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1
المؤلفون: Ranran Zhang, Ravi Kothapalli, Rosalyn B. Irby, Mithun Vinod Shah, Ty Arrington, Thomas P. Loughran, Xin Liu, Bryan Frank, Norman H. Lee
المصدر: Blood. 112:770-781
مصطلحات موضوعية: Programmed cell death, Cell Survival, Lymphocyte, CD3, Immunology, Apoptosis, Biology, Biochemistry, medicine, Humans, Cytotoxic T cell, Sphingolipids, Neoplasia, Gene Expression Profiling, Cell Biology, Hematology, medicine.disease, Cell biology, Gene Expression Regulation, Neoplastic, Leukemia, Large Granular Lymphocytic, Receptors, Lysosphingolipid, Leukemia, medicine.anatomical_structure, Case-Control Studies, Galactosylgalactosylglucosylceramidase, biology.protein, Signal transduction, CD8, Signal Transduction, T-Lymphocytes, Cytotoxic
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2
المؤلفون: Xingxuan He, Efrat Eliyahu, Edward H. Schuchman, Ruth Shalgi, Jae-Ho Park, Nataly Shtraizent
المصدر: Journal of Biological Chemistry. 283:11253-11259
مصطلحات موضوعية: Protein Conformation, Stereochemistry, CHO Cells, Arginine, Cleavage (embryo), Biochemistry, Hydrolysis, Cricetulus, Protein structure, Cricetinae, Hydrolase, Animals, Humans, Cysteine, Isoleucine, Molecular Biology, chemistry.chemical_classification, Aspartic Acid, Enzyme Catalysis and Regulation, Hydrogen Bonding, Cell Biology, Cysteine protease, Recombinant Proteins, Amino acid, Enzyme Activation, Acid Ceramidase, chemistry, Galactosylgalactosylglucosylceramidase, Mutagenesis, Site-Directed
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3
المؤلفون: Naoko Takezaki, Kazuhito Tsuboi, Natsuo Ueda
المصدر: Chemistry & Biodiversity. 4:1914-1925
مصطلحات موضوعية: Molecular Sequence Data, Bioengineering, Biochemistry, Amidohydrolases, Amidase, chemistry.chemical_compound, Fatty acid amide hydrolase, N-Acylethanolamine, Hydrolase, Animals, Humans, Amino Acid Sequence, Molecular Biology, chemistry.chemical_classification, Hydrolysis, Fatty acid, General Chemistry, General Medicine, Anandamide, Ceramidase, Amino acid, Acid Ceramidase, chemistry, Ethanolamines, Galactosylgalactosylglucosylceramidase, Molecular Medicine
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4
المؤلفون: David H. Holman, John McKillop, Jian-Yun Dong, Terrence A. Day, Saeed Elojeimy, Yusuf A. Hannun, Ahmed El-Zawahry, James S. Norris, Lorianne S. Turner, Alicja Bielawska, Joseph C. Cheng, Ayman Mahdy, Xiang Liu, William D Meacham, Jonathan Y Cheng, Antonio F. Saad
المصدر: Molecular Therapy. 15:1259-1263
مصطلحات موضوعية: Small interfering RNA, Fas Ligand Protein, Cell Survival, Genetic enhancement, Cell, Down-Regulation, Mice, Nude, Biology, Ceramides, Sensitivity and Specificity, Fas ligand, Mice, 03 medical and health sciences, 0302 clinical medicine, Cell Line, Tumor, Drug Discovery, Genetics, medicine, Animals, Humans, Enzyme Inhibitors, RNA, Small Interfering, Molecular Biology, 030304 developmental biology, Pharmacology, 0303 health sciences, Cancer, Genetic Therapy, medicine.disease, Xenograft Model Antitumor Assays, 3. Good health, Gene Expression Regulation, Neoplastic, Acid Ceramidase, stomatognathic diseases, Cell killing, medicine.anatomical_structure, Head and Neck Neoplasms, Apoptosis, 030220 oncology & carcinogenesis, Immunology, Galactosylgalactosylglucosylceramidase, Cancer research, Molecular Medicine, Female
