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1
المؤلفون: Rajeswari R. Moganty, Hans Goldenberg, Barbara Scheiber-Mojdehkar, Hannes Steinkellner, Himanshu Narayan Singh, Brigitte Sturm, Martina U. Muckenthaler
المصدر: Gene. 621:5-11
مصطلحات موضوعية: 0301 basic medicine, Ataxia, Iron, Protoporphyrins, Heme, Hemoglobins, 03 medical and health sciences, chemistry.chemical_compound, Iron-Binding Proteins, Genetics, medicine, Humans, Erythropoiesis, Cells, Cultured, Erythroid Precursor Cells, Protoporphyrin IX, biology, Microarray analysis techniques, General Medicine, Ferrochelatase, Molecular biology, Oxidative Stress, 030104 developmental biology, chemistry, Friedreich Ataxia, Case-Control Studies, Frataxin, biology.protein, Hemoglobin, medicine.symptom, Stem cell
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2
المؤلفون: Monika Praschberger, Kathrin Haider, Hans Goldenberg, Brigitte Sturm, Carolin Cornelius, Markus Schitegg, Barbara Scheiber-Mojdehkar
المصدر: BioMetals. 28:35-50
مصطلحات موضوعية: Iron, Ascorbic Acid, Iron sucrose, Ferric Compounds, General Biochemistry, Genetics and Molecular Biology, Cell Line, Biomaterials, Glucaric Acid, Hepcidin, medicine, Humans, Maltose, Ferric Oxide, Saccharated, chemistry.chemical_classification, biology, Vitamin C, Macrophages, Metals and Alloys, Biological activity, Hep G2 Cells, Ascorbic acid, Bioavailability, Ferritin, Liver, chemistry, Biochemistry, Transferrin, Ferritins, biology.protein, General Agricultural and Biological Sciences, medicine.drug
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3
المؤلفون: Wolfgang Nachbauer, Barbara Scheiber-Mojdehkar, Sylvia Boesch, Marek Kubicki, Michael Schocke, Karl Egger, Christian Clemm von Hohenberg, Martha E. Shenton, Brigitte Sturm, Demian Wassermann, Christian Kremser, Charles R.G. Guttmann, Marlene C. Wigand
المصدر: Journal of Neuroimaging. 24:504-508
مصطلحات موضوعية: medicine.medical_specialty, Pathology, Ataxia, business.industry, Multiple sclerosis, medicine.disease, Pons, White matter, medicine.anatomical_structure, Erythropoietin, Fractional anisotropy, medicine, Physical therapy, Radiology, Nuclear Medicine and imaging, Neurology (clinical), medicine.symptom, business, Stroke, Diffusion MRI, medicine.drug
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4
المؤلفون: Markus Reindl, Wolfgang Nachbauer, Andreas Eigentler, Barbara Scheiber-Mojdehkar, Brigitte Sturm, Werner Poewe, Sylvia Boesch, Julia Wanschitz, Hannes Steinkellner, Kurt Hufler
المصدر: Movement Disorders. 26:1935-1938
مصطلحات موضوعية: Adult, Male, congenital, hereditary, and neonatal diseases and abnormalities, medicine.medical_specialty, Time Factors, Ataxia, Biopsy, Statistics as Topic, Peripheral blood mononuclear cell, Disability Evaluation, Iron-Binding Proteins, Internal medicine, medicine, Humans, Muscle, Skeletal, Erythropoietin, Mitochondrial protein, biology, business.industry, Skeletal muscle, Middle Aged, Peripheral blood, Endocrinology, medicine.anatomical_structure, Neurology, Friedreich Ataxia, Cancer research, Frataxin, biology.protein, Biomarker (medicine), Female, Neurology (clinical), medicine.symptom, business, Biomarkers, medicine.drug
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5
المؤلفون: Sascha Hering, Brigitte Sturm, Guenter Weiss, Alexander Strasak, Markus Seifert, Hannes Steinkellner, Barbara Scheiber-Mojdehkar, Wolfgang Nachbauer, Sylvia Boesch, Werner Poewe, Markus Reindl
المصدر: The Cerebellum. 10:763-769
