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1Academic Journal
المؤلفون: Blanka Pinkova, Hana Buckova, Romana Borska, Lenka Fajkusova
المصدر: Biomedical Papers, Vol 164, Iss 4, Pp 357-365 (2020)
مصطلحات موضوعية: ichthyosis, diagnostics, molecular analysis of dna, therapy, Medicine
وصف الملف: electronic resource
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2Academic Journal
المؤلفون: Jemima E. Mellerio, Maya El Hachem, Nathalia Bellon, Giovanna Zambruno, Hana Buckova, Rudolf Autrata, Carmen Salavastru, Tamara Caldaro, Celine Greco, Cristina Has, Christine Bodemer
المصدر: Orphanet Journal of Rare Diseases, Vol 15, Iss 1, Pp 1-10 (2020)
مصطلحات موضوعية: Epidermolysis bullosa, Blister, Esophageal obstruction, Airway obstruction, Corneal erosion, Urinary retention, Medicine
وصف الملف: electronic resource
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3Academic Journal
المؤلفون: Romana Borská, Blanka Pinková, Kamila Réblová, Hana Bučková, Lenka Kopečková, Jitka Němečková, Alena Puchmajerová, Marcela Malíková, Markéta Hermanová, Lenka Fajkusová
المصدر: Orphanet Journal of Rare Diseases, Vol 14, Iss 1, Pp 1-5 (2019)
مصطلحات موضوعية: Autosomal recessive congenital ichthyosis, Keratinopathic ichthyosis, In silico analysis, 3D protein structure, Medicine
Relation: http://link.springer.com/article/10.1186/s13023-019-1076-7; https://doaj.org/toc/1750-1172; https://doaj.org/article/43bc9ac616384e6fadfac80169ee5993
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4
المؤلفون: Jana Kravcova, William Steingartner, Hana Buckova
المصدر: 2021 19th International Conference on Emerging eLearning Technologies and Applications (ICETA).
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5
المؤلفون: Carmen Salavastru, Jemima E. Mellerio, Cristina Has, Christine Bodemer, P Fischer, M. El Hachem, Céline Greco, Hana Buckova, P Nevoránková, Giovanna Zambruno, M Friedová
المصدر: Journal of the European Academy of Dermatology and Venereology : JEADVReferences. 35(12)
مصطلحات موضوعية: Position statement, medicine.medical_specialty, Consensus, integumentary system, Health professionals, business.industry, Inherited epidermolysis bullosa, Dermatology, Disease, medicine.disease, Infectious Diseases, Blister, Rare Diseases, Medicine, Humans, Clinical severity, Epidermolysis bullosa, business, Epidermolysis Bullosa, Skin blisters, Skin
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6
المؤلفون: Jiri Dostal, Hana Buckova
المصدر: 2020 18th International Conference on Emerging eLearning Technologies and Applications (ICETA).
مصطلحات موضوعية: Czech, School teachers, Information and Communications Technology, Informatics, Pedagogy, Perspective (graphical), ComputingMilieux_COMPUTERSANDEDUCATION, language, Survey research, Sociology, Curriculum, language.human_language
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7
المؤلفون: Hana Buckova, Jiri Dostal
المصدر: 2019 IEEE 15th International Scientific Conference on Informatics.
مصطلحات موضوعية: Enthusiasm, Computational thinking, media_common.quotation_subject, Professional development, ComputingMilieux_COMPUTERSANDEDUCATION, Mathematics education, Negative attitude, Psychology, Curriculum, Coding (social sciences), media_common
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8
المؤلفون: Jiri Dostal, Hana Buckova
المصدر: 2019 17th International Conference on Emerging eLearning Technologies and Applications (ICETA).
مصطلحات موضوعية: Czech, Point (typography), Subject (documents), Context (language use), language.human_language, Information and Communications Technology, Informatics, ComputingMilieux_COMPUTERSANDEDUCATION, language, Mathematics education, media_common.cataloged_instance, European union, Curriculum, media_common
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9
المؤلفون: Xiaojun Wang, Jiri Dostal, Hana Buckova
المصدر: Proceedings of the 2018 2nd International Conference on Education and E-Learning.