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5
المؤلفون: Kristi L. Norris, David H. Holman, Jacek Bielawski, James S. Norris, Youssef H. Zeidan, Saeed Elojeimy, Xiang Liu, Lorianne S. Turner, Zdzislaw M. Szulc, Ahmed El-Zawahry, Yusuf A. Hannun, Alicja Bielawska
المصدر: Cancer Chemotherapy and Pharmacology. 61:231-242
مصطلحات موضوعية: Male, Cancer Research, Programmed cell death, Ceramide, Blotting, Western, Antineoplastic Agents, Apoptosis, Biology, Ceramides, Toxicology, Membrane Potentials, chemistry.chemical_compound, Prostate cancer, Cell Line, Tumor, medicine, Humans, Pharmacology (medical), Enzyme Inhibitors, Pharmacology, Sphingolipids, Microscopy, Confocal, Reverse Transcriptase Polymerase Chain Reaction, Prostatic Neoplasms, Cancer, Hydrogen-Ion Concentration, Ceramidase, medicine.disease, Sphingolipid, Enzyme Activation, Acid Ceramidase, Sphingomyelin Phosphodiesterase, Oncology, chemistry, Biochemistry, Caspases, Mitochondrial Membranes, Cancer cell, Galactosylgalactosylglucosylceramidase, Cancer research, Indicators and Reagents, Lysosomes, Subcellular Fractions
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6
المؤلفون: Albert Morales, Montserrat Marí, José C. Fernández-Checa, Laura Llacuna, Carmen García-Ruiz
المصدر: Hepatology. 44:561-572
مصطلحات موضوعية: Ceramide, Blotting, Western, Ischemia, Down-Regulation, Oleic Acids, Pharmacology, Polymerase Chain Reaction, Mice, chemistry.chemical_compound, medicine, Animals, RNA, Messenger, Enzyme Inhibitors, Hepatology, business.industry, Lipid signaling, medicine.disease, Ceramidase, Sphingolipid, Mice, Inbred C57BL, Acid Ceramidase, Disease Models, Animal, Sphingomyelin Phosphodiesterase, Liver, chemistry, Ethanolamines, Reperfusion Injury, Immunology, Galactosylgalactosylglucosylceramidase, Tumor necrosis factor alpha, business, Reperfusion injury, Endocannabinoids, Follow-Up Studies
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7
المؤلفون: David H. Holman, Joseph C. Cheng, Ahmed El-Zawahry, Maristella Villani, Saeed Elojeimy, Youssef H. Zeidan, Yusuf A. Hannun, Ayman Mahdy, James S. Norris, Alicja Bielwaska, Xiang Liu
المصدر: FEBS Letters. 580:4751-4756
مصطلحات موضوعية: Male, Sphingomyelin, medicine.medical_specialty, Ceramide, Biophysics, Antidepressive Agents, Tricyclic, Biochemistry, Cathepsin B, 03 medical and health sciences, chemistry.chemical_compound, 0302 clinical medicine, Structural Biology, Cell Line, Tumor, Desipramine, Internal medicine, Genetics, medicine, Humans, Acid sphingomyelinase, Cationic amphiphilic drugs, Enzyme Inhibitors, Molecular Biology, 030304 developmental biology, Sphingolipids, 0303 health sciences, Reverse Transcriptase Polymerase Chain Reaction, Hydrolysis, Cell Biology, Sphingolipid, 3. Good health, Acid Ceramidase, Cysteine Endopeptidases, Endocrinology, chemistry, Mechanism of action, Acid ceramidase, 030220 oncology & carcinogenesis, Galactosylgalactosylglucosylceramidase, medicine.symptom, Pepstatin, medicine.drug
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8
المؤلفون: Benjamin J. Pettus, James S. Norris, Saeed Elojeimy, Toshihiko Kawamori, Youssef H. Zeidan, Tarek A. Taha, Yusuf A. Hannun, Lina M. Obeid
المصدر: Journal of Biological Chemistry. 281:24695-24703