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Ataxia, Pilot Projects, Neuroprotection, Drug Administration Schedule, Downregulation and upregulation, Iron-Binding Proteins, Internal medicine, medicine, Humans, Erythropoietin, Dose-Response Relationship, Drug, biology, Middle Aged, Recombinant Proteins, Mitochondria, Ferritin, Endocrinology, Neurology, Biochemistry, Friedreich Ataxia, Frataxin, biology.protein, Female, Neurology (clinical), NAD+ kinase, medicine.symptom, Function (biology), medicine.drug
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6
المؤلفون: Sylvia Boesch, Barbara Scheiber-Mojdehkar, Werner Poewe, Wolfgang Nachbauer, Rainer Schneider, Sascha Hering, Brigitte Sturm, Hannes Steinkellner
المصدر: The Open Drug Discovery Journal. 2:18-24
مصطلحات موضوعية: Ataxia, Growth factor, medicine.medical_treatment, Oxidative phosphorylation, Mitochondrion, Biology, Pharmacology, Neuroprotection, Haematopoiesis, Biochemistry, Erythropoietin, Drug Discovery, Frataxin, biology.protein, medicine, medicine.symptom, medicine.drug
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7
المؤلفون: Hannes Steinkellner, Hans Goldenberg, Brigitte Sturm, Barbara Scheiber-Mojdehkar, Mohammad Mehdi Heidari, Melissa Helminger
المصدر: European Journal of Clinical Investigation. 40:561-565
مصطلحات موضوعية: medicine.medical_specialty, Ataxia, biology, Clinical Biochemistry, Iron-binding proteins, General Medicine, Biochemistry, Erythropoietin receptor, Endocrinology, Cell culture, Erythropoietin, hemic and lymphatic diseases, Internal medicine, medicine, Frataxin, biology.protein, Cancer research, Monocytic leukemia, medicine.symptom, medicine.drug, K562 cells
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8
المؤلفون: Hannes Steinkellner, Brigitte Sturm, Hans Goldenberg, Werner Poewe, Barbara Scheiber-Mojdehkar, Sylvia Boesch, Sascha Hering
المصدر: Movement Disorders. 23:1940-1944
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Ataxia, Enzyme-Linked Immunosorbent Assay, Pilot Projects, Hematocrit, medicine.disease_cause, Severity of Illness Index, Gastroenterology, Central nervous system disease, Iron-Binding Proteins, Internal medicine, medicine, Humans, Lymphocytes, Erythropoietin, biology, medicine.diagnostic_test, business.industry, Deoxyguanosine, Middle Aged, Phlebotomy, medicine.disease, Recombinant Proteins, Surgery, Clinical trial, Treatment Outcome, Neurology, 8-Hydroxy-2'-Deoxyguanosine, Friedreich Ataxia, Frataxin, biology.protein, Female, Neurology (clinical), medicine.symptom, business, Oxidative stress, Follow-Up Studies, medicine.drug
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9
المصدر: Nephrology Dialysis Transplantation. 22:2824-2830
مصطلحات موضوعية: Time Factors, Iron, Enzyme-Linked Immunosorbent Assay, In Vitro Techniques, Hydroxyethyl starch, Cell Line, Hydroxyethyl Starch Derivatives, chemistry.chemical_compound, Dichlorofluorescein, Humans, Medicine, Iron Dextran Complex, Chelating Agents, Hetastarch, Transplantation, Dose-Response Relationship, Drug, biology, business.industry, Macrophages, Dextrans, In vitro, Calcein, Ferritin, Dextran, Liver, chemistry, Biochemistry, Nephrology, Ferritins, biology.protein, business, Oxidation-Reduction, medicine.drug
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10
المؤلفون: Hans Goldenberg, Sylvia Czingraber, Brigitte Sturm, Nina Ternes, Barbara Scheiber-Mojdehkar, Birgit Knapitsch, Teresa E. Twaroch
المصدر: Biochimie. 88:575-581
مصطلحات موضوعية: biology, Ebselen, Iron, Respiratory chain, Iron Chelating Agents, Antimycin A, General Medicine, Metabolism, Mitochondrion, medicine.disease_cause, Biochemistry, Ferritin, Oxidative Stress, chemistry.chemical_compound, Nitrofurantoin, chemistry, Cell Line, Tumor, biology.protein, medicine, Humans, Oxidative stress
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11
المصدر: FEBS Letters. 579:6486-6492
