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1
المؤلفون: Marion C. Jones, Mark Higgins, Jerry A. Nick, Connie G. St. Clair, Vx Study Team, Lan Lan
المصدر: Journal of Cystic Fibrosis. 19:91-98
مصطلحات موضوعية: Male, 0301 basic medicine, Pulmonary and Respiratory Medicine, medicine.medical_specialty, Adolescent, Cystic Fibrosis, Functional Residual Capacity, Cystic Fibrosis Transmembrane Conductance Regulator, Quinolones, Lung Clearance Index, Aminophenols, Placebo, Cystic fibrosis, Gastroenterology, Ivacaftor, Young Adult, 03 medical and health sciences, 0302 clinical medicine, Double-Blind Method, Forced Expiratory Volume, Internal medicine, medicine, Clinical endpoint, Humans, Chloride Channel Agonists, Adverse effect, Cross-Over Studies, biology, business.industry, medicine.disease, Cystic fibrosis transmembrane conductance regulator, Confidence interval, Respiratory Function Tests, Treatment Outcome, 030104 developmental biology, 030228 respiratory system, Mutation, Pediatrics, Perinatology and Child Health, biology.protein, Female, business, medicine.drug
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2
المؤلفون: Milene T. Saavedra, Michael D. Iseman, Charles L. Daley, Christine M. Barboa, Cathy S. Chacon, Sara J. Brayshaw, Connie G. St. Clair, Frank J. Accurso, Marion C. Jones, Robert L. Young, David P. Nichols, Gwen A. Huitt, Jennifer S. Janssen, Jennifer L. Taylor-Cousar, Marci K. Sontag, Jerry A. Nick
المصدر: American Journal of Respiratory and Critical Care Medicine. 182:614-626
مصطلحات موضوعية: Adult, Male, Pulmonary and Respiratory Medicine, Pediatrics, medicine.medical_specialty, Colorado, Pancreatic disease, Cystic Fibrosis, Population, Cystic Fibrosis Transmembrane Conductance Regulator, Critical Care and Intensive Care Medicine, Severity of Illness Index, Cystic fibrosis, Age Distribution, Intensive care, Severity of illness, medicine, Humans, Registries, Survivors, Age of Onset, Sex Distribution, education, Aged, Retrospective Studies, education.field_of_study, business.industry, Respiratory disease, B. Cystic Fibrosis, Retrospective cohort study, Middle Aged, Patient Acceptance of Health Care, medicine.disease, Surgery, Disease Progression, Female, Age of onset, business
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3
المؤلفون: Jerry A. Nick, Jennifer L. Taylor-Cousar, Marion C. Jones, David P. Nichols, Linda A. Felton, Connie G. St. Clair, Milene T. Saavedra
المصدر: A23. ADULT CYSTIC FIBROSIS: ADVANCES IN TREATMENT AND UNDERSTANDING OF MECHANISMS OF DISEASE.
مصطلحات موضوعية: medicine.medical_specialty, chemistry.chemical_compound, Pharmacokinetics, chemistry, business.industry, Sildenafil, Internal medicine, Medicine, business, medicine.disease, Cystic fibrosis, Gastroenterology, Administration (government)
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4
المؤلفون: Michael Puderbach, Jennifer L. Taylor-Cousar, Jerry A. Nick, John Newell, Milene T. Saavedra, Jürgen Biederer, Marion C. Jones, David P. Nichols, Connie G. St. Clair, Jonathan H. Chung, Joyce D. Schroeder
المصدر: A23. ADULT CYSTIC FIBROSIS: ADVANCES IN TREATMENT AND UNDERSTANDING OF MECHANISMS OF DISEASE.
مصطلحات موضوعية: Correlation, medicine.medical_specialty, Lung, medicine.anatomical_structure, medicine.diagnostic_test, business.industry, medicine, Magnetic resonance imaging, Radiology, business, medicine.disease, Cystic fibrosis, Semi quantitative