مصطلحات موضوعية: Models, Molecular, medicine.medical_specialty, medicine.medical_treatment, Sphingosine kinase, Pharmacology, Biology, Biochemistry, Dinoprostone, Cell Line, Mice, chemistry.chemical_compound, Sphingosine, Internal medicine, Desipramine, medicine, Animals, Molecular Biology, Tumor Necrosis Factor-alpha, Cell Biology, Sphingolipid, Acid Ceramidase, Sphingomyelin Phosphodiesterase, Endocrinology, chemistry, Galactosylgalactosylglucosylceramidase, RNA Interference, lipids (amino acids, peptides, and proteins), Lysophospholipids, Acid sphingomyelinase, Sphingomyelin, Signal Transduction, medicine.drug, Prostaglandin E
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9
المؤلفون: Efrat Eliyahu, Goutham Narla, John A. Martignetti, Analisa DiFeo, Edward H. Schuchman, Jae Ho Park
المصدر: Biochimica et Biophysica Acta (BBA) - Gene Structure and Expression. 1732:82-87
مصطلحات موضوعية: Blotting, Western, Kruppel-Like Transcription Factors, Biophysics, Electrophoretic Mobility Shift Assay, Biology, Biochemistry, Gene Expression Regulation, Enzymologic, Mice, Genes, Reporter, Structural Biology, Cell Line, Tumor, Proto-Oncogene Proteins, Gene expression, Kruppel-Like Factor 6, Genetics, Animals, Humans, Electrophoretic mobility shift assay, RNA, Messenger, Northern blot, Gene, Transcription factor, Gene Expression Profiling, Exons, Molecular biology, Gene expression profiling, Acid Ceramidase, KLF6, Galactosylgalactosylglucosylceramidase, NIH 3T3 Cells, RNA Interference
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10
المؤلفون: Jens-Michael Jensen, Michael Förl, Ehrhardt Proksch, Michael Schunck, Stefan Schütze, Supandi Winoto-Morbach, Sophie Seite
المصدر: Experimental Dermatology. 14:609-618
مصطلحات موضوعية: Aging, Ceramide, Lipid Bilayers, Dermatology, Sphingomyelin phosphodiesterase, Biology, Biochemistry, Permeability, Mice, chemistry.chemical_compound, Skin Physiological Phenomena, Stratum corneum, medicine, Animals, Molecular Biology, Ceramide synthase, Skin, Mice, Hairless, integumentary system, Ceramidase, Skin Aging, Sphingomyelins, Cell biology, Exfoliatins, Acid Ceramidase, Sphingomyelin Phosphodiesterase, medicine.anatomical_structure, Ceramidase activity, chemistry, Galactosylgalactosylglucosylceramidase, Epidermis, Acid sphingomyelinase, Oxidoreductases, medicine.drug
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11
المصدر: Journal of Biological Chemistry. 280:20148-20153
مصطلحات موضوعية: Ceramide, DNA, Complementary, medicine.medical_treatment, Muscle Fibers, Skeletal, Palmitic Acid, Gene Expression, Fatty Acids, Nonesterified, Protein Serine-Threonine Kinases, Biochemistry, Cell Line, Mice, chemistry.chemical_compound, Insulin resistance, Sphingosine, Proto-Oncogene Proteins, medicine, Animals, Humans, Insulin, Molecular Biology, Base Sequence, biology, Cell Biology, Lipid signaling, medicine.disease, Sphingolipid, Recombinant Proteins, Acid Ceramidase, Insulin receptor, chemistry, Galactosylgalactosylglucosylceramidase, biology.protein, lipids (amino acids, peptides, and proteins), Proto-Oncogene Proteins c-akt, Signal Transduction
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12
المؤلفون: Mutsumi Murakami, Takashi Shimada, Mari Hayakawa, Masaharu Kotani, Shinichiro Inagaki, Makoto Migita, Atushi Fujita, Yoshitaka Fukunaga, Junko Yoshida, Masamichi Ishizaki, Hitoshi Sakuraba
المصدر: Journal of Nippon Medical School. 72:387-390
