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المؤلفون: Eun-Jin Lee, Monica S. Diaz-Aguilar, Hyejung Min, Jihee Choi, Diego A. Valdez Duran, Julia M. Grandjean, R. Luke Wiseman, Heike Kroeger, Jonathan H. Lin
المصدر: The American journal of pathology.
مصطلحات موضوعية: Pathology and Forensic Medicine
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المؤلفون: Jonathan H. Lin, R. Luke Wiseman, Jennifer Okalova, Michel Michaelides, Amanda Nguyen, Daphne D. Bindels, Rebecca Mastey, Joseph Carroll, Evan T. Powers, Julia M. D. Grandjean, Wei-Chieh Jerry Chiang, Jeffery W. Kelly, Heike Kroeger, Neil Grimsey
المصدر: Proc Natl Acad Sci U S A
مصطلحات موضوعية: Achromatopsia, genetic structures, Induced Pluripotent Stem Cells, Activating transcription factor, Gene Expression, Color Vision Defects, Biology, Retina, chemistry.chemical_compound, medicine, Humans, Induced pluripotent stem cell, Vision, Ocular, Multidisciplinary, ATF6, Endoplasmic reticulum, Retinal, Biological Sciences, medicine.disease, Cone Opsins, eye diseases, Cell biology, Activating Transcription Factor 6, Organoids, HEK293 Cells, chemistry, Unfolded protein response, Retinal Cone Photoreceptor Cells, sense organs, Visual phototransduction
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المؤلفون: Jonathan H. Lin, Patricia M. Gaffney, John H. Kim, Heike Kroeger, Christina J. Sigurdson, Jerry Yang, Kevin J. Cao
المصدر: Translational Vision Science & Technology
مصطلحات موضوعية: Genetically modified mouse, Pathology, medicine.medical_specialty, Amyloid, Biomedical Engineering, Mice, Transgenic, Plaque, Amyloid, Article, Retina, law.invention, Immunolabeling, chemistry.chemical_compound, Mice, In vivo, Confocal microscopy, law, Alzheimer Disease, mental disorders, medicine, Animals, Humans, Amyloid beta-Peptides, Chemistry, amyloid, imaging, Retinal, Alzheimer's disease, Ophthalmology, medicine.anatomical_structure, Immunostaining
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المؤلفون: Wei-Chieh Chiang, R. Luke Wiseman, Joseph Carroll, Amanda Nguyen, Julia M. D. Grandjean, Heike Kroeger, Jennifer Okalova, Jonathan H. Lin, Neil Grimsey, Evan T. Powers, Michel Michaelides, Jeffery W. Kelly, Daphne S. Bindels, Rebecca Mastey
مصطلحات موضوعية: genetic structures, ATF6, Endoplasmic reticulum, Activating transcription factor, Retinal, Biology, Cell biology, chemistry.chemical_compound, Proteostasis, chemistry, Unfolded protein response, Organoid, sense organs, Visual phototransduction
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المؤلفون: Daniel L. Chao, Jonathan H. Lin, Anthony T. Moore, Isabelle Audo, Rebecca Mastey, Chloe Xiaoke Bi, Dorota Skowronska-Krawczyk, Britta Baumann, Kyle Kim, Leon Chea, Wei-Chieh Chiang, Susanne Kohl, R. Luke Wiseman, Joseph Carroll, Eun-Jin Lee, Scott R. Lambert, Heike Kroeger, Julia M. D. Grandjean, Stephen H. Tsang
المصدر: JCI Insight
مصطلحات موضوعية: Male, Achromatopsia, Adolescent, genetic structures, Color Vision Defects, Biology, Exon, chemistry.chemical_compound, medicine, Humans, Allele, Gene, Alleles, Sequence Deletion, Genetics, Retina, Base Sequence, medicine.diagnostic_test, Retinal, Exons, General Medicine, medicine.disease, eye diseases, Activating Transcription Factor 6, HEK293 Cells, medicine.anatomical_structure, chemistry, Female, Trans-acting, Research Article, Electroretinography