مصطلحات موضوعية: Czech, 05 social sciences, 050301 education, Subject (documents), Context (language use), 02 engineering and technology, language.human_language, 020204 information systems, Computer literacy, Informatics, ComputingMilieux_COMPUTERSANDEDUCATION, 0202 electrical engineering, electronic engineering, information engineering, language, Mathematics education, Sociology, Everyday life, 0503 education, Curriculum, Digital literacy
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10
المؤلفون: Verena, Wally, Alain, Hovnanian, Juliette, Ly, Hana, Buckova, Victoria, Brunner, Thomas, Lettner, Michael, Ablinger, Thomas K, Felder, Peter, Hofbauer, Martin, Wolkersdorfer, Florian B, Lagler, Wolfgang, Hitzl, Martin, Laimer, Sophie, Kitzmüller, Anja, Diem, Johann W, Bauer
المصدر: Journal of the American Academy of Dermatology. 78(5)
مصطلحات موضوعية: Male, Dose-Response Relationship, Drug, Orphan Drug Production, Administration, Topical, Anti-Inflammatory Agents, Anthraquinones, Risk Assessment, Severity of Illness Index, Drug Administration Schedule, Treatment Outcome, Double-Blind Method, Child, Preschool, Epidermolysis Bullosa Simplex, Humans, Patient Compliance, Female, Child, Follow-Up Studies
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11
المؤلفون: Adriana M Valencia, Olivia Boccara, Ilona J. Frieden, Peter H. Hoeger, María Isabel Febrer Bosch, Danuta Perek, Pierre Souteyrand, Sheila Fallon Friedlander, Antonio Torrelo, Annabel Maruani, Przemysław Przewratil, Juliette Mazereeuw-Hautier, Nicholas Birchall, Orli Wargon, Anthony J. Mancini, Frédéric Cambazard, Pierre Vabres, Alain Delarue, Sharon A. Glick, Cyrus R. Mehta, Rainer Grantzow, Sorilla Prey, Jose Bernabeu-Wittel, Rosalia Ballona, Alfons Krol, Regina Foelster-Holst, Juan Carlos López Gutiérrez, Jean-Jacques Voisard, Christine Léauté-Labrèze, Hana Buckova, Caroline C. Morgan, Gintas Posiunas, Dariusz Wyrzykowski, Zsuzsanna Szalai, Jochen Roessler, Stephane Heritier, Charles I Berul, Brandie J. Metz, Héctor Cáceres, Franck Boralevi, Laurent Guibaud, Sébastien Barbarot, Latanya Benjamin, John C Su, Eulalia Baselga, Elena Pope, Julie Powell, Roderic J Phillips
المساهمون: Service de Dermatologie (CHU de Dijon), Centre Hospitalier Universitaire de Dijon - Hôpital François Mitterrand (CHU Dijon), CHU Clermont-Ferrand, Department of Cardiology, Harvard Medical School [Boston] (HMS), Biothérapies des maladies génétiques et cancers, Université Bordeaux Segalen - Bordeaux 2-Institut National de la Santé et de la Recherche Médicale (INSERM), Hôpital Pellegrin, CHU Bordeaux [Bordeaux]-Groupe hospitalier Pellegrin, CHU Bordeaux [Bordeaux], centre de référence des maladies rares de la peau, CHU Toulouse, Hôpital Larrey [Toulouse], CHU Toulouse [Toulouse]-CHU Toulouse [Toulouse], Hôpital Femme Mère Enfant [CHU - HCL] (HFME), Hospices Civils de Lyon (HCL), Department of Pediatric Oncology, The Children's Memorial Health Institute, Centre hospitalier universitaire de Nantes (CHU Nantes), Centre Hospitalier Régional Universitaire de Tours (CHRU Tours), MethodS in Patients-centered outcomes and HEalth ResEarch (SPHERE), Université de Tours (UT)-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Nantes - UFR des Sciences Pharmaceutiques et Biologiques, Université de Nantes (UN)-Université de Nantes (UN), CHU Necker - Enfants Malades [AP-HP], Assistance publique - Hôpitaux de Paris (AP-HP) (AP-HP), Centre Hospitalier Universitaire de Saint-Etienne (CHU de Saint-Etienne), Sydney Children's hospital, Centre Hospitalier Régional Universitaire de Tours (CHRU TOURS), Université de Tours-Institut National de la Santé et de la Recherche Médicale (INSERM)-Université de Nantes - UFR des Sciences Pharmaceutiques et Biologiques
المصدر: The New England Journal of Medicine
The New England Journal of Medicine, 2015, 372 (8), pp.735-746. ⟨10.1056/NEJMoa1404710⟩
NEW ENGLAND JOURNAL OF MEDICINE
r-IIB SANT PAU. Repositorio Institucional de Producción Científica del Instituto de Investigación Biomédica Sant Pau
instnameمصطلحات موضوعية: Oral, Male, medicine.medical_specialty, Randomization, [SDV]Life Sciences [q-bio], Adrenergic beta-Antagonists, Administration, Oral, Placebo, Drug Administration Schedule, law.invention, Hemangioma, Dose-Response Relationship, Randomized controlled trial, Double-Blind Method, law, medicine, Clinical endpoint, Humans, Dose-Response Relationship, Drug, business.industry, Infant, General Medicine, Interim analysis, medicine.disease, Propranolol, 3. Good health, Surgery, Clinical trial, Regimen, Treatment Outcome, Administration, Female, Drug, Hypotension, business