مصطلحات موضوعية: inorganic chemicals, Antioxidant, Cations, Divalent, medicine.medical_treatment, Radical, Inorganic chemistry, Amidines, Biophysics, Wine, Photochemistry, Biochemistry, chemistry.chemical_compound, Lipid oxidation, Sulfite, Structural Biology, Transition Elements, Genetics, medicine, Sulfites, Molecular Biology, Aqueous solution, biology, Chemistry, Copper ions, Aqueous two-phase system, Cell Biology, Oxidants, Pro-oxidant, Lipoproteins, LDL, Catalase, biology.protein, Reactive Oxygen Species, LDL oxidation, Oxidation-Reduction, Copper
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12
المؤلفون: Brigitte Sturm, Joseph P. Sarsero, Ursula Rauen, Barbara Scheiber-Mojdehkar, Ute Bistrich, Herbert de Groot, Panos A. Ioannou, Matthias Schranzhofer, Frank Petrat
المصدر: Journal of Biological Chemistry. 280:6701-6708
مصطلحات موضوعية: Lymphoblast, Iron Chelating Agents, Transferrin receptor, Cell Biology, Oxidative phosphorylation, Metabolism, Mitochondrion, Biology, Biochemistry, medicine, Frataxin, biology.protein, Ferric, Molecular Biology, medicine.drug
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13
المؤلفون: Geneieve Tai, Monika Praschberger, Andrew Churchyard, Martin B. Delatycki, Barbara Scheiber-Mojdehkar, Katherine J Lee, Sarah E.M. Stephenson, Louise A. Corben, Monique M. Ryan, Adam P. Vogel, Eppie M. Yiu, Gary Rance, Creina S. Stockley, Chung-Yung J. Lee, Marguerite V. Evans-Galea, Brigitte Sturm, Joseph P. Sarsero, Kevin D. Croft, Roger E. Peverill, Trevor A. Mori, Paul J. Lockhart
المصدر: ResearcherID
مصطلحات موضوعية: Oncology, Adult, Male, medicine.medical_specialty, Ataxia, Resveratrol, medicine.disease_cause, Peripheral blood mononuclear cell, Antioxidants, chemistry.chemical_compound, Young Adult, Internal medicine, Iron-Binding Proteins, Stilbenes, medicine, Humans, RNA, Messenger, Adverse effect, Genetics, F2-Isoprostanes, biology, Fourier Analysis, Deoxyguanosine, Middle Aged, Clinical trial, Treatment Outcome, Neurology, Tolerability, chemistry, 8-Hydroxy-2'-Deoxyguanosine, Friedreich Ataxia, Frataxin, biology.protein, Leukocytes, Mononuclear, Female, Neurology (clinical), medicine.symptom, Oxidative stress
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14
المؤلفون: Markus Schitegg, Brigitte Sturm, Barbara Scheiber-Mojdehkar, Hans Goldenberg, Carolin Cornelius, Monika Praschberger
المصدر: Pharmaceutical development and technology. 20(2)
مصطلحات موضوعية: Sucrose, Anemia, Cell Culture Techniques, Pharmaceutical Science, Biological Availability, Enzyme-Linked Immunosorbent Assay, Iron sucrose, Ferric Compounds, chemistry.chemical_compound, Glucaric Acid, Drug Stability, medicine, Drugs, Generic, Humans, Food science, Ferric Oxide, Saccharated, biology, Anemia, Iron-Deficiency, Dose-Response Relationship, Drug, Macrophages, Spectrophotometry, Atomic, General Medicine, Iron deficiency, Hep G2 Cells, medicine.disease, Bioavailability, Calcein, Ferritin, Drug Liberation, chemistry, Biochemistry, Toxicity, Ferritins, Injections, Intravenous, biology.protein, medicine.drug
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15
المؤلفون: Karl, Egger, Christian, Clemm von Hohenberg, Michael F, Schocke, Charles R G, Guttmann, Demian, Wassermann, Marlene C, Wigand, Wolfgang, Nachbauer, Christian, Kremser, Brigitte, Sturm, Barbara, Scheiber-Mojdehkar, Marek, Kubicki, Martha E, Shenton, Sylvia, Boesch
المصدر: Journal of neuroimaging : official journal of the American Society of Neuroimaging. 24(5)
مصطلحات موضوعية: Adult, Male, Adolescent, Middle Aged, White Matter, Article, Young Adult, Diffusion Tensor Imaging, Neuroprotective Agents, Treatment Outcome, Friedreich Ataxia, Humans, Female, Erythropoietin