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المؤلفون: Wei-Chieh Chiang, Amanda Nguyen, Jonathan H. Lin, Julia Felden, Heike Kroeger
المصدر: The FEBS Journal. 286:399-412
مصطلحات موضوعية: 0301 basic medicine, Retinal degeneration, Ocular health, Eye Diseases, genetic structures, Eye disease, Disease, Endoplasmic Reticulum, Eye, Biochemistry, Article, Regulatory molecules, 03 medical and health sciences, 0302 clinical medicine, medicine, Animals, Humans, Molecular Biology, business.industry, Endoplasmic reticulum, fungi, Cell Biology, Endoplasmic Reticulum Stress, medicine.disease, eye diseases, 030104 developmental biology, medicine.anatomical_structure, 030220 oncology & carcinogenesis, Unfolded Protein Response, Unfolded protein response, Human eye, sense organs, business, Neuroscience, Signal Transduction
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المؤلفون: Daphne S. Bindels, Amanda Nguyen, Jonathan H. Lin, Julia M. D. Grandjean, Wei-Chieh Chiang, Rebecca Mastey, Michel Michaelides, Evan T. Powers, Jeffery W. Kelly, Joseph Carroll, Heike Kroeger, R. Luke Wiseman, Jennifer Okalova, Neil Grimsey
المصدر: SSRN Electronic Journal.
مصطلحات موضوعية: Pathology, medicine.medical_specialty, genetic structures, ATF6, Endoplasmic reticulum, Retinal, Biology, chemistry.chemical_compound, Proteostasis, chemistry, Unfolded protein response, medicine, Organoid, sense organs, Induced pluripotent stem cell, Visual phototransduction
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المؤلفون: Jonathan H. Lin, Wei-Chieh Chiang, Heike Kroeger, Lulu Chea
المصدر: Adv Exp Med Biol
Retinal Degenerative Diseases ISBN: 9783030273774مصطلحات موضوعية: Protein Folding, Chemistry, ATF6, Endoplasmic reticulum, Activating transcription factor, Golgi Apparatus, Golgi apparatus, Endoplasmic Reticulum Stress, Article, Cell biology, Activating Transcription Factor 6, 03 medical and health sciences, symbols.namesake, 0302 clinical medicine, RNA splicing, Mutation, symbols, Unfolded protein response, Retinal Cone Photoreceptor Cells, Humans, 030212 general & internal medicine, Signal transduction, Transcription factor, Signal Transduction
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9Electronic Resource
المؤلفون: Eun-Jin, Lee, Wei-Chieh Jerry, Chiang, Heike, Kroeger, Chloe Xiaoke, Bi, Daniel L., Chao, Dorota, Skowronska-Krawczyk, Rebecca R., Mastey, Stephen H., Tsang, Leon, Chea, Kyle, Kim, Scott R., Lambert, Julia M.D., Grandjean, Britta, Baumann, Isabelle, Audo, Susanne, Kohl, Anthony T., Moore, R. Luke, Wiseman, Joseph, Carroll, Jonathan H., Lin
مصطلحات الفهرس: Journal Article, VoR
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المؤلفون: JoAnn Trejo, Heike Kroeger, Jonathan H. Lin, Ryan J Paxman, Wei-Chieh Chiang, Ying Jones, Neil Grimsey, Stephen H. Tsang, Jeffery W. Kelly, Lars Plate, Peter X. Shaw, R. Luke Wiseman, Evan T. Powers
المصدر: Science signaling, vol 11, iss 517
