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المؤلفون: Paulína Káňovičová, Petra Čermáková, Dominika Kubalová, Lenka Bábelová, Petra Veselá, Martin Valachovič, Jakub Zahumenský, Anton Horváth, Jan Malínský, Mária Balážová
المصدر: The Journal of Biological Chemistry
مصطلحات موضوعية: WT, wild type, tafazzin, CL, cardiolipin, TAG, triacylglycerols, VPA, valproic acid, Cardiolipins, Pgc1, phosphatidylglycerol phospholipase C, Pgs1, phosphatidylglycerolphosphate synthase, Saccharomyces cerevisiae, PE, phosphatidylethanolamine, PG, phosphatidylglycerol, Biochemistry, Erg1, squalene epoxidase, PI, phosphatidylinositol, ETS capacity, maximum electron transfer system capacity, PC, phosphatidylcholine, valproic acid, BTHS, Barth syndrome, Crd1, cardiolipin synthase, Humans, phosphatidylglycerol, PA, phosphatidic acid, RCI, respiratory control index, Molecular Biology, MLCL, monolysocardiolipin, OXPHOS capacity, oxidative phosphorylation capacity, SE, sterol esters, Taz1, lyso-phosphatidylcholine acyltransferase, Phosphatidylglycerols, Cell Biology, PS, phosphatidylserine, mitochondria, Phenotype, Erg11, lanosterol 14-alpha-demethylase, PGP, phosphatidylglycerol phosphate, Barth Syndrome, lipids (amino acids, peptides, and proteins), DAG, diacylglycerol, Acyltransferases, Transcription Factors, Research Article