sai S Duraisingham, Matthew Buckland, John Dempster, Lorena Lorenzo, Sofia Grigoriadou, Hilary J Longhurst
المصدر: PLoS ONE, Vol 9, Iss 6, p e100324 (2014)
Relation: http://europepmc.org/articles/PMC4074074?pdf=render; https://doaj.org/toc/1932-6203; https://doaj.org/article/fbd8d6be68194714a4ad435a1b6858a2
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17Academic Journal
المؤلفون: Hilary J Longhurst
المصدر: Vascular Health and Risk Management, Vol 2010, Iss default, Pp 795-802 (2010)
مصطلحات موضوعية: Diseases of the circulatory (Cardiovascular) system, RC666-701
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18
المؤلفون: Marcus, Maurer, Werner, Aberer, Rosana, Agondi, Mona, Al-Ahmad, Maryam Ali, Al-Nesf, Ignacio, Ansotegui, Rand, Arnaout, Luisa Karla, Arruda, Riccardo, Asero, Emel, Aygören-Pürsün, Aleena, Banerji, Andrea, Bauer, Moshe, Ben-Shoshan, Alejandro, Berardi, Jonathan A, Bernstein, Stephen, Betschel, Carsten, Bindslev-Jensen, Mojca, Bizjak, Isabelle, Boccon-Gibod, Konrad, Bork, Laurence, Bouillet, Henrik Balle, Boysen, Nicholas, Brodszki, Sigurd, Broesby-Olsen, Paula, Busse, Thomas, Buttgereit, Anette, Bygum, Teresa, Caballero, Régis A, Campos, Mauro, Cancian, Ivan, Cherrez-Ojeda, Danny M, Cohn, Célia, Costa, Timothy, Craig, Paulo Ricardo, Criado, Roberta F, Criado, Dorottya, Csuka, Joachim, Dissemond, Aurélie, Du-Thanh, Luis Felipe, Ensina, Ragıp, Ertaş, José E, Fabiani, Claudio, Fantini, Henriette, Farkas, Silvia Mariel, Ferrucci, Ignasi, Figueras-Nart, Natalia L, Fili, Daria, Fomina, Atsushi, Fukunaga, Asli, Gelincik, Ana, Giménez-Arnau, Kiran, Godse, Mark, Gompels, Margarida, Gonçalo, Maia, Gotua, Richard, Gower, Anete S, Grumach, Guillermo, Guidos-Fogelbach, Michihiro, Hide, Natalia, Ilina, Naoko, Inomata, Thilo, Jakob, Dario O, Josviack, Hye-Ryun, Kang, Allen, Kaplan, Alicja, Kasperska-Zając, Constance, Katelaris, Aharon, Kessel, Andreas, Kleinheinz, Emek, Kocatürk, Mitja, Košnik, Dorota, Krasowska, Kanokvalai, Kulthanan, M Sendhil, Kumaran, José Ignacio, Larco Sousa, Hilary J, Longhurst, William, Lumry, Andrew, MacGinnitie, Markus, Magerl, Michael P, Makris, Alejandro, Malbrán, Alexander, Marsland, Inmaculada, Martinez-Saguer, Iris V, Medina, Raisa, Meshkova, Martin, Metz, Iman, Nasr, Jan, Nicolay, Chikako, Nishigori, Isao, Ohsawa, Kemal, Özyurt, Nikolaos G, Papadopoulos, Claudio A S, Parisi, Jonathan Grant, Peter, Wolfgang, Pfützner, Todor, Popov, Nieves, Prior, German D, Ramon, Adam, Reich, Avner, Reshef, Marc A, Riedl, Bruce, Ritchie, Heike, Röckmann-Helmbach, Michael, Rudenko, Andaç, Salman, Mario, Sanchez-Borges, Peter, Schmid-Grendelmeier, Faradiba S, Serpa, Esther, Serra-Baldrich, Farrukh R, Sheikh, William, Smith, Angèle, Soria, Petra, Staubach, Urs C, Steiner, Marcin, Stobiecki, Gordon, Sussman, Anna, Tagka, Simon Francis, Thomsen, Regina, Treudler, Solange, Valle, Martijn, van Doorn, Lilian, Varga, Daniel O, Vázquez, Nicola, Wagner, Liangchun, Wang, Christina, Weber-Chrysochoou, Young-Min, Ye, Anna, Zalewska-Janowska, Andrea, Zanichelli, Zuotao, Zhao, Yuxiang, Zhi, Torsten, Zuberbier, Ricardo D, Zwiener, Anthony, Castaldo
المصدر: Allergy. 75(8)
مصطلحات موضوعية: Urticaria, Humans, Angioedema
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19
المؤلفون: Paul, Tuijnenburg, Hana, Lango Allen, Siobhan O, Burns, Daniel, Greene, Machiel H, Jansen, Emily, Staples, Jonathan, Stephens, Keren J, Carss, Daniele, Biasci, Helen, Baxendale, Moira, Thomas, Anita, Chandra, Sorena, Kiani-Alikhan, Hilary J, Longhurst, Suranjith L, Seneviratne, Eric, Oksenhendler, Ilenia, Simeoni, Godelieve J, de Bree, Anton T J, Tool, Ester M M, van Leeuwen, Eduard H T M, Ebberink, Alexander B, Meijer, Salih, Tuna, Deborah, Whitehorn, Matthew, Brown, Ernest, Turro, Adrian J, Thrasher, Kenneth G C, Smith, James E, Thaventhiran, Taco W, Kuijpers, Christopher, Watt
المصدر: The Journal of Allergy and Clinical Immunology
مصطلحات موضوعية: Adult, Male, Adolescent, T-Lymphocytes, NF-κB, Nuclear factor κB, RHD, Rel homology domain, Article, NIHRBR-RD, NIHR BioResource–Rare Diseases, Young Adult, Loss of Function Mutation, CVID, Common variable immunodeficiency, nuclear factor κB1, Humans, PML, Progressive multifocal leukoencephalopathy, Child, Aged, Aged, 80 and over, B cells, B-Lymphocytes, VEP, Variant effect predictor, LOF, Loss-of-function, NF-kappa B, Infant, Newborn, Infant, NF-kappa B p50 Subunit, Middle Aged, CFSE, Carboxyfluorescein succinimidyl ester, Europe, Common Variable Immunodeficiency, Phenotype, NFKB1, Nuclear factor κB subunit 1, Child, Preschool, Mutation, Female, PID, Primary immunodeficiency disease
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20
المؤلفون: Matthew Helbert, Graham Bothamley, Lourdes Ceron-Gutierrez, Rainer Doffinger, Gabriela Barcenas-Morales, Stéphanie Dupuis, Clara Espitia-Pinzon, Hilary J. Longhurst, Jean-Laurent Casanova, Kun Yang, Dinakantha S. Kumararatne, Neil Barnes
المصدر: Clinical Infectious Diseases. 38:e10-e14
مصطلحات موضوعية: Male, Microbiology (medical), medicine.medical_treatment, Mycobacterium Infections, Nontuberculous, Mycobacterium chelonae, Autoimmunity, medicine.disease_cause, Peripheral blood mononuclear cell, Immunoglobulin G, Mycobacterium tuberculosis, Interferon-gamma, Hypothyroidism, Humans, Tuberculosis, Medicine, Interferon gamma, Autoantibodies, biology, business.industry, Autoantibody, Middle Aged, biology.organism_classification, Virology, Diabetes Mellitus, Type 1, Infectious Diseases, Cytokine, Immunology, biology.protein, Disease Susceptibility, business, medicine.drug