مصطلحات موضوعية: 0301 basic medicine, 1.1 Normal biological development and functioning, Induced Pluripotent Stem Cells, Activating transcription factor, Gene Expression, Biology, Endoplasmic Reticulum, Regenerative Medicine, Biochemistry, Article, Cell Line, Mesoderm, Small Molecule Libraries, 03 medical and health sciences, 0302 clinical medicine, Underpinning research, Genetics, Animals, Humans, 2.1 Biological and endogenous factors, Stem Cell Research - Embryonic - Human, Aetiology, Induced pluripotent stem cell, Molecular Biology, Transcription factor, Stem Cell Research - Induced Pluripotent Stem Cell, Stem Cell Research - Induced Pluripotent Stem Cell - Human, ATF6, Endoplasmic reticulum, Cell Differentiation, Cell Biology, Endoplasmic Reticulum Stress, Stem Cell Research, Embryonic stem cell, Activating Transcription Factor 6, Cell biology, 030104 developmental biology, Mutation, Unfolded Protein Response, Unfolded protein response, Stem Cell Research - Nonembryonic - Non-Human, Generic health relevance, Biochemistry and Cell Biology, Stem cell, 030217 neurology & neurosurgery, Signal Transduction, Biotechnology
وصف الملف: application/pdf
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11
المؤلفون: S. Yu, C. E. Bueso-Ramos, Steve Kornblau, Jaroslav Jelinek, Andrew Kelly, Rong He, Yue Lu, Justin T. Lee, Matteo Cesaroni, Rodolphe Taby, Farhad Ravandi, Shoudan Liang, Sherry Pierce, Y. Li, Frank Neumann, Jean Pierre J. Issa, Bela Patel, Jumpei Yamazaki, Heike Kroeger, Hagop M. Kantarjian
المصدر: Leukemia
مصطلحات موضوعية: 0301 basic medicine, Adult, Male, Risk, Cancer Research, IDH1, Adolescent, Datasets as Topic, Pilot Projects, Biology, Gene mutation, Article, 03 medical and health sciences, Young Adult, 0302 clinical medicine, AML, CEBPA, Humans, Epigenetics, neoplasms, Aged, Retrospective Studies, DNA methylation, CpG Island Methylator Phenotype, CIMP, Myeloid leukemia, Hematology, DNA, Neoplasm, Middle Aged, Prognosis, Survival Analysis, digestive system diseases, Isocitrate Dehydrogenase, 3. Good health, Leukemia, Myeloid, Acute, 030104 developmental biology, Phenotype, Oncology, CpG site, 030220 oncology & carcinogenesis, Mutation, Cancer research, CpG Islands, Female, IDH2
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المؤلفون: Jonathan H. Lin, Heike Kroeger, Katherine J. Wert, Stephen H. Tsang, Frances Wu
مصطلحات موضوعية: business.industry, Medicine, business, Neuroscience, Mechanism (sociology)
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المؤلفون: Rong He, Carlos E. Bueso-Ramos, Lanlan Shen, Woonbok Chung, Kimie Kondo, Jaroslav Jelinek, Hagop M. Kantarjian, Jean Pierre J. Issa, Heike Kroeger, Li Zhang, Marcos R. Estecio
المصدر: Blood. 112:1366-1373
مصطلحات موضوعية: Adult, Myeloid, Adolescent, Immunology, Biology, Biochemistry, Recurrence, hemic and lymphatic diseases, medicine, Humans, Epigenetics, Neoplasia, Cancer, Myeloid leukemia, Genomics, Cell Biology, Hematology, Methylation, DNA Methylation, Middle Aged, medicine.disease, Leukemia, Myeloid, Acute, Leukemia, medicine.anatomical_structure, CpG site, Case-Control Studies, Karyotyping, DNA methylation, Disease Progression, Cancer research, CpG Islands, Genes, Neoplasm
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14
المؤلفون: Michael T. Matthes, Douglas Yasumura, Jonathan H. Lin, Marcel V. Alavi, Wei-Chieh Chiang, Douglas B. Gould, Matthew M. LaVail, Heike Kroeger, Takao Iwawaki
المصدر: Investigative ophthalmology & visual science, vol 56, iss 11