مصطلحات موضوعية: Heterozygote, Pathology, medicine.medical_specialty, Adolescent, Biopsy, Kidney, Asymptomatic, medicine, Humans, Pathological, Subclinical infection, medicine.diagnostic_test, business.industry, General Medicine, Enzyme replacement therapy, medicine.disease, Fabry disease, alpha-Galactosidase, Galactosylgalactosylglucosylceramidase, Fabry Disease, Female, Renal biopsy, medicine.symptom, business, Nephrotic syndrome
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13
المؤلفون: Fei Liu, Cheng-Xin Gong, Hitoshi Tanimukai, Khalid Iqbal, Yu Huang, Inge Grundke-Iqbal
المصدر: European Journal of Neuroscience. 20:3489-3497
مصطلحات موضوعية: Aged, 80 and over, chemistry.chemical_classification, biology, Sialyltransferase, General Neuroscience, Brain, Human brain, Middle Aged, medicine.disease, Enzyme Activation, Acid Ceramidase, Enzyme activator, medicine.anatomical_structure, Biochemistry, chemistry, Alzheimer Disease, Galactosylgalactosylglucosylceramidase, medicine, biology.protein, Humans, Alzheimer's disease, Glycoprotein, Neuronal Cell Adhesion Molecule, Aged, CD81
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14
المصدر: European Journal of Cell Biology. 83:667-679
مصطلحات موضوعية: Keratinocytes, Histology, Keratin 14, Cellular differentiation, Serine C-Palmitoyltransferase, Gene Expression, Apoptosis, Filaggrin Proteins, Biology, Ceramides, Nitric Oxide, Saposins, Pathology and Forensic Medicine, Nitric oxide, chemistry.chemical_compound, Intermediate Filament Proteins, Keratin, Gene expression, medicine, Humans, RNA, Messenger, Cells, Cultured, Skin, chemistry.chemical_classification, Cell Differentiation, Cell Biology, General Medicine, Molecular biology, Cell biology, Acid Ceramidase, NG-Nitroarginine Methyl Ester, Sphingomyelin Phosphodiesterase, Gene Expression Regulation, chemistry, Glucosyltransferases, Galactosylgalactosylglucosylceramidase, Glucosylceramidase, Keratins, Calcium, Nitric Oxide Synthase, Acid sphingomyelinase, Acyltransferases, Biomarkers, medicine.drug
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15
المؤلفون: T Muramatsu, Minoru Yamada, Hiroko Tsukamoto, Chikara Kokubu, Itaru Yanagihara, Toshinori Nishigaki, Koji Inui, Makoto Ito, Norio Sakai
المصدر: Journal of Inherited Metabolic Disease. 25:585-592
مصطلحات موضوعية: Male, medicine.medical_specialty, DNA, Complementary, DNA Mutational Analysis, Mutation, Missense, Gene Expression, Biology, medicine.disease_cause, Exon, Japan, Internal medicine, Genetics, medicine, Lysosomal storage disease, Animals, Humans, Missense mutation, Child, Gene, Genetics (clinical), Sequence Deletion, Farber disease, Mutation, Polymorphism, Genetic, Base Sequence, Exons, Ceramidase, medicine.disease, Molecular biology, Lysosomal Storage Diseases, Acid Ceramidase, Endocrinology, COS Cells, Galactosylgalactosylglucosylceramidase, Female
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16
المؤلفون: Makoto Kawashima, Yutaka Takagi, Mutsumi Ishibashi, Yoshiaki Ichikawa, Genji Imokawa, Junko Arikawa
المصدر: Journal of Investigative Dermatology. 119:433-439
مصطلحات موضوعية: Adult, Staphylococcus aureus, Ceramide, Allergy, Adolescent, Dermatology, Biology, Ceramides, medicine.disease_cause, Biochemistry, Dermatitis, Atopic, Microbiology, chemistry.chemical_compound, Sphingosine, Stratum corneum, medicine, Humans, Molecular Biology, integumentary system, Cell Biology, Atopic dermatitis, medicine.disease, Sphingolipid, body regions, Acid Ceramidase, medicine.anatomical_structure, chemistry, Immunology, Galactosylgalactosylglucosylceramidase, Epidermis