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16
المصدر: Analytica chimica acta. 659(1-2)
مصطلحات موضوعية: Ataxia, Locus (genetics), Enzyme-Linked Immunosorbent Assay, Computational biology, Biochemistry, Analytical Chemistry, Mice, Basic research, Cell Line, Tumor, Iron-Binding Proteins, High-Throughput Screening Assays, medicine, Environmental Chemistry, Electrochemiluminescence, Animals, Humans, Gene, Mitochondrial protein, Spectroscopy, biology, Chemistry, Molecular biology, Friedreich Ataxia, Luminescent Measurements, Frataxin, biology.protein, medicine.symptom, K562 Cells, HeLa Cells
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17
المؤلفون: Franco Laccone, Therese Boehm, Hans Goldenberg, Brigitte Sturm, Barbara Scheiber-Mojdehkar, Britta Kluge
المصدر: Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology. 32(2)
مصطلحات موضوعية: Male, congenital, hereditary, and neonatal diseases and abnormalities, Ataxia, Population, Enzyme-Linked Immunosorbent Assay, Dermatology, Age and sex, Polymerase Chain Reaction, Iron-Binding Proteins, medicine, Humans, Lymphocytes, Allele, education, Gene, Genetics, education.field_of_study, biology, Intron, nutritional and metabolic diseases, General Medicine, Molecular biology, Psychiatry and Mental health, Austria, Frataxin, biology.protein, Female, Neurology (clinical), medicine.symptom, Trinucleotide repeat expansion, Trinucleotide Repeat Expansion
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18
المؤلفون: Brigitte Sturm, Werner Poewe, Sylvia Boesch, Hans Goldenberg, Sascha Hering, Barbara Scheiber-Mojdehkar
المصدر: Annals of neurology. 62(5)
مصطلحات موضوعية: Adult, Male, medicine.medical_specialty, Pathology, Ataxia, Adolescent, Urinary system, Pilot Projects, medicine.disease_cause, Gastroenterology, law.invention, Central nervous system disease, law, Internal medicine, Iron-Binding Proteins, medicine, Humans, Erythropoietin, biology, business.industry, Middle Aged, medicine.disease, Recombinant Proteins, Clinical trial, Neurology, Friedreich Ataxia, Frataxin, biology.protein, Recombinant DNA, Female, Neurology (clinical), medicine.symptom, business, Oxidative stress, medicine.drug
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19
المؤلفون: Hilde Laggner, Markus K. Muellner, Sabine Schreier, Brigitte Sturm, Marcela Hermann, Markus Exner, Bernhard M. K. Gmeiner, Stylianos Kapiotis
المصدر: Free radical research. 41(7)
مصطلحات موضوعية: Electrophoresis, Apolipoprotein B, biology, Hypochlorous acid, Stereochemistry, Chloramines, Hypochlorite, General Medicine, Glutathione, Hydrogen Peroxide, Atherosclerosis, Biochemistry, Hypochlorous Acid, Lipoproteins, LDL, chemistry.chemical_compound, chemistry, Myeloperoxidase, biology.protein, Humans, Hydrogen Sulfide, Hydrogen peroxide, Heme, Peroxidase
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20
المؤلفون: Hans Goldenberg, Markus Exner, Stefan Kopp, Barbara Scheiber-Mojdehkar, Stylianos Kapiotis, Brigitte Sturm, Bernhard M.K. Gmeiner, Marcela Hermann, Peter Chiba
المصدر: Free radical research. 39(11)
مصطلحات موضوعية: inorganic chemicals, Electrophoresis, Time Factors, Free Radicals, Iron, Lipoproteins, Phospholipid, Biochemistry, Thiobarbituric Acid Reactive Substances, chemistry.chemical_compound, Lipid oxidation, Renal Dialysis, TBARS, Humans, Cells, Cultured, Ions, Liposome, integumentary system, General Medicine, Hydrogen Peroxide, Atherosclerosis, Lipid Metabolism, Lipids, Lipoproteins, LDL, Oxygen, Spectrometry, Fluorescence, chemistry, Low-density lipoprotein, Hemin, lipids (amino acids, peptides, and proteins), Endothelium, Vascular, Lipid Peroxidation, Oxidation-Reduction, Fluorescence anisotropy, Copper, Lipoprotein, Aluminum