Alavi, MV; Chiang, WC; Kroeger, H; Yasumura, D; Matthes, MT; Iwawaki, T; et al.(2015). In vivo visualization of endoplasmic reticulum stress in the retina using the ERAI reporter mouse. Investigative Ophthalmology and Visual Science, 56(11), 6961-6970. doi: 10.1167/iovs.15-16969. UCSF: Retrieved from: http://www.escholarship.org/uc/item/9xx0d1f0مصطلحات موضوعية: Genetically modified mouse, funduscopy, Aging, genetic structures, Transgene, Mice, Transgenic, Biology, Protein Serine-Threonine Kinases, Endoplasmic Reticulum, GFP, Eye, Ophthalmology & Optometry, Polymerase Chain Reaction, Medical and Health Sciences, Retina, Transgenic, Green fluorescent protein, chemistry.chemical_compound, Mice, In vivo, Animals, Longitudinal Studies, Tomography, Eye Disease and Disorders of Vision, Ultrasonography, Endoplasmic reticulum, Tunicamycin, Neurosciences, Membrane Proteins, Biological Sciences, Protein-Serine-Threonine Kinases, Endoplasmic Reticulum Stress, Molecular biology, eye diseases, Ophthalmoscopy, Retinal Cell Biology, chemistry, Optical Coherence, Unfolded protein response, Signal transduction, ER stress, Tomography, Optical Coherence, Signal Transduction
وصف الملف: application/pdf
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المؤلفون: Judith A. Coppinger, Michael T. Matthes, Heike Kroeger, Douglas Yasumura, Krzysztof Palczewski, Carissa Messah, Wei Chieh Chiang, Matthew M. LaVail, Jonathan H. Lin, Sanae Sakami
المصدر: Molecular Neurobiology, vol 52, iss 1
Molecular neurobiology, vol 52, iss 1
Chiang, WC; Kroeger, H; Sakami, S; Messah, C; Yasumura, D; Matthes, MT; et al.(2015). Robust Endoplasmic Reticulum-Associated Degradation of Rhodopsin Precedes Retinal Degeneration. Molecular Neurobiology, 52(1), 679-695. doi: 10.1007/s12035-014-8881-8. UC San Diego: Retrieved from: http://www.escholarship.org/uc/item/0388f1mtمصطلحات موضوعية: Retinal degeneration, genetic structures, Messenger, Apoptosis, Inbred C57BL, Photoreceptor cell, Unfolded protein response, Mice, 2.1 Biological and endogenous factors, Psychology, Gene Knock-In Techniques, Aetiology, biology, Retinal Degeneration, Endoplasmic Reticulum-Associated Degradation, Protein-Serine-Threonine Kinases, Endoplasmic Reticulum Stress, Cell biology, medicine.anatomical_structure, Neurology, Rhodopsin, Cognitive Sciences, Signal transduction, ER stress, Signal Transduction, Neuroscience (miscellaneous), Protein Serine-Threonine Kinases, Protein degradation, Endoplasmic-reticulum-associated protein degradation, Article, Retina, Cellular and Molecular Neuroscience, medicine, Animals, Immunoprecipitation, Retinal Photoreceptor Cell Inner Segment, RNA, Messenger, Eye Disease and Disorders of Vision, Neurology & Neurosurgery, Endoplasmic reticulum, Ubiquitination, Neurosciences, Membrane Proteins, Newborn, medicine.disease, Mice, Inbred C57BL, Animals, Newborn, Proteolysis, biology.protein, RNA, sense organs, Rod photoreceptor, Transcription Factor CHOP
وصف الملف: application/pdf
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المؤلفون: Lulu Huang, Rachid Karam, Heike Kroeger, Chih-Hong Lou, Miles F. Wilkinson, Jonathan H. Lin
المصدر: EMBO reports. 16(5)
مصطلحات موضوعية: endocrine system, Transcription, Genetic, Genetic Vectors, Gene Expression, Regulatory Factor X Transcription Factors, Biology, Protein Serine-Threonine Kinases, environment and public health, digestive system, Biochemistry, Cell Line, Pathogenesis, Mice, Endoribonucleases, Gene Order, Genetics, Animals, RNA, Messenger, RNA, Small Interfering, Molecular Biology, Mice, Knockout, RNA quality control, Endoplasmic reticulum, fungi, RNA, RNA-Binding Proteins, Endoplasmic Reticulum Stress, In vitro, Hot off the Press, Cell biology, Nonsense Mediated mRNA Decay, DNA-Binding Proteins, Gene Expression Regulation, biological sciences, Unfolded protein response, Unfolded Protein Response, RNA Interference, Function (biology), Intracellular, Transcription Factors