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17
المؤلفون: Genji Imokawa, Reiko Okamoto, Makoto Kawashima, Junko Hara, Kazuhiko Higuchi
المصدر: Biochemical Journal. 350:747-756
مصطلحات موضوعية: Ceramide, Biochemistry, Dermatitis, Atopic, Palmitic acid, chemistry.chemical_compound, Sphingosine, Stratum corneum, medicine, Humans, Choline, Isoelectric Point, Molecular Biology, Skin, chemistry.chemical_classification, integumentary system, Molecular mass, Cell Biology, Hydrogen-Ion Concentration, Molecular Weight, Acid Ceramidase, Enzyme, medicine.anatomical_structure, chemistry, Case-Control Studies, Chromatography, Gel, Galactosylgalactosylglucosylceramidase, Electrophoresis, Polyacrylamide Gel, Chromatography, Thin Layer, Sphingomyelin, Carboxylic Ester Hydrolases, Research Article
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18
المؤلفون: Hong-Jun Rhee, Jae-Ho Park, Edward H. Schuchman, Brynn Levy, Seung-Beom Hong, Chi-Ming Li, Ook Joon Yoo, Xingxuan He
المصدر: Genomics. 62:232-241
مصطلحات موضوعية: DNA, Complementary, Transcription, Genetic, Sequence analysis, Recombinant Fusion Proteins, TATA box, Molecular Sequence Data, Biology, Transfection, Primer extension, Amidohydrolases, Mice, Complementary DNA, Genetics, Animals, Humans, Amino Acid Sequence, Cloning, Molecular, Gene, Base Sequence, Sequence Homology, Amino Acid, Nucleic acid sequence, Proteins, Molecular biology, Open reading frame, Organ Specificity, Protein Biosynthesis, COS Cells, Chromosomal region, Galactosylgalactosylglucosylceramidase, RNA, Chromosomes, Human, Pair 4, 5' Untranslated Regions
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19
المصدر: Annals of Plastic Surgery. 39:405-410
مصطلحات موضوعية: Reoperation, medicine.medical_specialty, medicine.medical_treatment, Chromosome Disorders, Genes, Recessive, Ceramides, Gingivectomy, Central nervous system disease, Autosomal recessive trait, medicine, Humans, Child, Chromosome Aberrations, Farber disease, Granuloma, business.industry, Pharynx, Airway obstruction, medicine.disease, Surgery, medicine.anatomical_structure, Gingival Diseases, Galactosylgalactosylglucosylceramidase, Female, Contracture, medicine.symptom, Lysosomes, business
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20
المؤلفون: Zhongjian Zhang, Asim K. Mandal, Janice Y. Chou, Anil B. Mukherjee
المصدر: The FASEB Journal. 15:1834-1836
مصطلحات موضوعية: Swine, Phospholipid, Receptors, Cell Surface, Biochemistry, Tropomyosin receptor kinase C, Phospholipases A, Mice, chemistry.chemical_compound, Cytosol, Growth factor receptor, Genetics, Animals, RNA, Messenger, Receptor, Pancreas, Molecular Biology, Phospholipids, Protein kinase C, chemistry.chemical_classification, Sphingolipids, Hepatocyte Growth Factor, Receptors, Phospholipase A2, 3T3 Cells, Fibroblast growth factor receptor 4, Cell biology, Fibroblast Growth Factors, Isoenzymes, Acid Ceramidase, Phospholipases A2, Sphingomyelin Phosphodiesterase, Enzyme, Gene Expression Regulation, chemistry, Cyclooxygenase 2, Prostaglandin-Endoperoxide Synthases, Galactosylgalactosylglucosylceramidase, Interleukin-1, Signal Transduction, Biotechnology