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المؤلفون: Michael T. Matthes, Krzysztof Palczewski, Heike Kroeger, Jonathan H. Lin, Matthew M. LaVail, Douglas Yasumura, Wei-Chieh Chiang, Carissa Messah, Sanae Sakami
المصدر: The FASEB Journal. 28
مصطلحات موضوعية: Retinal degeneration, Retina, genetic structures, biology, Chemistry, Mutant, Endoplasmic-reticulum-associated protein degradation, medicine.disease, Biochemistry, eye diseases, Cell biology, medicine.anatomical_structure, Rhodopsin, Genetics, medicine, biology.protein, Missense mutation, sense organs, Receptor, Molecular Biology, Biotechnology, Visual phototransduction
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المؤلفون: Heike Kroeger, Matthew M. LaVail, Jonathan H. Lin
المصدر: Retinal Degenerative Diseases ISBN: 9781461432081
Kroeger, H; Lavail, MM; & Lin, JH. (2014). Endoplasmic reticulum stress in vertebrate mutant rhodopsin models of retinal degeneration. UC San Diego: Retrieved from: http://www.escholarship.org/uc/item/1zm978dzمصطلحات موضوعية: Retinal degeneration, Photoreceptors, Rhodopsin, genetic structures, Mutant, Mice, Transgenic, Biology, Neurodegenerative, Endoplasmic Reticulum, Eye, Medical and Health Sciences, Article, Photoreceptor cell, Transgenic, Mice, Xenopus laevis, Rare Diseases, Species Specificity, General & Internal Medicine, Retinitis pigmentosa, medicine, Genetics, Animals, Humans, 2.1 Biological and endogenous factors, Aetiology, Eye Disease and Disorders of Vision, Animal, Endoplasmic reticulum, Retinal Degeneration, Neurosciences, medicine.disease, Endoplasmic Reticulum Stress, Cell biology, Rats, Disease Models, Animal, medicine.anatomical_structure, P23H rhodopsin, Vertebrates, Disease Models, Unfolded protein response, biology.protein, Unfolded Protein Response, sense organs, Rats, Transgenic, Signal transduction
وصف الملف: application/pdf
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المؤلفون: Rong He, Steven M. Kornblau, Carlos E. Bueso-Ramos, Rodolphe Taby, Sijia Yu, Farhad Ravandi, Jean Pierre J. Issa, Jaroslav Jelinek, Andrew Kelly, Yue Lu, Hagop M. Kantarjain, Matteo Cesaroni, Shoudan Liang, Heike Kroeger, Jumpei Yamazaki, Sherry Pierce, Justin T. Lee, Frank Neumann
المصدر: Cancer Research. 76:2779-2779
مصطلحات موضوعية: Cancer Research, NPM1, CpG Island Methylator Phenotype, Methylation, Gene mutation, Biology, digestive system diseases, Oncology, CpG site, CEBPA, DNA methylation, Cancer research, Epigenetics, neoplasms
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المؤلفون: Jonathan H. Lin, Wei-Chieh Chiang, Heike Kroeger
المصدر: Retinal Degenerative Diseases ISBN: 9781461406303
مصطلحات موضوعية: chemistry.chemical_classification, Rhodopsin, Glycosylation, biology, Chemistry, Endoplasmic reticulum, Retinal Degeneration, macromolecular substances, Anatomy, Endoplasmic-reticulum-associated protein degradation, Endoplasmic Reticulum, Article, Cell biology, chemistry.chemical_compound, Membrane protein, biology.protein, Humans, ERAD pathway, Proteostasis Deficiencies, Glycoprotein, Secretory pathway, Glycoproteins, Photoreceptor Cells, Vertebrate